Superior semicircular canal dehiscence with a large tegmental defect

We report on the presentation and clinical manifestations of superior semicircular canal dehiscence in association with a large defect of the tegmen tympani in a 41-year-old woman with no previous history of trauma. Based on this case we recommend that clinicians consider the possibility of superior semicircular canal dehiscence in patients presenting with symptoms associated with tegmen defects.

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Clinical Manifestations of Superior Semicircular Canal Dehiscence

The Laryngoscope ◽

10.1097/01.mlg.0000178324.55729.b7 ◽

2005 ◽

Vol 115 (10) ◽

pp. 1717-1727 ◽

Cited By ~ 333

Author(s):

Lloyd B. Minor

Keyword(s):

Semicircular Canal ◽

Clinical Manifestations ◽

Superior Semicircular Canal Dehiscence ◽

Superior Semicircular Canal ◽

Canal Dehiscence

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Superior Semicircular Canal Dehiscence Syndrome: Review of Clinical Manifestations in Adults and Children

Philippine Journal of Otolaryngology Head and Neck Surgery ◽

10.32412/pjohns.v24i2.675 ◽

2009 ◽

Vol 24 (2) ◽

pp. 6-13

Author(s):

Scheherazade C. Ibrahim ◽

Charlotte M. Chiong ◽

Nathaniel W. Yang

Keyword(s):

Semicircular Canal ◽

Clinical Manifestations ◽

Case Series ◽

Vestibular Evoked Myogenic Potential ◽

Superior Semicircular Canal Dehiscence ◽

Computed Tomographic ◽

Myogenic Potential ◽

Superior Semicircular Canal ◽

Computed Tomographic Scan ◽

Canal Dehiscence

Objective: This report aims to determine the clinical manifestations and management of patients with superior semicircular canal dehiscence syndrome (SSCDS). Methods: Study Design: Case series. Setting: Tertiary hospitals and private clinics Participants: Out of 30 patients with vestibular vertigo or otologic symptom, 14 patients were diagnosed with SSCDS based on high resolution computed tomographic scan (HRCT). The demographic features, incidence of specific signs and symptoms and management of these patients were described, including the audiograms, vestibular evoked myogenic potential (VEMP) responses and ancillary tests. Results: Vertigo was the most common vestibular symptom of SSCDS. Tullio phenomenon was elicited in 50% of patients with confirmed dehiscence on HRCT scan. Low frequency (250 Hz and 500 Hz) air-bone gap was noted in 21.4% of patients. Lowered VEMP responses were also noted in 66.7% of patients with confirmed SSCDS. Severity of symptoms may determine its management. Conclusion: The diagnosis of SSCDS does not conform to a specific clinical presentation or audiologic result thus good clinical correlation is needed in order to raise suspicion of the disease and prompt the clinician to order confirmatory imaging by computed tomographic scan or magnetic resonance imaging. The presence of this syndrome in a proportion of children that is greater than previously reported needs further study as these children may be genetically predisposed to have thinned out superior semicircular canals that eventually become dehisced albeit at an earlier age. Key words: Superior semicircular canal dehiscence, pure tone audiometry, vestibular evoked myogenic potential

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Ontogenetic Explanation for Tegmen Tympani Dehiscence and Superior Semicircular Canal Dehiscence Association

Acta Otorrinolaringologica (English Edition) ◽

10.1016/j.otoeng.2016.07.001 ◽

2016 ◽

Vol 67 (4) ◽

pp. 226-232 ◽

Cited By ~ 1

Author(s):

Jesús José Fraile Rodrigo ◽

Ana I. Cisneros ◽

Jesús Obón ◽

Carmen Yus ◽

Rafael Crovetto ◽

...

Keyword(s):

Semicircular Canal ◽

Superior Semicircular Canal Dehiscence ◽

Superior Semicircular Canal ◽

Tegmen Tympani ◽

Canal Dehiscence

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A Comparison of Diagnostic Accuracy of Superior Semicircular Canal Dehiscence in MDCT and MRI, and Coexistence with Tegmen Tympani Dehiscence

Journal of Neurological Surgery Part B Skull Base ◽

10.1055/s-0040-1714107 ◽

2020 ◽

Author(s):

Mikail Inal ◽

Nuray Bayar Muluk ◽

Mehmet H. Şahan ◽

Neşe Asal ◽

Gökçe Şimşek ◽

...

Keyword(s):

Temporal Lobe ◽

Semicircular Canal ◽

Temporal Distance ◽

Superior Semicircular Canal Dehiscence ◽

Superior Semicircular Canal ◽

Tegmen Tympani ◽

Males And Females ◽

Magnetic Resonance Imaging Mri ◽

The Right ◽

Canal Dehiscence

Abstract Objectives Tegmen tympani dehiscence in temporal multidetector computed tomography (MDCT) and superior semicircular canal dehiscence may be seen together. We investigated superior semicircular canal dehiscence in temporal MDCT and temporal magnetic resonance imaging (MRI). Methods In this retrospective study, 127 temporal MRI and MDCT scans of the same patients were reviewed. In all, 48.8% (n = 62) of cases were male, and 51.2% (n = 65) of cases were female. Superior semicircular canal dehiscence and superior semicircular canal-temporal lobe distance were evaluated by both MDCT and MRI. Tegmen tympani dehiscence was evaluated by MDCT. Results Superior semicircular canal dehiscence was detected in 14 cases (5.5%) by temporal MDCT and 15 cases (5.9%) by temporal MRI. In 13 cases (5.1%), it was detected by both MDCT and MRI. In one case (0.4%), it was detected by only temporal MDCT, and in two cases (0.8%), it was detected by only temporal MRI. Median superior semicircular canal-to-temporal distance was 0.66 mm in both males and females in temporal MDCT and temporal MRI. In both temporal MDCT and temporal MRI, as superior semicircular canal-to-temporal lobe distance increased, the presence of superior semicircular canal dehiscence in temporal MDCT and temporal MRI decreased. Tegmen tympani dehiscence was detected in eight cases (6.3%) on the right side and six cases (4.7%) on the left side. The presence of tegmen tympani dehiscence in temporal MDCT and the presence of superior semicircular dehiscence in MDCT and MRI increased. Conclusion Superior semicircular canal dehiscence was detected by both MDCT and MRI. Due to the accuracy of the MRI method to detect superior semicircular dehiscence, we recommend using MRI instead of MDCT to diagnose superior semicircular canal dehiscence. Moreover, there is no radiation exposure from MRI.

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Dural Contact to the Malleus Head in Patients with Superior Semicircular Canal Dehiscence (SSCD): Case Series and Review of SSCD and Tegmen Defects

Annals of Otology Rhinology & Laryngology ◽

10.1177/00034894211007257 ◽

2021 ◽

pp. 000348942110072

Author(s):

Carissa Wentland ◽

Joseph Cousins ◽

Jason May ◽

Arnaldo Rivera

Keyword(s):

Semicircular Canal ◽

Tertiary Care ◽

Case Series ◽

Superior Semicircular Canal Dehiscence ◽

Superior Semicircular Canal ◽

Tegmen Tympani ◽

Limited Series ◽

Tertiary Care Institution ◽

The Mean ◽

Canal Dehiscence

Objective: Report a series of cases in which patients have concomitant superior semicircular canal dehiscence (SSCD) and a dehiscent tegmen tympani with Dural contact to the malleus head (DCMH). Methods: An analysis of radiologic and audiologic data in 4 patients who presented with SSCD and DCMH at a tertiary care institution. A pertinent literature review was performed. Results: Four patients (5 ears) had SSCD and DCMH. In 3 patients with unilateral DCMH, the mean maximum air-bone gap was 15 dB in the ear with DCMH compared to 50 dB in the ear without DCMH. Of the 5 ears with DCMH, the mean air conduction threshold at 250 Hz was 17 dB compared to 42 dB in the 3 ears without DCMH. Conclusions: We report the findings of DCMH in a series of 4 patients with bilateral SSCD. This limited series suggests that ears with SSCD and DCMH have less of an air-bone gap than would be expected, as 1 would expect an additive effect of DCMH and SSCD on the air-bone gap.

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