Malignant peripheral nerve sheath tumours of the infraorbital nerve: case report and literature review

2008 ◽  
Vol 123 (4) ◽  
pp. 466-470 ◽  
Author(s):  
I Beegun ◽  
I D Bottrill ◽  
K Hollowood
Keyword(s):  
Peripheral Nerve ◽  
World Literature ◽  
Case Reports ◽  
Surgical Excision ◽  
Infraorbital Nerve ◽  
Caucasian Woman ◽  
Magnetic Resonance Imaging Scan ◽  
Nerve Sheath Tumour ◽  
Nerve Sheath ◽  
Peripheral Nerve Sheath Tumour

AbstractObjective:We report a case of malignant peripheral nerve sheath tumour seen in our department.Method:We present case reports and a review of the world literature concerning malignant peripheral nerve sheath tumour.Results:A 38-year-old Caucasian woman was diagnosed with malignant peripheral nerve sheath tumour of the infraorbital nerve. She underwent a wide enbloc resection followed by a course of radiotherapy. A five-year post-operative magnetic resonance imaging scan revealed no evidence of recurrence.Conclusion:Malignant peripheral nerve sheath tumours are rare in the head and neck. An awareness of their occurrence is important for early diagnosis. Management involves: accurate histological diagnosis; radiological imaging to define tumour extent and plan resection; wide surgical excision with histologically negative margins; reconstruction of the tissue defect; and post-operative radiotherapy.

scholarly journals A LARGE MALIGNANT PERIPHERAL NERVE SHEATH (MPNST) OF RADIAL NERVE- A RARE CASE REPORT.

2020 ◽  
pp. 1-3
Author(s):  
Dhanabir Thangjam ◽  
L. Chittaranjan Singh ◽  
Ramthaipou Kamei ◽  
Nehar Sinam ◽  
M. Amitkumar
Keyword(s):  
Peripheral Nerve ◽  
Radial Nerve ◽  
Case Reports ◽  
Neurofibromatosis Type ◽  
Needle Aspiration ◽  
Low Grade ◽  
Nerve Sheath Tumour ◽  
Nerve Sheath ◽  
Rare Case Report ◽  
Peripheral Nerve Sheath Tumour

Malignant peripheral nerve sheath tumour (MPNST) are rare, aggressive sarcomatous tumours of peripheral nerve sheaths which can arise from preexisting neurofibroma or de novo.Sporadic origin accounts for nearly half of all MPNST cases,while other cases occur in association with neurofibromatosis type 1 (NF1).The most common site is nerve trunks of extremities like sciatic nerve. On literature search only four case reports of MPNST of radial nerve are published till date.We report a case of 50 years old lady presenting with a large,firm,ovoid swelling measuring 7 cm x 8 cm over her right arm with symptoms of neuropathy.The fine needle aspiration cytology report was a benign neurogenenic tumour. MRI reported as a radial nerve sheath tumour. Core biopsy shows features of neurofibroma(NF).She was subjected to treatment as a benign pathology but the final histopathological report was a low grade - malignant peripheral nerve sheath tumour.

Malignant peripheral nerve sheath tumour arising in the submandibular gland

2020 ◽  
Vol 13 (11) ◽  
pp. e238110
Author(s):  
Muhammad Ibaad ur rehman Alvi ◽  
Richard Pilkington ◽  
Raguwinder S Sahota ◽  
James Adams
Keyword(s):  
Peripheral Nerve ◽  
Submandibular Gland ◽  
Literature Search ◽  
Case Reports ◽  
Surgical Excision ◽  
High Rate ◽  
Nerve Sheath ◽  
Complete Surgical Excision ◽  
Common Association ◽  
Peripheral Nerve Sheath Tumour

Malignant peripheral nerve sheath tumours (MPNSTs) are tumours that arise from or differentiate towards cells of the peripheral nerve sheath. They are extremely rare with an incidence of 0.001% in the general population. The most common association is with neurofibromatosis 1—an incidence of 5%–42% in this subset of the population is quoted in the literature. These tumours are aggressive with a high rate of local recurrence. Complete surgical excision remains the mainstay of treatment. A literature search found only three case reports of MPNSTs originating in the salivary glands—in all other cases the parotid gland. We present here the first documented case of a patient presented with an MPNST of the submandibular gland managed surgically by a specialty centre.

Malignant tumours as a rare cause of recurrent thrombophlebitis of the great saphenous vein

Phlebologie ◽  
2008 ◽  
Vol 37 (06) ◽  
pp. 297-300
Author(s):  
N. König ◽  
H. J. Stark ◽  
P.-M. Baier
Keyword(s):  
Differential Diagnosis ◽  
Saphenous Vein ◽  
Great Saphenous Vein ◽  
Case Reports ◽  
Malignant Tumours ◽  
Nerve Sheath Tumour ◽  
Below The Knee ◽  
Nerve Sheath ◽  
Unfavourable Prognosis ◽  
Peripheral Nerve Sheath Tumour

SummaryWe present two case reports concerning patients who had to undergone surgical treatment according tp the diagnosis of thrombophlebitis with insufficiency of the greater saphenous vein and putative encapsulated haematoma in the lower left leg area. During the operation we found tumours with urgent suspicion of malignancy. The histological examination revealed the diagnosis of mesenchymal chondrosarcoma and malignant peripheral nerve sheath tumour which are extremely malignant, but very rare neoplasmas with unfavourable prognosis. Conclusion: Since both types of tumours are often located below the knee, phlebotomists and vascular surgeons should take them into account as differential diagnosis.

scholarly journals MRI of malignant peripheral nerve sheath tumour in pericardial cavity

2018 ◽  
pp. bcr-2018-224481
Author(s):  
Ryoma Endo ◽  
Tomoko Tomioka ◽  
Ken Okada ◽  
Kanichi Inoue
Keyword(s):  
Peripheral Nerve ◽  
Nerve Sheath Tumour ◽  
Pericardial Cavity ◽  
Nerve Sheath ◽  
Peripheral Nerve Sheath Tumour

scholarly journals Malignant peripheral nerve sheath tumour of the tongue

2006 ◽  
Vol 42 (5) ◽  
pp. 210-212 ◽  
Author(s):  
Anacélia Mendes Fernandes ◽  
Aline Cristina Batista Rodrigues Johann ◽  
João Batista da Silveira-Júnior ◽  
Maria Cássia Ferreira de Aguiar ◽  
Maria Auxiliadora Vieira do Carmo ◽  
...  
Keyword(s):  
Peripheral Nerve ◽  
Nerve Sheath Tumour ◽  
Nerve Sheath ◽  
Peripheral Nerve Sheath Tumour

scholarly journals Unusual histopathological findings in a young Pekingese dog with intrathoracic malignant peripheral nerve sheath tumour

2009 ◽  
Vol 19 (2) ◽  
pp. 217-220 ◽  
Author(s):  
Omid Dezfoulian ◽  
Sharam Jamshidi ◽  
Masoud Selk Ghaffari ◽  
Maria Tresa Capucchio ◽  
Majid Masoudifard ◽  
...  
Keyword(s):  
Peripheral Nerve ◽  
Nerve Sheath Tumour ◽  
Histopathological Findings ◽  
Nerve Sheath ◽  
Peripheral Nerve Sheath Tumour
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