Complete heart block as a cause of syncope in hypertrocphic cardiomyopathy

1994 ◽  
Vol 4 (1) ◽  
pp. 79-81 ◽  
Author(s):  
Juan Calderón-Colmenero ◽  
Mario Baltazares ◽  
Alfonso Buendía
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Atrioventricular Block ◽  
Right Bundle Branch Block ◽  
Heart Block ◽  
Complete Heart Block ◽  
Conduction Delay ◽  
Complete Atrioventricular Block ◽  
Bundle Branch Block ◽  
The Relationship ◽  
Complete Atrioventricular

SummaryWe report a 12-year-old boy with hypertrophic cardiomyopathy presenting with syncope. His electrocardiogram showed first-degree atrioventricular block, complete right bundle branch block, conduction delay in the anterior fascicle of the left bundle branch, and intermittent complete atrioventricular block. We detected hypertrophic cardiomyopathy in the mother. The relationship between the diseases is discussed, and interpreted in the light of previous descriptions.

Use of terbutaline in the treatment of complete heart block in the fetus

2001 ◽  
Vol 11 (6) ◽  
pp. 683-686 ◽  
Author(s):  
Blair V. Robinson ◽  
José A. Ettedgui ◽  
Frederick S. Sherman
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Atrioventricular Block ◽  
Heart Block ◽  
Complete Heart Block ◽  
Average Rate ◽  
Ventricular Rate ◽  
Initial Increase ◽  
Complete Atrioventricular Block ◽  
Complete Atrioventricular

Between 1989 and 2000, 21 fetuses were diagnosed with complete atrioventricular block. Seven women with fetal ventricular rates of less than 60 were given oral terbutaline, and 6 of these had an initial increase in the fetal ventricular rate. Four fetuses (57%) maintained an increased average rate of 60 beats per minute and survived. Two fetuses returned to rates below 55 and died. The final fetus, with hypertrophic cardiomyopathy, was unresponsive. Terbutaline, therefore, is initially effective in raising the fetal ventricular rate, but this effect may be transient.

scholarly journals Complete Heart Block, Severe Right Ventricular Dysfunction in a Child with COVID-19 Infection

2021 ◽  
pp. 1-10
Author(s):  
Sezen Gulumser Sisko ◽  
Sezen Ugan Atik ◽  
Cem Karadeniz ◽  
Alper Guzeltas ◽  
Yakup Ergul
Keyword(s):  
Atrioventricular Block ◽  
Heart Block ◽  
Ventricular Dysfunction ◽  
Complete Heart Block ◽  
Pacemaker Implantation ◽  
Right Ventricular Dysfunction ◽  
Right Heart Failure ◽  
Complete Atrioventricular Block ◽  
Right Heart ◽  
Complete Atrioventricular

Abstract A young child presented with hepatomegaly, ascites, and bradycardia in the setting of coronavirus disease-2019. Permanent complete atrioventricular block and severe right heart failure were diagnosed. He was treated with surgical epicardial pacemaker implantation. This report is the first description of coronavirus disease-2019–induced permanent complete atrioventricular block in a child.

Successful management of fetal hydrops due to congenitally complete atrioventricular block

2003 ◽  
Vol 13 (4) ◽  
pp. 380-383 ◽  
Author(s):  
Jacintha Sivarajah ◽  
Ian C. Huggon ◽  
Eric Rosenthal
Keyword(s):  
Preterm Delivery ◽  
Atrioventricular Block ◽  
Heart Block ◽  
Complete Heart Block ◽  
Complete Atrioventricular Block ◽  
Successful Management ◽  
Fetal Hydrops ◽  
Complete Atrioventricular

At 32 weeks, a fetus was found to be hydropic with congenitally complete heart block in an asymptomatic mother who was positive to anti-Ro antibodies. Maternal therapy with oral salbutamol was successful in prolonging gestation for a period of 3 weeks so that preterm delivery was delayed until the 35th week of gestation. Following treatment with inotropes and diuretics, a permanent transvenous pacemaker was implanted at 8 weeks of age. The child is now thriving at 20 months of age.

scholarly journals Cardiomyopathie hypertrophique avec bloc auriculo-ventriculaire masqué. Rapport de 2 cas

2021 ◽  
Vol 8 (1) ◽  
pp. 88-91
Author(s):  
Hanane Zouzou ◽  
◽  
Fatseh Mohamedi ◽  
Imed Alloune ◽  
Hinda Bourmouche ◽  
...  
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Atrioventricular Block ◽  
Accessory Pathway ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Outflow Tract ◽  
Complete Atrioventricular Block ◽  
Bundle Branch Block ◽  
Refractory Heart Failure ◽  
Complete Atrioventricular

Background. Hypertrophic cardiomyopathy is the most common genetic cardiac disorder in Algeria, although syncope is often caused by ventricular arrhythmias or left outflow tract obstruction, it may also be related to complete atrioventricular block; the latter is rarely reported in the literature, the diagnosis is not so obvious, and should be thoroughly researched in presence of syncope. We report two cases of patients with hypertrophic cardiomyopathy and atrioventricular block revealed by syncope. Cases’ presentation. We reported two patients who presented hypertrophic cardiomyopathy, with recurrent syncope; one patient presented an accessory pathway that masked the complete atrioventricular block and the other patient presented an alternating occurrence of right bundle branch block and left bundle branch block at the ECG monitoring over a 48 hour. Echocardiography showed hypertrophy of left ventricular walls, but no left ventricular outflow tract gradient was detected. Extensive fibrosis especially in the septum was detected by late gadolinium enhancement. The two patients were implanted with dual-chamber pacemakers. During follow-up, one patient had developed refractory heart failure and died in 2014. Conclusions. The accessory pathway may mask complete atrioventricular block, also alternating bundle branch block could be the only proof of complete atrioventricular block. Fibrosis is the principal substrate of the reentry phenomenon, but septal fibrosis can also damage the atrioventricular conduction system. Non-obstructive hypertrophic cardiomyopathy could be related to fibrosis, and/or asynchrony. Keywords: Convulsive Syncope, Sudden Cardiac Death, Alternating Bundle Branch Block, Accessory Pathway.

scholarly journals Bloqueo auriculoventricular fetal completo: enfoque diagnóstico y terapéutico; reporte de caso en Bogotá, Colombia y revisión de la literatura

2017 ◽  
Vol 68 (4) ◽  
pp. 305
Author(s):  
Diana Cecilia Poveda-Rojas ◽  
Natalia Vélez-Tirado ◽  
Leonardo Bonilla-Cortes ◽  
Juan Pablo Rozo-Galindo
Keyword(s):  
Atrioventricular Block ◽  
Heart Block ◽  
Complete Heart Block ◽  
Complete Atrioventricular Block ◽  
Congenital Complete Heart Block ◽  
Para Determinar ◽  
Complete Atrioventricular ◽  
Hospital General

Objetivo: reportar un caso de bloqueo auriculoventricular completo congénito y realizar una revisión de la literatura del diagnóstico y tratamiento.Materiales y métodos: se reporta el caso de una gestante de 27 años quien consulta a un hospital general de alto nivel de complejidad, con un embarazo de 33 semanas, con feto único, con diagnóstico de bloqueo auriculoventricular completo y cardiomiopatía dilatada secundaria. Se inició manejo prenatal con betamimético con pobre respuesta, por lo cual fue necesario finalizar el embarazo. El recién nacido requiere implantación de marcapasos ventricular en el primer día de vida con excelentes resultados en el seguimiento a un año. Se realiza revisión de la literatura  publicada en las bases de datos: Medline vía PubMed, Lilacs y SciELO mediante los términos: “fetal complete atrioventricular block”, “congenital complete heart block”, con límites de año de 2000 a 2016, en español e inglés.Resultados: se obtuvieron 21 publicaciones; siete reportes de caso, diez revisiones de literatura, cuatro estudios de cohorte. El diagnóstico se basa en la ecocardiografía fetal para determinar el intervalo PR, la relación auriculoventricular y la detección de anomalías intracardiacas, entre las que se encuentran: regurgitación valvular, hiperecogenicidad miocárdica/valvular-fibroelastosis endocárdica, contracciones atriales prematuras y efusión pericárdica. Respecto al tratamiento prenatal, los medicamentos más utilizados son los corticoesteroides y los betamiméticos. El tratamiento de la bradiarritimia severa refractaria neonatal puede requerir la implantación de un marcapaso como manejo definitivo.Conclusión: el bloqueo AV congénito de tercer grado requiere diagnóstico temprano y tratamiento oportuno, ya que se acompaña de alta morbimortalidad perinatal. Se requieren estudios con mayor calidad metodológica que permitan avalar otras opciones y esquemas terapéuticos prometedores.

The Association Between Cardio-Ankle Vascular Index and Primary Idiopathic Complete Atrioventricular Block in an Elderly Population

Angiology ◽  
2021 ◽  
pp. 000331972110287
Author(s):  
Turhan Turan ◽  
Faruk Kara ◽  
Selim Kul ◽  
Muhammet Rasit Sayın ◽  
Sinan Sahin ◽  
...  
Keyword(s):  
Arterial Stiffness ◽  
Atrioventricular Block ◽  
Elderly Population ◽  
Complete Atrioventricular Block ◽  
Age Related ◽  
And Gender ◽  
The Relationship ◽  
Block Frequency ◽  
Complete Atrioventricular ◽  
Relevant Factors

The most common cause of complete atrioventricular block (CAVB) is age-related fibrotic degeneration and is referred to as primary idiopathic complete atrioventricular block (iCAVB). This study aims to investigate the relationship between iCAVB and arterial stiffness using the cardio-ankle vascular index (CAVI). In this study, of 205 CAVB patients, 41 patients with iCAVB implanted with a dual-chamber permanent pacemaker and 40 age- and gender-matched controls were studied. Arterial stiffness was assessed by a VaSera VS-1000 CAVI instrument. The CAVI values of patients with iCAVB were significantly higher compared with the controls (9.63 ± 1.42 vs 8.57 ± 1.12, P < .001). Idiopathic complete atrioventricular block frequency was higher among patients with abnormal CAVI values than those with borderline and normal CAVI ( P = .04). In multivariate analysis, only CAVI was an independent predictor of iCAVB after adjusting for other relevant factors (odds ratio, 2.575; 95% CI [1.390-4.770]; P = .003). The present study demonstrated that CAVI, as a marker of arterial stiffness, was increased among elderly patients with iCAVB. Thus, we provide a possible additional mechanism linking easily measured CAVI with iCAVB.

scholarly journals Transient Congenital Complete Heart Block: A Case Report

Children ◽  
2021 ◽  
Vol 8 (9) ◽  
pp. 790
Author(s):  
Ying-Tzu Ju ◽  
Yu-Jen Wei ◽  
Ming-Ling Hsieh ◽  
Jieh-Neng Wang ◽  
Jing-Ming Wu
Keyword(s):  
Heart Block ◽  
Rare Case ◽  
Complete Heart Block ◽  
Normal Sinus Rhythm ◽  
Structural Heart Disease ◽  
Normal Heart ◽  
Complete Atrioventricular Block ◽  
Normal Sinus ◽  
Congenital Complete Heart Block ◽  
Complete Atrioventricular

Congenital complete heart block is defined as a complete atrioventricular block occurring prenatally, at birth, or within the first month of life. Congenital complete heart block has a high mortality rate, and in infants with normal heart morphology, it is often associated with maternal connective tissue disease. In these latter cases, neonatal congenital complete heart block is usually irreversible. We present a rare case of a female neonate who had bradycardia noted at a gestational age of 37 weeks. Her mother had no autoimmune disease history. She had no structural heart disease, and the serology surveys for autoantibodies including SSA/Ro and SSB/La were all negative. Without intervention or medication, her congenital complete heart block completely recovered to a normal sinus rhythm within 5 days. The cause of the transient congenital complete heart block was unknown in this case.

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