Audiological Features in 63 Patients With Cochlear Nerve Deficiency

2021 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Kazuki Matsuura ◽  
Hidekane Yoshimura ◽  
Jun Shinagawa ◽  
Masahiro Kurozumi ◽  
Yutaka Takumi
2013 ◽  
Vol 149 (2) ◽  
pp. 318-325 ◽  
Author(s):  
Clarice S. Clemmens ◽  
Jessica Guidi ◽  
Aviva Caroff ◽  
Samuel J. Cohn ◽  
Jason A. Brant ◽  
...  

2012 ◽  
Vol 13 (1) ◽  
pp. 16-25 ◽  
Author(s):  
Peter Roland ◽  
Kathryn Henion ◽  
Timothy Booth ◽  
Julia Dee Campbell ◽  
Anu Sharma

2014 ◽  
Vol 151 (1_suppl) ◽  
pp. P93-P93
Author(s):  
Giacomo Colletti ◽  
Marco Mandala ◽  
Liliana Colletti ◽  
Vittorio Colletti

2011 ◽  
Vol 121 (9) ◽  
pp. 1979-1988 ◽  
Author(s):  
Craig A. Buchman ◽  
Holly F. B. Teagle ◽  
Patricia A. Roush ◽  
Lisa R. Park ◽  
Debora Hatch ◽  
...  

2012 ◽  
Vol 76 (8) ◽  
pp. 1188-1195 ◽  
Author(s):  
Zhihua Zhang ◽  
Yun Li ◽  
Lingxiang Hu ◽  
Zhaoyan Wang ◽  
Qi Huang ◽  
...  

2019 ◽  
Vol 128 (6) ◽  
pp. 485-489
Author(s):  
Brian William Herrmann ◽  
Campbell R. Hathaway ◽  
Michael Fadell

Objective: To identify and characterize hearing loss (HL) in children with septo-optic dysplasia (SOD). Methods: Otologic and audiometric data for patients less than 18 years of age identified as having SOD who were seen in the Children’s Healthcare of Atlanta-Scottish Rite Hospital clinic between 2013 and 2017 were collected and reviewed through a HIPAA-compliant medical record search. Relevant literature was also reviewed with the assistance of Medline. Results: Sixty-four patients with SOD were identified, and 7 of those patients (10.9%) were diagnosed with hearing loss. Type of hearing loss was sensorineural (SNHL) in 5 patients (63%), mixed (MHL) in 1(14%), and conductive (CHL) in 1(14%). Bilateral loss presented in 60% (3/5) of SNHL patients, while the rest demonstrated unilateral loss. Unilateral findings included cochlear nerve deficiency (1) and atresia/microtia (1). Tympanostomy tubes were required in 57% (4/7) of SOD children with hearing loss. Amplification was successfully implemented in 86% (6/7). Conclusions: Hearing loss was found in nearly 11% of SOD children, and SNHL was identified as (63%) the predominant form of loss. To our knowledge, this is the first retrospective review of hearing loss in a pediatric SOD cohort and the first to report of cochlear nerve deficiency and atresia/microtia in this population. Based on these findings, early identification of hearing loss with imaging when appropriate and treatment of otitis in this population is recommended.


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