scholarly journals Desmoplastic Fibroma of the Left 6th Rib in a 35-year-old Man: a Case Report and Literature Review

Author(s):  
Kai Zhang ◽  
Wu Weibin ◽  
Guan Jiexia ◽  
Wu Yonghui ◽  
Chen Huiguo ◽  
...  

Abstract Background: Desmoplastic fibroma (DF) is a rare, benign tumor. The most common sites are the long tubular bones and mandible. Although generally considered a benign tumor, it can invade surrounding tissues and has a high rate of local recurrence after incomplete surgical excision. However, there is currently no stantard treatment. Here we present a novel case of DF in the left 6th rib in a 35-year-old man.Case presentation: The man presented to our center with left chest pain and swelling. Enhanced computed tomography (CT) showed a 4.5×2.0 cm mass on the left 6th rib with pathological fracture. Wide resection was performed. Open biopsy revealed that the tumor destroyed medullary cavity and partially broke through the bone cortex. Pathologically, the tumor was composed of spindle-shaped cells arranging in a woven pattern on a backgroung of abundant collagenous fiber. No β-catenin were detected. Based on the pathological and radiological findings, a final diagnosis of DF was made. No postoperative adjuvant treatments were administerded. Fortunately, there was no evidence of recurrence 22 months after surgery. Conclusions: DF originated from rib is a kind of extremly rare benign tumor but locally aggressive and show unique biologically features. Wide resection or total resection can effectively reduce the risk of local recurrence when compared with curettage. Rarity of the tumor favors documentation in literature.

2021 ◽  
Author(s):  
Kai Zhang ◽  
Wu Weibin ◽  
Guan Jiexia ◽  
Wu Yonghui ◽  
Chen Huiguo ◽  
...  

Abstract Background: Desmoplastic fibroma (DF) is a rare, benign tumor. The most common sites are the long tubular bones and mandible. Although generally considered a benign tumor, it can invade surrounding tissues and has a high rate of local recurrence after incomplete surgical excision. However, there is currently no stantard treatment. Here we present a novel case of DF in the left 6th rib in a 35-year-old man.Case presentation: The man presented to our center with left chest pain and swelling. Enhanced computed tomography (CT) showed a 4.5×2.0 cm mass on the left 6th rib with pathological fracture.Wide resection was performed. Open biopsy revealed that the tumor destroyed medullary cavity and partially broke through the bone cortex. Pathologically, the tumor was composed of spindle-shaped cells arranging in a woven pattern on a backgroung of abundant collagenous fiber. No β-catenin were detected. Based on the pathological and radiological findings, a final diagnosis of DF was made. No postoperative adjuvant treatments were administerded. Fortunately, there was no evidence of recurrence 22 months after surgery. Conclusions: DF originated from rib is a kind of extremly rare benign tumor but locally aggressive and show unique biologically features. Wide resection or total resection can effectively reduce the risk of local recurrence when compared with curettage. Rarity of the tumor favors documentation in literature.


2016 ◽  
Vol 106 (1) ◽  
pp. 76-78
Author(s):  
Nathalia Doobay ◽  
Jason Mallette

Eccrine syringofibroadenoma is a rare, benign tumor of eccrine ductal differentiation, typically presenting in the extremities. Herein we report a case of a 77-year-old man with pain in the lateral midfoot and the presence of an eccrine syringofibroadenoma lesion in the lateral heel. On surgical excision of the lesion, the foot pain promptly resolved, and at the most recent follow-up visit, the patient remained pain free.


2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Anastasija Arechvo ◽  
Svajunas Balseris ◽  
Laura Neverauskiene ◽  
Irina Arechvo

Tumors originating from ceruminous glands are rare lesions of the external auditory canal. The lack of specific clinical and radiological signs makes their diagnosis challenging. We report the case of an exceptionally rare benign tumor, a syringocystadenoma papilliferum (SCAP), in an atypical location in the bony segment of the external auditory canal with uncommon clinical signs. The special traits of the case included the following: the most lateral component of the tumor was macroscopically cystic and a granular myringitis with an obstructing keratin mass plug was observed behind the mass. The clinical, audiological, radiological, and histological characteristics of the neoplasm are consequently presented. Intraoperative diagnosis of the epidermal cyst was proposed. The final diagnosis of SCAP was determined only by histological analysis after the surgical excision. The educational aspects of the case are critically discussed.


Author(s):  
Adil Eabdenbtsen ◽  
Mohammed Mouzouri ◽  
Ahlam Bellouchi ◽  
Noureddine Oulali ◽  
Mohammed Bouziane ◽  
...  

Introduction : The odontogenic myxoma is a rare benign tumor of the maxilla, whose clinical and radiological manifestations are variable and nonspecific and can be confused with other radiolucent lesions. Its origin would be the embryonic mesenchyme of the dental follicle.Case report : We report the case of odontogenic myxoma of the right maxilla, discovered by chance in a 25 year old patient. Clinically, the patient had painless, firm on palpation, swelling of the right maxilla, impeding chewing and speech. Facial CT-scan showed an expansive osteolytic process blowing the right maxilla off. A biopsy was in favor of an odontogenic myxoma. The diagnosis was based on clinical, radiological and especially anatomopathological arguments.Conclusion : The local aggressiveness of the odontogenic myxoma and its high rate of recurrence justify a radical treatment beyond the lesion’s boundaries and thus imply a postoperative repair.


Cureus ◽  
2021 ◽  
Author(s):  
Bappy Basak ◽  
Alexander Haragan ◽  
Michael Shackcloth ◽  
Joyce Thekkudan

2016 ◽  
Vol 6 (12) ◽  
pp. 1043-1045
Author(s):  
P Poudel ◽  
B Bajracharya ◽  
S Bhattacharya ◽  
D Bajracharya ◽  
S Singh ◽  
...  

Odontogenic myxofibroma is a rare, benign tumor, which is considered to be the variant of odontogenic myxoma. It is locally infiltrative, aggressive and has high recurrence rate. Only 24 specific cases of myxofibroma have been reported since 1950 and only two cases have been reported with excessive calcifications till 2012. Here, we report a rare case of Odontogenic myxofibroma with calcifications in 53 years old female patient who presented with the chief complain of swelling. The final diagnosis of Odontogenic myxofibroma was established after histopathological and immunohistochemical examination.


2007 ◽  
Vol 121 (8) ◽  
pp. 786-789 ◽  
Author(s):  
T Wilson ◽  
H B Hellquist ◽  
S Ray ◽  
J Pickles

AbstractWe present a case report of a patient who developed a sinonasal myopericytoma treated by surgical excision through a lateral rhinotomy. Some aggressive features on pre-operative computed tomography scanning and the complexity of recent changes in the histological nomenclature for these tumours led to consideration of adjuvant therapy. The close histological relationship between myopericytoma, myofibromatosis, solitary myofibroma and infantile haemangiopericytoma is discussed. This group of lesions constitute a single morphological spectrum with differentiation towards perivascular myoid cells (pericytes). Currently myopericytoma is the most appropriate and accepted term embracing all these entities. A review of the literature has been reassuring in identifying these tumours as benign but with a reasonably high rate of local recurrence (17 per cent). The treatment of choice is surgical excision with further excisions for local recurrence.


2020 ◽  
Vol 8 ◽  
pp. 2050313X2098146
Author(s):  
Kyuin Lee ◽  
Yoon Jung Choi ◽  
Hyun Seung Choi ◽  
Junhui Jeong

Osteoma of the external auditory canal is a rare benign tumor with an estimated incidence of 0.05% of total otologic surgeries. In most cases, an osteoma in the external auditory canal does not cause symptoms because the tumor grows slowly and does not occlude the ear canal. However, if the mass grows to occlude the external auditory canal, several symptoms can occur, including conductive hearing loss, aural fullness, and keratin debris accumulation. We present two cases of this rare tumor in a 23-year-old woman and a 19-year-old man. The mass was surgically excised at the level of the peduncle under local anesthesia with microscope assistance. The base of the excised mass was drilled with a diamond burr to remove all osseous lesions. Histopathologic findings showed spongiotic osteomas. In these cases, patients had symptoms of aural fullness, although the osteomas did not completely occlude the external auditory canal, and the symptoms improved after surgical excision without recurrence.


1997 ◽  
Vol 111 (7) ◽  
pp. 669-670 ◽  
Author(s):  
Ramesh Chandran Ramanathan ◽  
J. Meirion Thomas

AbstractInfantile fibromatosis, one of the fibrous tumours of infancy and childhood, is a fibroproliferative lesion characterized by aggressive local invasion without any tendency to metastasize, the absence of cytological evidence of malignancy and a high rate of local recurrence when incompletely excised. We report a case of infantile (desmoid-type) fibomatosis in a seven-year-old girl arising from the deep lobe of the parotid gland that was treated by complete surgical excision with preservation of the facial nerve. The clinical features, pathology and treatment are briefly discussed.


2020 ◽  
Vol 8 (9) ◽  
pp. 941-944
Author(s):  
Zahra Sayad ◽  
◽  
Bouchra Dani ◽  
Malik Boulaadas

Introduction: The infraorbital schwannoma or neuroma is a rare benign tumor of the orbit. Its clinical and radiological presentation is not very specific. Its diagnosis is essentially histological. Observation: We report the case of a 46-year-old woman, diabetic under treatment, consulting for an irreducible, non-axial and non-pulsatile exophthalmos. Clinical examination of the left eye found visual acuity corrected to 8/10 without limitation of ocular motility or diplopia. The examination of the right eye is unremarkable.The orbital CT objectified a mass measuring 25.3mm × 13.8mm, homogeneous of the floor of the left orbit, pushing the eyeball up and out. The orbital floor was pushed inferiorly by the mass however, its integrity was preserved. Tumor excision was performed via the sub-ciliary cutaneous incision with reconstruction of the floor by an iliac crest graft. The histological analysis allowed us to have a definite diagnosis of schwannoma. Conclusion:The schwannoma is a rare tumor of the orbit. Its diagnosis is established solely by anatomopathological study of the operative specimen. Its treatment is based on a complete surgical excision to avoid any recurrence.


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