Aberrant origin of the left pulmonary artery, congenital tracheal stenosis and ring-sling complex (part I)

2018 ◽  
Vol 19 (1) ◽  
pp. 14-27
Author(s):  
V.V. Bazylev ◽  
A.E. Chernogrivov ◽  
I.E. Chernogrivov
Keyword(s):  
Pulmonary Artery ◽  
Tracheal Stenosis ◽  
Left Pulmonary Artery ◽  
Congenital Tracheal Stenosis ◽  
Complex Part

The evolution of the pulmonary arterial sling syndrome, with particular reference to the need for reoperations because of untreated tracheal stenosis

2009 ◽  
Vol 19 (5) ◽  
pp. 446-450 ◽  
Author(s):  
Tsvetomir S. Loukanov ◽  
Christian Sebening ◽  
Wolfgang Springer ◽  
Siegfried Hagl ◽  
Matthias Karck ◽  
...  
Keyword(s):  
Cardiopulmonary Bypass ◽  
Pulmonary Artery ◽  
Tracheal Stenosis ◽  
Left Pulmonary Artery ◽  
Tracheobronchial Tree ◽  
Tracheal Resection ◽  
Computer Tomography Angiography ◽  
Pulmonary Arterial ◽  
The Mean

AbstractBackgroundWe present a group of infants and children with pulmonary arterial sling and tracheal stenosis. In some of the patients, the anomalously located pulmonary artery had previously been reimplanted, but without simultaneous repair of the trachea.MethodsFrom 1992 to 2007, we reimplanted the left pulmonary artery in 13 children with a pulmonary arterial sling. Their median age was 8 months, with a range from 1 to 72 months. We also performed tracheal resection with end-to-end anastomosis, or complex tracheal reconstructions. In 5 patients, the reoperation was indicated because of persistent tracheal stenosis not treated initially at first correction of the arterial sling. All patients presented with stridor and respiratory distress. Cardiac catheterization, bronchoscopy and multidetecting computer tomography angiography were performed in all cases prior to the operation. All operations were performed under cardiopulmonary bypass.ResultsThere was no operative or late mortality. The patients were extubated under bronchoscopic control. The mean period of intubation was 18 plus or minus 8 days, and the average follow-up was 8 plus or minus 4 years. The patients showed no signs of tracheal re-stenosis clinically or on bronchoscopy. The group of the patients under reoperations, however, required longer periods of intubation and hospitalization.ConclusionOur experience demonstrates that, in patients with a pulmonary arterial sling, any associated tracheal stenosis should be explored at the initial operation, since decompression of the trachea by reimplanting the anomalously located pulmonary artery fails to provide relief. The funnel trachea, if present, undergoes progressive stenosis, and will require surgical repair. The use of cardiopulmonary bypass permitted extensive mobilization of the tracheobronchial tree, and allowed us to perform a tension-free anastomotic reconstruction of the trachea.

Single Stage Repair of Tetralogy of Fallot Associated With Left Pulmonary Artery Sling and Tracheal Stenosis

2013 ◽  
Vol 28 (5) ◽  
pp. 595-598 ◽  
Author(s):  
Ajeya Joshi ◽  
Saket Agarwal ◽  
Satish Kumar Aggarwal ◽  
Vishnu Datt ◽  
G. R. Sethi ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Tracheal Stenosis ◽  
Left Pulmonary Artery ◽  
Single Stage ◽  
Pulmonary Artery Sling ◽  
Left Pulmonary Artery Sling

Anomalous Origin of the Right Pulmonary Artery From the Aorta and Congenital Tracheal Stenosis: Staged Repair in a Neonate

2021 ◽  
pp. 215013512110493
Author(s):  
Nguyen L.T. Truong ◽  
Tran Q. Vinh ◽  
Nguyen T. Mai
Keyword(s):  
Pulmonary Artery ◽  
Tracheal Stenosis ◽  
Neonatal Period ◽  
Ascending Aorta ◽  
Anomalous Origin ◽  
Congenital Tracheal Stenosis ◽  
Unique Case ◽  
Right Pulmonary Artery ◽  
Rare Malformation ◽  
The Right

Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA), sometimes referred to as hemitruncus, is a rare malformation. We report a unique case of AORPA associated with Ebstein's anomaly and with congenital tracheal stenosis due to complete tracheal rings. The AORPA and tracheal stenosis were both successfully corrected in the neonatal period.

Pulmonary artery sling and congenital tracheal stenosis in another patient with Mowat–Wilson syndrome

2007 ◽  
Vol 143A (13) ◽  
pp. 1528-1530 ◽  
Author(s):  
Sibylle Strenge ◽  
Wolfram Heinritz ◽  
Christiane Zweier ◽  
Anita Rauch ◽  
Udo Rolle ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Tracheal Stenosis ◽  
Congenital Tracheal Stenosis ◽  
Pulmonary Artery Sling

Aortotracheal Fistula after Slide Tracheoplasty in a Patient with Dextrocardia, Left Pulmonary Artery Sling and Tracheal Stenosis: A Case Report

2021 ◽  
Author(s):  
Yu-san Chien ◽  
Yen-Chun Chao ◽  
Kuo-Sheng Lee ◽  
Kung-hong Hsu
Keyword(s):  
Pulmonary Artery ◽  
Tracheal Stenosis ◽  
Circulatory Arrest ◽  
Aortic Surgery ◽  
Left Pulmonary Artery ◽  
Laser Vaporization ◽  
Recurrent Bleeding ◽  
Pulmonary Artery Sling ◽  
Slide Tracheoplasty ◽  
Left Pulmonary Artery Sling

Abstract Background: Aortotracheal fistula (ATF) is an uncommon and fatal complication of tracheal or aortic surgery, especially among pediatric patients. Case presentation: We reported a case in a 1-year-old boy with dextrocardia, left pulmonary artery sling and long segment tracheal stenosis. He received slide tracheoplasty at 9 months of age and had post-operative refractory granulation at distal trachea status post repeated balloon dilatation and laser vaporization. Episodes of hemoptysis occurred on post-operative day 81. Bronchoscopy revealed a pulsating pseudoaneurysm at lower trachea which ruptured during the procedure. Urgent surgical repair under cardiopulmonary bypass with deep hypothermic circulatory arrest was done. No recurrent bleeding or significant neurologic deficits noticed at a 4-month follow-up. Conclusion: Congenital anomaly that changes the spatial relationship between trachea and aorta could have contributed to formation of ATF. This warrant future attention when managing tracheal granulation with this not uncommon anatomy.

Heliox as the Rescue Therapy for a Neonate with Congenital Tracheal Stenosis, Pulmonary Artery Sling, and Intracardiac Anomalies

2008 ◽  
Vol 26 (05) ◽  
pp. 357-360 ◽  
Author(s):  
Ming-Horng Tsai ◽  
Kin-Sun Wong ◽  
Reyin Lien ◽  
Hsuan-Rong Huang ◽  
Sui-Ling Liao ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Tracheal Stenosis ◽  
Rescue Therapy ◽  
Congenital Tracheal Stenosis ◽  
Pulmonary Artery Sling

A Case of Pulmonary Artery Sling Anomaly with Tracheal Stenosis and Management of Difficult Airway

2020 ◽  
Author(s):  
Emine G. Torun ◽  
Mutlu U. Yazıcı ◽  
Ebru Azapağası ◽  
Utku A. Örün ◽  
Hasibe G. Çınar ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Difficult Airway ◽  
Tracheal Stenosis ◽  
Pediatric Intensive Care ◽  
Male Infant ◽  
Left Pulmonary Artery ◽  
High Morbidity ◽  
Pulmonary Artery Sling ◽  
Vascular Abnormality ◽  
Pulmonary Sling

AbstractPulmonary artery sling is a rare congenital vascular abnormality, where the left pulmonary artery originates from the right pulmonary artery, passes between trachea, and esophagus and reaching the left hilum. Cough, wheezing, and difficulty in feeding are three major symptoms. Untreated pulmonary sling carries high morbidity and mortality, most of which is due to the airway and other associated anomalies. Herein, we report a 40-day-old male infant who admitted to the pediatric intensive care unit with progressive respiratory distress and diagnosed with left pulmonary sling with tracheal stenosis. We discuss the diagnosis and management of pulmonary artery sling and present the successful use of laryngeal mask in difficult airway management.

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