scholarly journals Sudden Sensorineural Hearing Loss Associated with the Presence of a Vascular Loop in the Internal Auditory Canal. Case Report

2021 ◽  
Vol 26 (3) ◽  
pp. 65-66
Author(s):  
Simona Șerban ◽  
Arthur Weisman
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Internal Auditory Canal ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Type Ii ◽  
Depth Of Penetration ◽  
Cerebellar Artery ◽  
Radiological Classification ◽  
Vascular Loop

Abstract The vascular loop refers to a trajectory abnormality of the antero-inferior cerebellar artery or its branch in the internal auditory canal. The Chavda radiological classification identifies three types of trajectory depending on the depth of penetration of the loop at the level of the internal auditory canal. The article presents the case of a 26-year-old patient admitted to the ENT department for left ear sudden sensorineural hearing loss and dizziness. The 3D Fiesta-C axial sequence MRI shows the presence of the vascular loop inside the internal auditory canal, without exceeding half of it. The hearing loss had an unfavourable evolution, without recovery after treatment with steroids and vasodilators. Sudden sensorineural hearing loss may be a consequence of the presence of the vascular loop in the internal auditory canal. The prognosis for recovery from hearing loss is poor if the loop is at least type II.

Hypertrophic Pachymeningitis of the Internal Auditory Canal: A Rare Case of Unilateral Sudden Sensorineural Hearing Loss

2018 ◽  
Vol 127 (9) ◽  
pp. 649-652 ◽  
Author(s):  
Thomas Muelleman ◽  
Hannah Kavookjian ◽  
James Lin ◽  
Hinrich Staecker
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Internal Auditory Canal ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
High Dose ◽  
Hypertrophic Pachymeningitis ◽  
Eighth Cranial Nerve ◽  
Mri Scans ◽  
Magnetic Resonance Imaging Mri

Objectives: To describe and increase awareness of a rare cause of unilateral sudden sensorineural hearing loss. Methods: Case report and literature review. Results: We present a 66-year-old female who suffered left-sided sudden sensorineural hearing loss and dizziness. Diagnostic magnetic resonance imaging (MRI) did not reveal masses or lesions along the eighth cranial nerve or in the inner ear. Upon eventual referral to neurotology clinic, hypertrophic pachymeningitis of her left internal auditory canal and adjacent middle and posterior fossa dura were identified. The ensuing laboratory workup for autoimmune and infectious etiology revealed mild elevation of ACE 93 (9-67) but otherwise normal results. Conclusions: Idiopathic hypertrophic pachymeningitis is a diagnosis of exclusion. Neoplastic, infectious, and autoimmune causes must be ruled out. The prevailing treatment for this condition is high-dose corticosteroids. This entity should be considered when evaluating MRI scans obtained in the setting of sudden sensorineural hearing loss.

Candidate Genes of Cerebrovascular Disease and Sudden Sensorineural Hearing Loss

2009 ◽  
Vol 16 (5) ◽  
pp. 559-562 ◽  
Author(s):  
Jae-Young Um ◽  
Chul-Ho Jang ◽  
Kyu-Yeob Kim ◽  
Su-Jin Kim ◽  
Na-Hyung Kim ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Cerebrovascular Diseases ◽  
Artery Occlusion ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Anterior Inferior Cerebellar Artery ◽  
Cerebellar Artery ◽  
Tnf Α ◽  
Auditory Dysfunction

Auditory dysfunction is related to large/small vessel occlusions and hemorrhage. Sudden sensorineural hearing loss (SSNHL) frequently occurs with anterior inferior cerebellar artery occlusion proximal to the internal auditory artery. Moreover, SSNHL has various pathogenetic mechanisms, the main proposed mechanisms being vascular disease, membrane ruptures, infection, and autoimmunity. Tumor necrosis factor (TNF) is an important cytokine in the inflammation process of cerebrovascular diseases. In the current study, the possible effects of polymorphisms in TNF-α and TNF-β genes on SSNHL are evaluated. Two genetic polymorphisms in the TNF locus (TNF-α —308 G - ->A and TNF-β +252 A - ->G) were investigated as risk factors for SSNHL by determining their prevalence in 97 SSNHL patients and in 587 controls. A significant increase was found for the TNF-β allele 1 in SSNHL patients compared with the controls (χ 2 = 7.251, P = .007, odds ratio [OR] = 1.534, confidence interval [CI] = 1.12-2.10). These findings suggest that the TNF-β +252 locus plays an important role in the etiopathogenesis of SSNHL.

scholarly journals Sudden Sensorineural Hearing Loss as Prodromal Symptom of Anterior Inferior Cerebellar Artery Infarction

ORL ◽  
2011 ◽  
Vol 73 (3) ◽  
pp. 137-140 ◽  
Author(s):  
Francesco Martines ◽  
Francesco Dispenza ◽  
Cesare Gagliardo ◽  
Enrico Martines ◽  
Daniela Bentivegna
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Prodromal Symptom ◽  
Anterior Inferior Cerebellar Artery ◽  
Cerebellar Artery

scholarly journals Intracochlear Hemorrhage: A Rare Cause of Sudden Sensorineural Hearing Loss

2021 ◽  
Vol 2021 ◽  
pp. 1-4
Author(s):  
Myriam Jrad ◽  
Haifa Zlitni ◽  
Miriam Boumediene ◽  
Atef Ben Nasr ◽  
Meriem Bouzrara
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Internal Auditory Canal ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Lower Intensity ◽  
Fluid Attenuated Inversion Recovery ◽  
3D Sequence ◽  
The Right ◽  
The Brain

Inner ear hemorrhage is an extremely rare cause of sudden sensorineural hearing loss with few cases reported in the literature. We report the case of a 30-year-old male who presented with a sudden left ear hearing loss, with no tinnitus nor vertigo. The audiogram revealed a profound left sensorineural hearing loss. An MRI of the brain and internal auditory canal was performed 3 weeks after and revealed an increased signal intensity on T1-weighted (T1W) and T2 fluid-attenuated inversion recovery (FLAIR) images in the left cochlea. No other abnormalities were found, in particular no enhancement after intravenous administration of gadolinium. The CISS 3D sequence showed a signal of discreetly lower intensity in the left cochlea compared to the right one. The diagnosis of intracochlear hemorrhage was made. No improvement of the hearing loss has been noted after medical treatment and hyperbaric oxygen therapy.

scholarly journals Anatomical and Pathological Findings of Magnetic Resonance Imaging in Idiopathic Sudden Sensorineural Hearing Loss

2020 ◽  
Vol 24 (4) ◽  
pp. 198-203
Author(s):  
Min Bum Kim ◽  
Jihyun Lim ◽  
Il Joon Moon
Keyword(s):  
Magnetic Resonance Imaging ◽  
Hearing Loss ◽  
Magnetic Resonance ◽  
Sensorineural Hearing Loss ◽  
Inner Ear ◽  
Internal Auditory Canal ◽  
Sudden Sensorineural Hearing Loss ◽  
Cochlear Nerve ◽  
Sensorineural Hearing ◽  
Resonance Imaging

Background and Objectives: We sought to evaluate the diagnostic and prognostic value of measurable parameters of internal auditory canal (IAC) magnetic resonance imaging (MRI) in patients with idiopathic sudden sensorineural hearing loss (ISSNHL).Subjects and Methods: We retrospectively reviewed the patients with ISSNHL who underwent IAC MRI from January 2008 to March 2019. Measurable parameters of IAC MRI, such as the diameter of the IAC, bony cochlear nerve canal, and cross-sectional area of the cochlear nerve, were measured by a single examiner. These parameters were then compared between the affected and healthy sides. Inner-ear abnormalities such as intralabyrinthine hemorrhage or labyrinthitis were also evaluated. The relationship between the surveyed parameters and the diagnosis of ISSNHL was assessed.Results: A total of 208 patients with ISSNHL were included. The measured parameters of IAC MRI were not different between the affected and healthy sides and were also not associated with the diagnosis of ISSNHL. However, inner-ear abnormalities of IAC MRI in ISSNHL displayed a significant association with worse hearing before and after treatment. An age that was older than 40 years also correlated with poorer outcomes. Further, inner-ear abnormalities were more frequently detected when IAC MRI was performed early after ISSNHL onset.Conclusions: Patients with ISSNHL and inner ear abnormalities such as intralabyrinthine hemorrhage or labyrinthitis identified via IAC MRI may experience poorer hearing outcomes. To detect such abnormal findings, it is recommended to perform IAC MRI early after the onset of ISSNHL.

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