Background: Colonic atresia is an uncommon entity. It may be associated with multiple anomalies.
Case Presentation: We present a case, which was initially suspected to be jejunal atresia, but was found to have colonic atresia as well intra-operatively. The associated jejunal atresia with apple-peel configuration was present as the content of inguinal hernia.
Conclusion: This case report highlights the rarity of the condition and the postoperative issues in the management of such patients.