Congenital Misalignment of Pulmonary Veins with Alveolar Capillary Dysplasia Causing Persistent Neonatal Pulmonary Hypertension: Report of Two Affected Siblings

2000 ◽  
Vol 3 (3) ◽  
pp. 271-276 ◽  
Author(s):  
Carmen Gutierrez ◽  
Angeles Rodriguez ◽  
Sylvia Palenzuela ◽  
Carolina Forteza ◽  
Jose L. Diaz Rossello

Misalignment of pulmonary vessels with alveolar capillary dysplasia is a rare cause of persistent pulmonary hypertension of the newborn. Most of the reported cases have been sporadic. We present two consecutive affected siblings with this disorder. This is the fifth reported family occurrence of this condition. In addition to the pulmonary abnormality, one of our cases had duodenal atresia.

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Joana Miranda ◽  
Gustavo Rocha ◽  
Henrique Soares ◽  
Ana Vilan ◽  
Otília Brandão ◽  
...  

Alveolar capillary dysplasia with misalignment of pulmonary veins (ACD/MPV) is a rare, fatal, developmental lung disorder, which usually presents as persistent pulmonary hypertension of the newborn (PPHN) unresponsive to treatment. The authors present their own experience with three cases admitted during the last 15 years.


2005 ◽  
Vol 13 (1) ◽  
pp. 82-84 ◽  
Author(s):  
Alan DL Sihoe ◽  
Alex TH Lee ◽  
Ka-Fai To ◽  
Kin-Hoi Thung ◽  
Tak-Wai Lee ◽  
...  

Alveolar capillary dysplasia with misalignment of pulmonary vessels is an uncommon congenital cause of persistent pulmonary hypertension of the newborn. It is universally fatal, and diagnosis is entirely dependent upon surgical lung biopsy. We present a case of alveolar capillary dysplasia with misalignment of pulmonary vessels occurring in a full-term neonate, emphasizing that early involvement of the thoracic surgeon for a histological diagnosis allows expensive and ineffective treatments to be avoided.


1997 ◽  
Vol 17 (6) ◽  
pp. 959-975 ◽  
Author(s):  
Sibylle Haraida ◽  
Hannelore Lochbuhler ◽  
A. Heger ◽  
A. Nerlich ◽  
J. Diebold ◽  
...  

1997 ◽  
Vol 17 (6) ◽  
pp. 959-975 ◽  
Author(s):  
Sibylle Haraida ◽  
Hannelore Lochbühler ◽  
A. Heger ◽  
A. Nerlich ◽  
J. Diebold ◽  
...  

1997 ◽  
Vol 17 (6) ◽  
pp. 959-976 ◽  
Author(s):  
Sibylle Haraida ◽  
Hannelore Lochbuhler ◽  
A. Heger ◽  
A. Nerlich ◽  
J. Diebold ◽  
...  

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