Progressive hemifacial atrophy (Romberg's disease): skeletal involvement and treatment

1993 ◽  
Vol 46 (1) ◽  
pp. 39-44 ◽  
Author(s):  
Mark H. Moore ◽  
Kee Sing Wong ◽  
Timothy W. Proudman ◽  
David J. David
Keyword(s):  
Hemifacial Atrophy ◽  
Skeletal Involvement ◽  
Progressive Hemifacial Atrophy ◽  
Romberg's Disease ◽  
Romberg’S Disease

Hemifacial atrophy (Romberg's disease)

BDJ ◽  
1987 ◽  
Vol 162 (5) ◽  
pp. 182-184 ◽  
Author(s):  
K H Ho
Keyword(s):  
Hemifacial Atrophy ◽  
Romberg's Disease ◽  
Romberg’S Disease

Progressive Hemifacial Atrophy Associated with Lyme Disease

1992 ◽  
Vol 90 (3) ◽  
pp. 479-483 ◽  
Author(s):  
Harvey S. Stern ◽  
L. Franklyn Elliott ◽  
Philip H. Beegle
Keyword(s):  
Lyme Disease ◽  
Hemifacial Atrophy ◽  
Progressive Hemifacial Atrophy

scholarly journals Progressive hemifacial atrophy: a review

2015 ◽  
Vol 10 (1) ◽  
Author(s):  
Stanislav N Tolkachjov ◽  
Nirav G Patel ◽  
Megha M Tollefson
Keyword(s):  
Hemifacial Atrophy ◽  
Progressive Hemifacial Atrophy

Craniofacial Syndromes Part II: Atypical Facial Clefts, Romberg Syndrome, Moebius Syndrome, Fibrous Dysplasia, and Neurofibromatosis

2020 ◽  
Author(s):  
Francesca Saldanha ◽  
Cory M. Resnick ◽  
Carolyn R. Rogers-Vizena
Keyword(s):  
Fibrous Dysplasia ◽  
Treatment Plan ◽  
Moebius Syndrome ◽  
Hemifacial Atrophy ◽  
Mccune Albright Syndrome ◽  
Facial Clefts ◽  
Progressive Hemifacial Atrophy ◽  
Parry Romberg Syndrome ◽  
Albright Syndrome ◽  
Craniofacial Syndromes

This final article of the two-part craniofacial series continues to provide the embryologic and developmental foundations necessary to understand congenital craniofacial pathology. Clinical characteristics and molecular genetics needed to make an accurate diagnosis and formulate a treatment plan will be detailed for atypical craniofacial clefts, Moebius Syndrome, Fibrous Dysplasia, Progressive Hemifacial Atrophy (Parry-Romberg syndrome) and Neurofibromatosis. Details of the operations applied in treatment of these disorders are discussed in separate Scientific American: Plastic Surgery (SAPS) articles as referenced. This review contains 3 tables, and 10 figures, and 42 references. Keywords: craniofacial, Tessier cleft, atypical facial cleft, Romberg syndrome, Parry-Romberg syndrome, Moebius syndrome, fibrous dysplasia, McCune Albright syndrome, neurofibromatosis

scholarly journals Parry Romberg Syndrome with contralateral iridocorneal endothelial syndrome: a unique case

2021 ◽  
Vol 8 (12) ◽  
pp. 1873
Author(s):  
Usha K. Raina ◽  
Shruti Bhattacharya ◽  
Prateeksha Sharma ◽  
Varun Saini
Keyword(s):  
Corneal Edema ◽  
Rare Disorder ◽  
Specular Microscopy ◽  
Unique Case ◽  
Hemifacial Atrophy ◽  
Normal Side ◽  
Ocular Manifestations ◽  
Iridocorneal Endothelial Syndrome ◽  
Progressive Hemifacial Atrophy ◽  
Parry Romberg Syndrome

Parry-Romberg syndrome (PRS) is a rare disorder which causes progressive hemifacial atrophy, with ocular manifestations like hypotony, enophthalmos and corneal edema on the ipsilateral atrophic side. This is a report of a unique case of PRS with contalateral manifestations like ectropion uvea, correctopia and endothelial deposits, along with polymegathism and pleomorphism seen on specular microscopy suggestive of Iridocorneal Endothelial (ICE) Syndrome. ICE syndrome and PRS have not been reported together in any literature so far. This case highlights the importance of a thorough glaucoma workup and corneal examination on the atrophic facial side as well as on the apparently normal side in all cases of PRS.

Rare health conditions 31: infantile neuroaxonal dystrophy, progressive hemifacial atrophy, acquired prosopagnosia; and offering emotional and psychological support

2020 ◽  
Vol 14 (1) ◽  
pp. 15-19
Author(s):  
Chris Barber
Keyword(s):  
Psychological Needs ◽  
Psychological Support ◽  
Neuroaxonal Dystrophy ◽  
Health Conditions ◽  
Infantile Neuroaxonal Dystrophy ◽  
Hemifacial Atrophy ◽  
Progressive Hemifacial Atrophy

The purpose of this series is to highlight a range of rare health conditions. Rare health conditions are those that affect no more and usually fewer than 1 person in every 2000 and many HCAs and nurses will encounter some of these conditions, given the high number of them. This 31st article will explore three of these conditions, as well as offering a brief discussion on meeting the emotional and psychological needs of the person.

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