Fallot's tetralogy with absent pulmonary valve and anomalous origin of the left pulmonary artery

1993 ◽  
Vol 42 (2) ◽  
pp. 175-177 ◽  
Author(s):  
Narayanswami Sreeram ◽  
Audrey Smith ◽  
Ian Peart
Keyword(s):  
Pulmonary Artery ◽  
Pulmonary Valve ◽  
Left Pulmonary Artery ◽  
Anomalous Origin ◽  
Absent Pulmonary Valve ◽  
Fallot's Tetralogy ◽  
Fallot’S Tetralogy

scholarly journals Anomalous origin of the left pulmonary artery from the ascending aorta: successful surgical correction in an infant with fallot's tetralogy

2002 ◽  
Vol 79 (5) ◽  
pp. 541-543 ◽  
Author(s):  
Fernando Amaral ◽  
Mônica A. C. Teixeira ◽  
João A. Granzotti ◽  
Paulo Henrique Manso ◽  
Walter V. A. Vicente
Keyword(s):  
Pulmonary Artery ◽  
Left Pulmonary Artery ◽  
Ascending Aorta ◽  
Surgical Correction ◽  
Anomalous Origin ◽  
Fallot's Tetralogy ◽  
Fallot’S Tetralogy

Unusual association of isolation of right pulmonary artery in absent pulmonary valve syndrome

2021 ◽  
pp. 021849232110063
Author(s):  
Kothandam Sivakumar ◽  
Asish Ranjan Mohakud ◽  
Ravi Agarwal
Keyword(s):  
Pulmonary Artery ◽  
Pulmonary Valve ◽  
Pulmonary Regurgitation ◽  
Left Pulmonary Artery ◽  
Absent Pulmonary Valve ◽  
Etiologic Role ◽  
Right Pulmonary Artery ◽  
Proximal Extension ◽  
Common Association ◽  
Absent Pulmonary Valve Syndrome

Absence of arterial duct, a sixth aortic arch derivative, plays an important etiologic role in Tetralogy of Fallot with absent pulmonary valve syndrome. When fetal ductus is absent, the large right ventricular stroke volume dilates the pulmonary trunk leading to pulmonary regurgitation. A proximal extension of the embryonic insult to the entire left sixth arch causes absence of the left pulmonary artery, a common association of absent pulmonary valve syndrome. On the contrary, absence of right pulmonary artery is not reported in absent pulmonary valve syndrome. A rare combination of tetralogy, absent pulmonary valve syndrome and isolation of a hypoplastic right pulmonary artery offered challenges to diagnosis and management.

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