Tc-99m MDP Uptake in a Giant Pulmonary Chondroma

1. Pulmonary chondroma 2. Gastrointestinal stromal tumor (GIST), formerly, gastric epithelioid leiomyosarcoma 3. Functioning extra-adrenal paraganglioma • Triad eventually present in more than half of patients • 〉90% of patients are female • Mean age: 17 years • Mechanism: unknown (disease absent in 1 identical twin)...

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Pulmonary chondroma, extra-adrenal paraganglioma, and gastric leiomyosarcoma

Journal of Thoracic and Cardiovascular Surgery ◽

10.1016/s0022-5223(19)39007-5 ◽

1982 ◽

Vol 84 (3) ◽

pp. 377-381 ◽

Cited By ~ 24

Author(s):

Amrit Dajee ◽

Himmet Dajee ◽

Steven Hinrichs ◽

Glen Lillington

Keyword(s):

Pulmonary Chondroma ◽

Gastric Leiomyosarcoma ◽

Extra Adrenal Paraganglioma

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Gastric epitheloid leiomyomas, pulmonary chondroma, non-functioning metastasizing extra-adrenal paraganglioma and myxoma: A variant of carney's triad

Klinische Wochenschrift ◽

10.1007/bf01731476 ◽

1985 ◽

Vol 63 (6) ◽

pp. 282-284 ◽

Cited By ~ 20

Author(s):

H. Rüfenacht ◽

M. J. Mihatsch ◽

K. Jundt ◽

A. Gächter ◽

K. Tanner ◽

...

Keyword(s):

Carney’S Triad ◽

Pulmonary Chondroma ◽

Extra Adrenal Paraganglioma

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Pulmonary chondroma in a dog

Veterinary Record ◽

10.1136/vr.155.2.59 ◽

2004 ◽

Vol 155 (2) ◽

pp. 59-60

Author(s):

J. C. Patterson-Kane ◽

A. R. Notenboom

Keyword(s):

Pulmonary Chondroma

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Extra-Adrenal Paraganglioma and Pulmonary Chondroma: A Case Report and Review of the Literature

The Journal of Urology ◽

10.1016/s0022-5347(17)43607-x ◽

1987 ◽

Vol 138 (5) ◽

pp. 1345-1345

Author(s):

S. Keyhani-Rofagha ◽

T.M. O’Dorisio ◽

J.G. Lucas ◽

M.B. Fontana ◽

S.E. Tuttle

Keyword(s):

Case Report ◽

Review Of The Literature ◽

Pulmonary Chondroma ◽

Extra Adrenal Paraganglioma

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Pulmonary Metastatic Leiomyosarcoma Coexisting With Pulmonary Chondroma in Carney's Triad

Archives of Internal Medicine ◽

10.1001/archinte.1983.00350070182029 ◽

1983 ◽

Vol 143 (7) ◽

pp. 1462 ◽

Cited By ~ 13

Author(s):

A. Philippe Chahinian

Keyword(s):

Carney’S Triad ◽

Pulmonary Chondroma

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Separate Occurrence of Extra-adrenal Paraganglioma and Gastrointestinal Stromal Tumor in Monozygotic Twins: Probable Familial Carney Syndrome

Pediatric and Developmental Pathology ◽

10.1007/s10024-004-8090-y ◽

2004 ◽

Vol 7 (4) ◽

pp. 380-384 ◽

Cited By ~ 16

Author(s):

Liliane Boccon-Gibod ◽

Françoise Boman ◽

Sabah Boudjemaa ◽

Monique Fabre ◽

Guy Leverger ◽

...

Keyword(s):

Gastrointestinal Stromal Tumor ◽

Monozygotic Twins ◽

Monozygotic Twin ◽

Stromal Tumor ◽

Gastric Gist ◽

Carney Triad ◽

Pulmonary Chondroma ◽

Carney Syndrome ◽

Extra Adrenal Paraganglioma

The nonfamilial Carney triad includes paraganglioma, gastrointestinal stromal tumor (GIST), and pulmonary chondroma. Some paraganglioma-GIST diads are familial and inherited in an apparent autosomal dominant manner. The familial paraganglioma-GIST syndrome differs from the Carney triad by the absence of female predilection and predominance of paragangliomas. We report the cases of a 12-year-old boy with a paraganglioma of the organ of Zuckerkandl, and his 13-year-old monozygotic twin with a gastric GIST. These two patients, to our knowledge, are the first to be reported as likely having the familial paraganglioma-GIST syndrome following its description by Carney and Stratakis (Am J Med Genet 2002;108:132–139) in 12 patients from five families. A lifetime follow-up and a periodic search for both tumors are indicated in these patients and their families.

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