scholarly journals Pulmonary Artery Aneurysm Repair with Alpha-1 Anti-trypsin Deficiency

Author(s):  
Brett Starr ◽  
Caitlin Takahashi-Pipkin ◽  
Michael Bates ◽  
Shahab Akhter

A 62-year-old woman with pulmonary hypertension due to alpha-1 antitrypsin deficiency and known congenital pulmonic valve stenosis presented with palpitations, chest pressure and bradycardia and was found to have a 6 cm pulmonary artery aneurysm on work-up. The patient underwent surgical pulmonary artery aneurysm repair and recovered from operation without complications.

2017 ◽  
Vol 5 (21) ◽  
pp. 32
Author(s):  
Audra Schwalk ◽  
Gilbert Berdine

Pulmonary artery (PA) aneurysms are uncommon and often diagnosed post-mortem. Theyare characterized by a PA/aorta diameter ratio greater than 2 on transthoracic echocardiographyor a pulmonary artery diameter greater than 4 or 5 cm on computed tomography. The mostcommon conditions associated with pulmonary artery aneurysm are congenital heart defectswith left-to-right shunts and pulmonic valve abnormalities. There are also numerous causesof acquired pulmonary artery aneurysms, including infection, vasculitis, pulmonary arterialhypertension, trauma, neoplasm and pulmonary embolism. Symptoms of PA aneurysm areusually non-specific, and physical examination findings are variable depending on the underlyingcause. Work-up includes various imaging modalities, transthoracic echocardiography, and rightheart catheterization. The gold standard treatment is surgery, but in select patients, conservativemanagement with close monitoring can be pursued.


2020 ◽  
Vol 159 (6) ◽  
pp. 2543-2550 ◽  
Author(s):  
Stefan Schwarz ◽  
Alberto Benazzo ◽  
Helmut Prosch ◽  
Peter Jaksch ◽  
Walter Klepetko ◽  
...  

1997 ◽  
Vol 5 (2) ◽  
pp. 180
Author(s):  
Jun Sik Nam ◽  
Hong Geun Jo ◽  
Ik Mo Jung ◽  
Shi Hun Park ◽  
Sung Hun Park ◽  
...  

Circulation ◽  
2016 ◽  
Vol 133 (12) ◽  
pp. 1218-1221 ◽  
Author(s):  
Peter Chiu ◽  
Mallory Irons ◽  
Matt van de Rijn ◽  
David. H. Liang ◽  
D. Craig Miller

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