Sinus venosus atrial septal defect with severe mitral stenosis: a rare variant of Lutembacher’s syndrome

Lutembacher’s syndrome is a rare cardiovascular defect comprising of mitral stenosis and atrial septal defect. A combination of acquired mitral stenosis and congenital atrial septal defect is the most well-recognized pattern. As atrial septal defect acts as a pressure relieving gateway, signs and symptoms of mitral stenosis may be attenuated and/or delayed in such patients. We have presented a case with Lutembacher’s syndrome that was incidentally diagnosed as having such defect during outpatient check-up for upper respiratory infection.

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Mitral Stenosis, Sinus Venosus Atrial Septal Defect, and Partial Anomalous Pulmonary Venous Return.

Echocardiography ◽

10.1111/j.1540-8175.1996.tb00946.x ◽

1996 ◽

Vol 13 (6) ◽

pp. 635-637 ◽

Cited By ~ 3

Author(s):

JAMSHID SHIRANI ◽

DANNY WOO ◽

WILLIAM GOTSIS ◽

JAY S. MEISNER ◽

JOEL A. STROM

Keyword(s):

Atrial Septal Defect ◽

Mitral Stenosis ◽

Septal Defect ◽

Venous Return ◽

Sinus Venosus ◽

Anomalous Pulmonary Venous Return

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Sinus venosus atrial septal defect with severe mitral stenosis: A rare presentation

Medical Journal of Dr D Y Patil University ◽

10.4103/0975-2870.157101 ◽

2015 ◽

Vol 8 (3) ◽

pp. 392

Author(s):

Shweta Shende ◽

Avinash Inamdar ◽

Sanjivani Inamdar

Keyword(s):

Atrial Septal Defect ◽

Mitral Stenosis ◽

Septal Defect ◽

Sinus Venosus ◽

Rare Presentation

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Rheumatic mitral stenosis associated with sinus venosus atrial septal defect and partial anomalous pulmonary venous return

General Thoracic and Cardiovascular Surgery ◽

10.1007/s11748-013-0293-6 ◽

2013 ◽

Vol 63 (6) ◽

pp. 361-364

Author(s):

Vithalkumar Malleshi Betigeri ◽

Anupama Vithalkumar Betigeri ◽

Balkrishnan Karthikeyan ◽

Kasturi Satya Venkata Kumar SubbaRao

Keyword(s):

Atrial Septal Defect ◽

Mitral Stenosis ◽

Septal Defect ◽

Venous Return ◽

Sinus Venosus ◽

Rheumatic Mitral Stenosis ◽

Anomalous Pulmonary Venous Return

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Single-Patch Fold-Back Technique for Augmentation of the Superior Vena Cava in Sinus Venosus Atrial Septal Defect Associated with Partial Anomalous Pulmonary Venous Return

The Heart Surgery Forum ◽

10.1532/hsf98.2014433 ◽

2015 ◽

Vol 17 (6) ◽

pp. 282

Author(s):

Suguru Ohira ◽

Kiyoshi Doi ◽

Takeshi Nakamura ◽

Hitoshi Yaku

Keyword(s):

Atrial Septal Defect ◽

Superior Vena Cava ◽

Septal Defect ◽

Venous Return ◽

Superior Vena ◽

Pulmonary Veins ◽

Vena Cava ◽

Sinus Venosus ◽

Right Atrial ◽

Anomalous Pulmonary Venous Return

Sinus venosus atrial septal defect (ASD) is usually associated with partial anomalous pulmonary venous return (PAPVR) of the right pulmonary veins to the superior vena cava (SVC), or to the SVC-right atrial junction. Standard procedure for repair of this defect is a patch roofing of the sinus venosus ASD and rerouting of pulmonary veins. However, the presence of SVC stenosis is a complication of this technique, and SVC augmentation is necessary in some cases. We present a simple technique for concomitant closure of sinus venosus ASD associated with PAPVR and augmentation of the SVC with a single autologous pericardial patch.

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