Bioprosthetic Pulmonary Valve Dysfunction in Congenital Heart Disease

2022 ◽  
Author(s):  
Parth M. Patel ◽  
David Zapata ◽  
William Qu ◽  
Mia Callahan ◽  
Nikita Rao ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Pulmonary Valve ◽  
Valve Dysfunction

scholarly journals Right ventricular restoration during pulmonary valve implantation in adults with congenital heart disease☆

2006 ◽  
Vol 29 ◽  
pp. S279-S285 ◽  
Author(s):  
Alessandro Frigiola ◽  
Alessandro Giamberti ◽  
Massimo Chessa ◽  
Marisa Di Donato ◽  
Raul Abella ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Right Ventricular ◽  
Congenital Heart ◽  
Pulmonary Valve ◽  
Valve Implantation ◽  
Ventricular Restoration ◽  
Pulmonary Valve Implantation

Lecompte Procedure for Relief of Severe Airway Compression in Children With Congenital Heart Disease

2019 ◽  
Vol 10 (5) ◽  
pp. 558-564
Author(s):  
Christina L. Greene ◽  
Richard D. Mainwaring ◽  
Douglas Sidell ◽  
Michal Palmon ◽  
Frank L. Hanley
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Surgical Procedure ◽  
Congenital Heart ◽  
Pulmonary Valve ◽  
Heart Defects ◽  
Pulmonary Atresia ◽  
Absent Pulmonary Valve ◽  
Airway Compression ◽  
Absent Pulmonary Valve Syndrome

Purpose: Children with congenital heart disease may present with severe airway compression prior to any surgical procedure or may develop airway compression following their surgical procedure. This combination of congenital heart defect and airway compression poses a significant management challenge. The purpose of this study was to review our experience with the Lecompte procedure for relief of severe airway compression. Methods: This was a retrospective review of ten patients who underwent a Lecompte procedure for relief of severe airway compression over the past nine years (2010-2018). Three patients with absent pulmonary valve syndrome presented with severe symptoms prior to any surgical procedure. Seven patients presented with symptoms of airway compression following repair of their congenital heart defects (one with absent pulmonary valve syndrome, three patients had repair of pulmonary atresia with ventricular septal defect, and three patients had undergone aortic arch surgery). The median age at presentation was two years (range: one day to seven years). Results: The ten patients underwent a Lecompte procedure without any significant complications or operative mortality. The median interval between the surgical procedure and extubation was 9.5 days. No patients have required any further interventions for relief of airway obstruction. Conclusions: The Lecompte procedure is a surgical option for young children who present with severe airway compression. The patients in this series responded well to the Lecompte procedure as evidenced by clinical relief of airway compression.

scholarly journals Outcome and performance of bioprosthetic pulmonary valve replacement in patients with congenital heart disease

2016 ◽  
Vol 152 (5) ◽  
pp. 1333-1342.e3 ◽  
Author(s):  
Rio Nomoto ◽  
Lynn A. Sleeper ◽  
Michele J. Borisuk ◽  
Lisa Bergerson ◽  
Frank A. Pigula ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Valve Replacement ◽  
Congenital Heart ◽  
Pulmonary Valve ◽  
Pulmonary Valve Replacement ◽  
And Performance

Variable expression of Alagille syndrome in a family with a new JAG1 gene mutation

2015 ◽  
Vol 26 (1) ◽  
pp. 164-167 ◽  
Author(s):  
Victoria C. Ziesenitz ◽  
Tsvetomir Loukanov ◽  
Christiane Gläser ◽  
Matthias Gorenflo
Keyword(s):  
Liver Transplantation ◽  
Congenital Heart Disease ◽  
Heart Disease ◽  
Tetralogy Of Fallot ◽  
Congenital Heart ◽  
Pulmonary Valve ◽  
Alagille Syndrome ◽  
Cardiac Repair ◽  
Absent Pulmonary Valve ◽  
Variable Expression

AbstractWe report the case of a patient with tetralogy of Fallot with absent pulmonary valve and familial Alagille syndrome who successfully underwent cardiac repair. The patient’s sister had liver and congenital heart disease. The father had undergone liver transplantation but showed no significant cardiac abnormalities. A yet-unknown mutation of the JAG1 gene was discovered in this family with variable expression of Alagille syndrome.

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