Fallot-type absent pulmonary valve syndrome with patent ductus arteriosus and disconnected pulmonary arteries

2021 ◽  
Vol 31 (2) ◽  
pp. 289-290
Author(s):  
Gaurav Kumar ◽  
Sanjiban Ghosh ◽  
Anuradha Sridhar
Keyword(s):  
Patent Ductus Arteriosus ◽  
Pulmonary Valve ◽  
Ductus Arteriosus ◽  
Pulmonary Arteries ◽  
Absent Pulmonary Valve ◽  
Absent Pulmonary Valve Syndrome ◽  
Patent Ductus

Tetralogy of Fallot With Absent Pulmonary Valve and Nonconfluent Pulmonary Arteries: A Management Conundrum

2018 ◽  
Vol 11 (4) ◽  
pp. NP168-NP171
Author(s):  
Sethuraman Swaminathan ◽  
Arpit Agarwal ◽  
Juan C. Infante ◽  
Eliot Rosenkranz
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Pulmonary Valve ◽  
Ductus Arteriosus ◽  
Pulmonary Arteries ◽  
Left Pulmonary Artery ◽  
Absent Pulmonary Valve ◽  
Rare Form ◽  
Respiratory Management ◽  
Absent Pulmonary Valve Syndrome

Tetralogy of Fallot with absent pulmonary valve syndrome is a rare form of congenital heart disease. Among the different variations with this rare anomaly is nonconfluent pulmonary artery branches with anomalous origin of the left pulmonary artery from the ductus arteriosus. The authors present one such case which was diagnosed prenatally to have tetralogy of Fallot with absent pulmonary valve and identified postnatally to have nonconfluent pulmonary artery branches in addition. We discuss the conundrum of respiratory management in this patient pre- and postoperatively due to a unique ventilation perfusion mismatch problem, which varies between the two lungs.

Sign in / Sign up

Export Citation Format

Share Document