Unusual right pulmonary artery–to-left atrial communication associated with scimitar syndrome

2021 ◽  
pp. 1-3
Author(s):  
Asish R. Mohakud ◽  
Sangamesh Bawage ◽  
Kothandam Sivakumar
Keyword(s):  
Pulmonary Artery ◽  
Blood Supply ◽  
Left Atrial ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Rare Association ◽  
Different Types ◽  
Right Pulmonary Artery ◽  
The Right

Abstract Right pulmonary artery to left atrial fistula is classified based on the right pulmonary artery branching, individual right pulmonary venous drainage, and presence of an aneurysmal segment. A rare association with scimitar syndrome and right lung devoid of blood supply from right pulmonary artery is described in this report. The anatomical and management differences between the different types are highlighted.

Systemic arterial supply of the right lung with venous drainage to the pulmonary arterial circuit

2011 ◽  
Vol 21 (6) ◽  
pp. 710-712 ◽  
Author(s):  
Peter Fritsch ◽  
Freyja-Maria Smolle-Juettner ◽  
Andreas Gamillscheg
Keyword(s):  
Pulmonary Artery ◽  
Venous Drainage ◽  
Left Pulmonary Artery ◽  
Scimitar Syndrome ◽  
Arterial Supply ◽  
Respiratory Problems ◽  
Right Pulmonary Artery ◽  
Pulmonary Arterial ◽  
The Right ◽  
Systemic Arterial Supply

AbstractIn a girl suffering from “Scimitar syndrome”, a rerouting of the scimitar vein was performed at the age of 6 years, but no embolisation of the aberrant systemic vessel was done. She presented with recurring respiratory problems 13 years later. An angiography revealed an invert flow from the aberrant systemic vessel via the right pulmonary artery into the left pulmonary artery. After pneumonectomy, she recovered well.

Scimitar syndrome associated with absence of the right pulmonary artery and a persistent primitive hepatic venous plexus

2005 ◽  
Vol 15 (2) ◽  
pp. 216-218 ◽  
Author(s):  
Gabriella Agnoletti ◽  
Damien Bonnet ◽  
Jacques De Blic
Keyword(s):  
Pulmonary Artery ◽  
Scimitar Syndrome ◽  
Venous Plexus ◽  
Caval Vein ◽  
Inferior Caval Vein ◽  
Right Pulmonary Artery ◽  
Unusual Variant ◽  
The Right

An 18-month-old boy, referred because of an infection of the airways, was found to have a right-sided heart, a hypoplastic right lung, absence of the right pulmonary artery, and persistence of the hepatic venous plexus. The benign association of this unusual variant of the scimitar syndrome and persistence of the hepatic venous plexus needs to be recognised in order to avoid extensive investigations and surgery involving the inferior caval vein.

Hypoplastic left heart syndrome with anomalous origin of right pulmonary artery

2020 ◽  
pp. 021849232095506
Author(s):  
Ashish Mishra ◽  
Bhavik Champaneri ◽  
Yashpal Rana ◽  
Gaurav Singh ◽  
Senthilraj Thangasami ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Hypoplastic Left Heart Syndrome ◽  
Venous Drainage ◽  
Anomalous Origin ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Right Pulmonary Artery ◽  
Complex Forms ◽  
The Right ◽  
Left Heart Syndrome

Classic hypoplastic left heart syndrome is a rare but fatal congenital heart disease associated with variable underdevelopment of the left side of the heart. Complex forms of hypoplastic left heart syndrome have been reported to coexist with anomalous pulmonary venous drainage, transposition of the great arteries, or pulmonary valve dysplasia. We report a case of hypoplastic left heart syndrome with anomalous origin of the right pulmonary artery from the ascending aorta a rare association not reported in the literature. Preoperative comprehensive echocardiography is essential for diagnosis and accurate recognition of such rare anatomic variations.

Partial anomalous pulmonary venous drainage repair concomitant with bilateral semilunar valve replacements and pulmonary artery reconstruction for an adult female 20 years after initial truncus arteriosus repair

2018 ◽  
Vol 28 (3) ◽  
pp. 514-515
Author(s):  
Toshiyuki Iwaya ◽  
Koichi Sughimoto ◽  
Kagami Miyaji
Keyword(s):  
Pulmonary Artery ◽  
Pulmonary Valve ◽  
Right Ventricular Outflow Tract ◽  
Venous Drainage ◽  
Ventricular Outflow Tract ◽  
Anomalous Pulmonary Venous Drainage ◽  
Right Pulmonary Artery ◽  
Pulmonary Artery Reconstruction ◽  
The Right ◽  
Artery Reconstruction

AbstractWe describe the case of a 21-year-old patient who underwent repairs for multiple lesions including aortic and pulmonary valve replacements, right ventricular outflow tract reconstruction, revision of the right pulmonary artery route, and a repair of partial anomalous pulmonary venous drainage, which was diagnosed during this fourth sternotomy. For these patients with adult CHD, it is most important to address all underlying factors as much as possible at the redo surgery.

The Right Pulmonary Artery—Left Atrial Axis Line

Radiology ◽  
1976 ◽  
Vol 118 (2) ◽  
pp. 265-274 ◽  
Author(s):  
Jack L. Westcott ◽  
Dennis Ferguson
Keyword(s):  
Pulmonary Artery ◽  
Left Atrial ◽  
Right Pulmonary Artery ◽  
The Right

Scimitar syndrome with absence of the right pulmonary artery: A case with volume-induced, reversible, left-sided pulmonary hypertension

1992 ◽  
Vol 13 (2) ◽  
pp. 119-121 ◽  
Author(s):  
Albrecht Beitzke ◽  
Gerfried Zobel ◽  
Bruno Rigler ◽  
J�rg Ingolf Stein ◽  
Christa Suppan
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Artery ◽  
Scimitar Syndrome ◽  
Right Pulmonary Artery ◽  
The Right

Variants of the scimitar syndrome

2015 ◽  
Vol 26 (5) ◽  
pp. 941-947 ◽  
Author(s):  
Ilaria Bo ◽  
Julene S. Carvalho ◽  
Emma Cheasty ◽  
Michael Rubens ◽  
Michael L. Rigby
Keyword(s):  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Caval Vein ◽  
Superior Caval Vein ◽  
Inferior Caval Vein ◽  
Small Series ◽  
Right Pulmonary Artery ◽  
Aortopulmonary Collateral ◽  
The Right ◽  
Lost To Follow Up

AbstractIntroductionThe scimitar syndrome comprises hypoplastic right pulmonary artery and lung, anomalous right pulmonary venous drainage to the inferior caval vein, aortopulmonary collateral(s) to the right lung, and bronchial anomalies.AimThe aim of this study was to describe the morphological and clinical spectrum of variants from the classical scimitar syndrome in a single institution over 22 years.ResultsIn total, 10 patients were recognised. The most consistent feature was an aortopulmonary collateral to the affected lung (90%), but there was considerable variation in the site and course of pulmonary venous drainage. This was normal in 3 (one with meandering course), anomalous right to superior caval vein in 1, to the superior caval vein and inferior caval vein in 2, and to the superior caval vein and the left atrium in 1; one patient had a right pulmonary (scimitar) vein occluded at the insertion into the inferior caval vein but connected to the right upper pulmonary vein via a fistula. There were two left-sided variants, one with anomalous left drainage to the coronary sinus and a second to the innominate vein.Among all, three patients had an antenatal diagnosis and seven presented between 11 and 312 months of age; 90% of the patients were symptomatic at first assessment.All the patients underwent cardiac catheterisation; collateral embolisation was performed in 50% of the patients. Surgical repair of the anomalous vein was carried out in two patients, one patient had a right pneumonectomy, and one patient was lost to follow-up. There was no mortality reported in the remainder of patients during the study period.ConclusionThe heterogeneity of this small series confirms the consistent occurrence of an anomalous arterial supply to the affected lung but considerable variation in pulmonary venous drainage.

scholarly journals Congenital unilateral absence of the right pulmonary artery and complex of fallot. A rare association.

1986 ◽  
Vol 27 (6) ◽  
pp. 885-892 ◽  
Author(s):  
Jorge R. BÜCHLER ◽  
Adib D. JATENE ◽  
Januario de ANDRADE
Keyword(s):  
Pulmonary Artery ◽  
Rare Association ◽  
Right Pulmonary Artery ◽  
The Right
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