Undiagnosed High Tracheal Bifurcation and Laryngomalacia in a Case of Tetralogy of Fallot With Absent Left Pulmonary Artery for Emergency Surgery

2007 ◽  
Vol 21 (6) ◽  
pp. 876-879
Author(s):  
Thomas Koshy ◽  
Prabhat Kumar Sinha ◽  
Arun Vijayakumar ◽  
Arun Kumar Gupta
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Emergency Surgery ◽  
Left Pulmonary Artery ◽  
Absent Left Pulmonary Artery ◽  
Tracheal Bifurcation

scholarly journals “Absent” left pulmonary artery with tetralogy of Fallot

1968 ◽  
Vol 55 (3) ◽  
pp. 333-336 ◽  
Author(s):  
Eugene Wallsh ◽  
Edmund H. Reppert ◽  
Eugenie F. Doyle ◽  
Frank C. Spencer
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Left Pulmonary Artery ◽  
Absent Left Pulmonary Artery

scholarly journals Tetralogy of Fallot with Absent Pulmonary Valve Syndrome with Absent Left Pulmonary Artery - A Rare Presentation

2020 ◽  
Vol 35 (1) ◽  
pp. 74-77
Author(s):  
Abul Kalam Shamsuddin ◽  
Prodip Kumar Biswas ◽  
Muhammad Ishtiaque Sayeed Al Manzoo ◽  
Md Abul Kalam Azad ◽  
Md Nurul Akhtar Hasan ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Pulmonary Valve ◽  
Postoperative Mortality ◽  
Left Pulmonary Artery ◽  
Absent Pulmonary Valve ◽  
Congenital Cardiac Anomaly ◽  
Ct Angiogram ◽  
Absent Left Pulmonary Artery ◽  
Absent Pulmonary Valve Syndrome

Absent left pulmonary artery with Tetralogy of Fallot (TOF) with absent pulmonary valve syndrome (APVS), is a rare congenital cardiac anomaly. Here we present such a case of A 2 year 11 month old girl with cyanosis, exertional dyspnoea. Her diagnosis is confirmed by echocardiography and CT angiogram. There are very few cases have been reported till date with high postoperative mortality. Although per operative decision making was challenging regarding pulmonary valve and size of the RPA, we performed ICR with RPA reductionplasty and creation of monocuspid pulmonary valve with success. As it is a rare association and we have overcome the hindrance we came across per operatively, we are reporting this case. Bangladesh Heart Journal 2020; 35(1) : 74-77

Intrapulmonary artery septation for unilateral absence of the pulmonary artery

2021 ◽  
pp. 021849232110139
Author(s):  
Junichi Koizumi ◽  
Tomoyuki Iwase ◽  
Shigeto Tsuji ◽  
Takuya Goto ◽  
Kotaro Oyama ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Left Pulmonary Artery ◽  
Post Surgery ◽  
Pulmonary Artery Reconstruction ◽  
Artery Reconstruction ◽  
Absent Pulmonary Artery ◽  
Absent Left Pulmonary Artery ◽  
Tetralogy Of Fallot Repair ◽  
Blalock Taussig Shunt

We describe a seven-month-old boy with tetralogy of Fallot and an absent left pulmonary artery. Due to the diminutive size of the left pulmonary artery, we performed a native tissue left pulmonary artery reconstruction and intrapulmonary artery septation procedure with a left modified Blalock-Taussig shunt. After confirming left pulmonary artery growth, the patient underwent tetralogy of Fallot repair, removal of septation patch, and division of the Blalock-Taussig shunt. Nine months post-surgery, we confirmed his balanced lung perfusion (R/L ratio 6:4). The intrapulmonary artery septation procedure would be suitable for both the resuscitation and reconstruction of the hypoplastic absent pulmonary artery.

Abstract 12430: Vicious Circle Between Progressive Right Ventricular Dilatation and Pulmonary Regurgitation in Patients After Tetralogy of Fallot Repair? Right Heart Enlargement Promotes Flow Reversal in the Left Pulmonary Artery

Circulation ◽  
2015 ◽  
Vol 132 (suppl_3) ◽  
Author(s):  
Atsuko Kato ◽  
Christian Drolet ◽  
Shi-Joon Yoo ◽  
Andrew Redington ◽  
Lars Grosse-Wortmann
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Left Lung ◽  
Pulmonary Regurgitation ◽  
Left Pulmonary Artery ◽  
Flow Reversal ◽  
Left Hemithorax ◽  
Forward Flow ◽  
Lung Area ◽  
The Right

Introduction: The left pulmonary artery (LPA) contributes more than the right (RPA) to total pulmonary regurgitation (PR) in patients after tetralogy of Fallot (TOF) repair, but the mechanism of this difference is not well known. We hypothesized that unilaterally increased pulmonary vascular resistance (PVR), resulting from lung compression by the enlarged and levorotated heart leads to greater PR in the LPA. This study aimed to analyze the interplay between heart and lung size, mediastinal geometry, and differential PR. Methods: This is a single-center retrospective analysis of 50 magnetic resonance studies in patients after TOF repair. Patients with more than mild discrete branch pulmonary artery stenosis were excluded. Blood flow was measured by phase-contrast velocity encoding within the branch pulmonary arteries. On the axial image with the largest total cardiac surface area, cardiac angle (α) between the thoracic anterior-posterior line and the interventricular septum, right and left lung areas as well as right and left hemithorax areas were measured (Figure). Results: There was no difference in LPA and RPA diameters. The LPA showed significantly less total forward flow (p=0.04), smaller net forward flow (p=<0.001), and greater RF (p=0.001) than the RPA. Left lung area was smaller than the right (p<0.001). RVEDVi correlated with LPA RF (R=0.48, p<0.001), but not with RPA RF. Larger RVEDVi correlated with a larger α angle (R=0.46, p<0.001), i.e. a more leftward cardiac axis and with smaller left lung area (R=-0.58, p<0.001). LPA RF, but not RPA RF, correlated inversely with left lung area indexed to the left hemithorax area (R=-0.34, p=0.02). Conclusions: An enlarged and levorotated heart - as a result of PR - is associated with smaller left lung size, and augments diastolic flow reversal in the LPA, presumably via increased left PVR. By imposing a further volume load on the RV, LPA regurgitation may thus close a positive feed-back loop of PR and RV dilatation.

scholarly journals Tetralogy of Fallot with atresia of the left pulmonary artery

1975 ◽  
Vol 69 (3) ◽  
pp. 458-466 ◽  
Author(s):  
Martin Goldsmith ◽  
Matthew A. Farina ◽  
Reda M. Shaher
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Left Pulmonary Artery

Anomalous origin of a pulmonary artery in a teenager with tetralogy of Fallot with associated double aortic arch and coronary arteriovenous fistula

2019 ◽  
Vol 29 (5) ◽  
pp. 727-729
Author(s):  
Vishal Agrawal ◽  
Parth Solanki ◽  
Ritesh Shah ◽  
Divyakant Parmar ◽  
Amit Mishra
Keyword(s):  
Pulmonary Artery ◽  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Vascular Ring ◽  
Right Ventricular Outflow Tract ◽  
Left Pulmonary Artery ◽  
Ventricular Outflow Tract ◽  
Double Aortic Arch ◽  
Anomalous Origin ◽  
Tract Fistula

AbstractWe report the case of a 14-year-old female who had tetralogy of Fallot along with anomalous origin of the left pulmonary artery from the ascending aorta with co-dominant double aortic arch forming a complete vascular ring compressing the oesophagus along with a left main coronary artery to right ventricular outflow tract fistula. She underwent surgical correction without conduit placement.

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