Prenatal diagnosis of multiple ventriculocoronary connections in pulmonary atresia with an intact ventricular septum: A case report

2015 ◽  
Vol 41 (8) ◽  
pp. 1278-1281 ◽  
Author(s):  
Hyun-Hwa Cha ◽  
Youn Sil Choo ◽  
Won Joon Seong

2005 ◽  
Vol 21 (5) ◽  
pp. 236-240
Author(s):  
Meng-Hsun Lee ◽  
Jiunn-Ren Wu ◽  
Zeng-Kong Dai ◽  
Jong-Hau Hsu ◽  
Chau-Chi Chou ◽  
...  


2006 ◽  
Vol 25 (8) ◽  
pp. 1069-1073 ◽  
Author(s):  
Jeng-Hsiu Hung ◽  
Jen-Her Lu ◽  
Jamie Hung ◽  
Jen-Chong Wong


1998 ◽  
Vol 14 (2) ◽  
pp. 67-70
Author(s):  
Carolyn T. Coffin ◽  
Julia A. Drose ◽  
Elizabeth M. Shaffer


Author(s):  
M.V. Medvedev , M.V. Kubrina , O.L. Galkina et all

A retrospective analysis of 21 cases of prenatal diagnosed of pulmonary atresia with intact ventricular septum (PA-IVS) is presented. In the study of the four chambers view of the fetal heart the right ventricle was hypoplastic in 16 (76.1 %), normal in 5 (23.8 %) cases. Tricuspid atresia identified in 8 (38 %) cases. The dysplasia of the tricuspid valve identified in 5 (23.8 %) cases. In 2 (8.7 %) cases PA-IVS were in combination with atrioventricular defects. The changes of the tricuspid valve were not identified in 6 (28.5 %) cases. In 100 % cases reduced pulmonary artery with retrograde flow in the pulmonary valve was registrated. Hydrops fetal is detected in 2 (9.5 %) cases. The left aortic arch was in 17 (80.9 %) cases and right aortic arch – 4 (19.1 %). The average gestational age at prenatal diagnosis was 22,6 weeks (range 11–32 weeks). Early diagnosis is represented by one case in 11 weeks. Cardiac defects were registered in 6 (28.5 %) cases and extracardiac defects in 5 (23.8 %) cases. Ventriculocoronary arterial communications were found in 2 (9.5 %) cases of PA-IVS. In 3 (13 %) cases were in combination with heterotaxy syndrome. In 2 (8.7 %) cases PA-IVS were in combination with left atrial isomerism and 1 (4.8 %) with right atrial isomerism. Outcomes in fetuses with PA-IVC: termination of pregnancy — 13 (61.9 %), fetal death — 2 (9.5 %), neonatal death — 5 (23.8 %) cases, only 1 (4.8 %) survivor.





2021 ◽  
pp. 1-3
Author(s):  
Marie Wilkin ◽  
Jean Michel Rauzier ◽  
Caroline Ovaert

Abstract Coronary abnormalities are frequent in pulmonary atresia and intact ventricular septum, mainly in patients with a very diminutive right ventricle. They severely impact on early and late prognosis. We describe an 8-year-old girl who presented with myocardial ischaemia, late after uneventful Fontan completion. The importance of precise delineation of the coronary anatomy upon initial assessment and during follow-up is emphasised.



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