Prenatal Diagnosis of Severe Tricuspid Insufficiency in Ebstein's Anomaly with Pulmonary Atresia and Intact Ventricular Septum: A Case Report

2000 ◽  
Vol 26 (3) ◽  
pp. 223-226 ◽  
Author(s):  
Tae-Bok Song ◽  
Jee-Young Lee ◽  
Yoon-Ha Kim ◽  
Bong-Suk Oh ◽  
Eun-Kyung Kim
Keyword(s):  
Case Report ◽  
Prenatal Diagnosis ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Ebstein’S Anomaly ◽  
Intact Ventricular Septum ◽  
Ebstein's Anomaly ◽  
Tricuspid Insufficiency

Comparison of the offset distance of the tricuspid septal leaflet in neonates with Ebstein’s anomaly and neonates with pulmonary atresia with intact ventricular septum

2014 ◽  
Vol 25 (1) ◽  
pp. 129-136 ◽  
Author(s):  
Min Jeong Kim ◽  
Jeong Jin Yu ◽  
So Yeon Kang ◽  
Chang Deok Seo ◽  
Jae Suk Baek ◽  
...  
Keyword(s):  
Body Surface ◽  
Pulmonary Atresia ◽  
The Body ◽  
Ventricular Septum ◽  
Ebstein’S Anomaly ◽  
Intact Ventricular Septum ◽  
Quantitative Criterion ◽  
Ebstein's Anomaly ◽  
Offset Distance ◽  
Offline Analysis

AbstractAn indexed offset distance of the tricuspid septal leaflet ⩾8 mm/m2is a quantitative criterion for the diagnosis of Ebstein’s anomaly. The purpose of this study was to investigate the validity of this criterion for the discrimination of Ebstein’s anomaly from pulmonary atresia with intact ventricular septum in neonatal patients. A total of 122 neonatal patients, 56 with Ebstein’s anomaly and 66 with pulmonary atresia with intact ventricular septum, were enrolled. Diagnosis of each anomaly was based on typical morphologic features. Echocardiographic variables, including the offset distance of the tricuspid septal leaflet, were measured via an offline analysis of images recorded before 1 month of age. The offset distance of the tricuspid septal leaflet was indexed by the body surface area, and the indexed offset distances in the Ebstein’s anomaly and pulmonary atresia with intact ventricular septum groups were 34.2 mm/m2(7.1–119.1 mm/m2) and 7.2 mm/m2(0.0–25.6 mm/m2), respectively. The indexed offset distance was ⩾8 mm/m2in 29 (43.9%) of the patients with pulmonary atresia with intact ventricular septum; clinical and echocardiographic characteristics were comparable between these 29 patients and the remaining 37 patients with pulmonary atresia with intact ventricular septum. When an indexed offset distance ⩾8 mm/m2was applied as a cut-off for the diagnosis of Ebstein’s anomaly, the sensitivity was 0.963 and the specificity was 0.561. In conclusion, indexed offset distance ⩾8 mm/m2cannot be used as a cut-off for the diagnosis of complicated Ebstein’s anomaly in neonatal patients with pulmonary atresia with intact ventricular septum.

Point ablation for macro-reentrant ventricular tachycardia associated with Ebstein’s anomaly and pulmonary atresia: a case report

2020 ◽  
pp. 1-3
Author(s):  
Keiko Toyohara ◽  
Yasuko Tomizawa ◽  
Morio Shoda
Keyword(s):  
Ventricular Tachycardia ◽  
Case Report ◽  
Catheter Ablation ◽  
Right Ventricle ◽  
Low Voltage ◽  
Pulmonary Atresia ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Slow Conduction ◽  
Hypoplastic Right Ventricle

Abstract We report a case with Ebstein’s anomaly and pulmonary atresia with sustained monomorphic ventricular tachycardia in a patient without a ventriculotomy history. In the low voltage area between the atrialised right ventricle and hypoplastic right ventricle, there was a ventricular tachycardia substrate and slow conduction. The tachycardia circuit was eliminated by a point catheter ablation at the area with diastolic fractionated potentials.

Congenital pulmonary atresia with intact ventricular septum, tricuspid insufficiency, and patent ductus arteriosus in two sibs

1989 ◽  
Vol 32 (2) ◽  
pp. 187-188 ◽  
Author(s):  
Nancy L. Eriksen ◽  
Louis Buttino ◽  
Richard C. Juberg ◽  
John M. Opitz ◽  
James F. Reynolds
Keyword(s):  
Patent Ductus Arteriosus ◽  
Ductus Arteriosus ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Tricuspid Insufficiency ◽  
Patent Ductus

scholarly journals Right Ventricle-dependent Coronary Circulation in Pulmonary Atresia with Intact Ventricular Septum: A Case Report

2005 ◽  
Vol 21 (5) ◽  
pp. 236-240
Author(s):  
Meng-Hsun Lee ◽  
Jiunn-Ren Wu ◽  
Zeng-Kong Dai ◽  
Jong-Hau Hsu ◽  
Chau-Chi Chou ◽  
...  
Keyword(s):  
Case Report ◽  
Right Ventricle ◽  
Coronary Circulation ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum

Prenatal Diagnosis of Pulmonary Atresia With an Intact Ventricular Septum and Ebstein Malformation

2006 ◽  
Vol 25 (8) ◽  
pp. 1069-1073 ◽  
Author(s):  
Jeng-Hsiu Hung ◽  
Jen-Her Lu ◽  
Jamie Hung ◽  
Jen-Chong Wong
Keyword(s):  
Prenatal Diagnosis ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum

Prenatal Diagnosis of Pulmonary Atresia With Intact Ventricular Septum

1998 ◽  
Vol 14 (2) ◽  
pp. 67-70
Author(s):  
Carolyn T. Coffin ◽  
Julia A. Drose ◽  
Elizabeth M. Shaffer
Keyword(s):  
Prenatal Diagnosis ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum
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