scholarly journals Cochlear Implantation in Patients with Neurofibromatosis Type 2 and Patients with Vestibular Schwannoma in the Only Hearing Ear

2012 ◽  
Vol 2012 ◽  
pp. 1-12 ◽  
Author(s):  
Erika Celis-Aguilar ◽  
Luis Lassaletta ◽  
Javier Gavilán
Keyword(s):  
Cochlear Implants ◽  
Vestibular Schwannoma ◽  
Cochlear Implantation ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Environmental Sound ◽  
Auditory Brainstem Implant ◽  
Surgical Option

Cochlear implants are a new surgical option in the hearing rehabilitation of patients with neurofibromatosis type 2 (NF2) and patients with vestibular schwannoma (VS) in the only hearing ear. Auditory brainstem implant (ABI) has been the standard surgical treatment for these patients. We performed a literature review of patients with NF2 and patients with VS in the only hearing ear. Cochlear implantation (CI) provided some auditory benefit in all patients. Preservation of cochlear nerve integrity is crucial after VS resection. Results ranged from environmental sound awareness to excellent benefit with telephone use. Promontory stimulation is recommended although not crucial. MRI can be performed safely in cochlear implanted patients.

The Auditory Brainstem Implant in Neurofibromatosis Type 2: Experience from the Manchester Programme

Skull Base ◽  
2008 ◽  
Vol 18 (S 01) ◽  
Author(s):  
Simon Freeman ◽  
Richard Ramsden ◽  
Shakeel Saeed ◽  
Martin O'Driscoll ◽  
Deborah Mawman ◽  
...  
Keyword(s):  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Auditory Brainstem Implant

Cochlear Implantation in Patients with Neurofibromatosis Type 2 and Bilateral Vestibular Schwannoma

2006 ◽  
Vol 27 (4) ◽  
pp. 512-518 ◽  
Author(s):  
Lawrence R. Lustig ◽  
Jennifer Yeagle ◽  
Colin L. W. Driscoll ◽  
Nikolas Blevins ◽  
Howard Francis ◽  
...  
Keyword(s):  
Vestibular Schwannoma ◽  
Cochlear Implantation ◽  
Neurofibromatosis Type ◽  
Neurofibromatosis Type 2

scholarly journals Combined translabyrinthine, anterior petrosal approach for resection of collision vestibular schwannoma and petrous apex meningioma in neurofibromatosis type 2, with auditory brainstem implant placement

2021 ◽  
Vol 5 (2) ◽  
pp. V17
Author(s):  
Usman A. Khan ◽  
Jillian H. Plonsker ◽  
Rick A. Friedman ◽  
Marc S. Schwartz
Keyword(s):  
Vestibular Schwannoma ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Petrous Apex ◽  
Surgical Decision ◽  
Implant Placement ◽  
History Of ◽  
Sporadic Tumors

The natural history of neurofibromatosis type 2 (NF2) is profound bilateral hearing loss. The decision to pursue microsurgery may be more complicated in NF2 than with sporadic tumors. Schwannomas in NF2 often occur with other skull base tumors. Treatment should be tailored to preserve auditory perception for as long as possible. The authors present the case of a man with NF2 and a vestibular schwannoma who has poor hearing on the same side as a large petrous apex meningioma, both opposite to a well-hearing ear. This case highlights surgical decision-making and technical nuances during resection of collision tumors in NF2. The video can be found here: https://stream.cadmore.media/r10.3171/2021.7.FOCVID21130

scholarly journals Restoration of Hearing with an Auditory Brainstem Implant in a Patient with Neurofibromatosis Type 2

2000 ◽  
Vol 40 (10) ◽  
pp. 524-527 ◽  
Author(s):  
Yojiro SEKI ◽  
Hiromichi UMEZU ◽  
Masaaki USUI ◽  
Kozo KUMAKAWA ◽  
Fumiai KUMAGAI ◽  
...  
Keyword(s):  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Auditory Brainstem Implant

Cochlear implantation and auditory brainstem implantation in neurofibromatosis type 2

2018 ◽  
Vol 128 (9) ◽  
pp. 2163-2169 ◽  
Author(s):  
Kevin A. Peng ◽  
Mark B. Lorenz ◽  
Steven R. Otto ◽  
Derald E. Brackmann ◽  
Eric P. Wilkinson
Keyword(s):  
Cochlear Implantation ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2

Auditory Brainstem Implant: I. Issues in Surgical Implantation

1993 ◽  
Vol 108 (6) ◽  
pp. 624-633 ◽  
Author(s):  
Derald E. Brackmann ◽  
William E. Hitselberger ◽  
Ralph A. Nelson ◽  
Jean Moore ◽  
Michael D. Waring ◽  
...  
Keyword(s):  
Single Channel ◽  
Cranial Nerves ◽  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Electrode Placement ◽  
Anatomic Landmarks ◽  
Auditory Evoked Response ◽  
Auditory Brainstem Implant

Most patients with neurofibromatosis type 2 (NF2) are totally deaf after removal of their bilateral acoustic neuromas. Twenty-five patients with neurofibromatosis type 2 have been implanted with a brainstem electrode during surgery to remove an acoustic neuroma. The electrode is positioned in the lateral recess of the fourth ventricle, adjacent to the cochlear nuclei. The present electrode consists of three platinum plates mounted on a Dacron mesh backing, a design that has been demonstrated to be biocompatible and positionally stable in an animal model. Correct electrode placement depends on accurate identification of anatomic landmarks from the translabyrinthine surgical approach and also on Intrasurglcal electrophysiologic monitoring. Some tumors and their removal can result in significant distortion of the brainstem and surrounding structures. Even in the absence of Identifiable anatomic landmarks, electrode location can be adjusted during surgical placement to find the location that maximizes the auditory evoked response and minimizes activation of other monitored cranial nerves. Stimulation of the electrodes produces auditory sensations in most patients, with results similar to those of single-channel cochlear Implants. A coordinated multldlscipllnary team is essential for successful application of an auditory brainstem implant.

Ipsilateral Cochlear Implantation After Cochlear Nerve Preserving Vestibular Schwannoma Surgery in Patients With Neurofibromatosis Type 2

2014 ◽  
Vol 35 (1) ◽  
pp. 43-51 ◽  
Author(s):  
Simon Kingsley Wickham Lloyd ◽  
Fergal John Glynn ◽  
Scott Alexander Rutherford ◽  
Andrew Thomas King ◽  
Deborah Jane Mawman ◽  
...  
Keyword(s):  
Vestibular Schwannoma ◽  
Cochlear Implantation ◽  
Neurofibromatosis Type ◽  
Neurofibromatosis Type 2 ◽  
Cochlear Nerve

scholarly journals Auditory rehabilitation of patients with neurofibromatosis Type 2 by using cochlear implants

2011 ◽  
Vol 115 (4) ◽  
pp. 827-834 ◽  
Author(s):  
Pamela C. Roehm ◽  
Jon Mallen-St. Clair ◽  
Daniel Jethanamest ◽  
John G. Golfinos ◽  
William Shapiro ◽  
...  
Keyword(s):  
Cochlear Implants ◽  
Cochlear Implantation ◽  
Neurofibromatosis Type ◽  
Neurofibromatosis Type 2 ◽  
Speech Understanding ◽  
Speech Discrimination ◽  
Auditory Rehabilitation ◽  
Open Set ◽  
Cochlear Ossification

Object The aim of this study was to determine whether patients with neurofibromatosis Type 2 (NF2) who have intact ipsilateral cochlear nerves can have open-set speech discrimination following cochlear implantation. Methods Records of 7 patients with documented NF2 were reviewed to determine speech discrimination outcomes following cochlear implantation. Outcomes were measured using consonant-nucleus-consonant words and phonemes; Hearing in Noise Test sentences in quiet; and City University of New York sentences in quiet and in noise. Results Preoperatively, none of the patients had open-set speech discrimination. Five of the 7 patients had previously undergone excision of ipsilateral vestibular schwannoma (VS). One of the patients who received a cochlear implant had received radiation therapy for ipsilateral VS, and another was undergoing observation for a small ipsilateral VS. Following cochlear implantation, 4 of 7 patients with NF2 had open-set speech discrimination following cochlear implantation during extended follow-up (15–120 months). Two of the 3 patients without open-set speech understanding had a prolonged period between ipsilateral VS resection and cochlear implantation (120 and 132 months), and had cochlear ossification at the time of implantation. The other patient without open-set speech understanding had good contralateral hearing at the time of cochlear implantation. Despite these findings, 6 of the 7 patients were daily users of their cochlear implants, and the seventh is an occasional user, indicating that all of the patients subjectively gained some benefit from their implants. Conclusions Cochlear implantation can provide long-term auditory rehabilitation, with open-set speech discrimination for patients with NF2 who have intact ipsilateral cochlear nerves. Factors that can affect implant performance include the following: 1) a prolonged time between VS resection and implantation; and 2) cochlear ossification.

Use of a Multichannel Auditory Brainstem Implant for Neurofibromatosis Type 2

2003 ◽  
Vol 81 (1-4) ◽  
pp. 110-114 ◽  
Author(s):  
Marc S. Schwartz ◽  
Steven R. Otto ◽  
Derald E. Brackmann ◽  
William E. Hitselberger ◽  
Robert V. Shannon
Keyword(s):  
Neurofibromatosis Type ◽  
Auditory Brainstem ◽  
Neurofibromatosis Type 2 ◽  
Auditory Brainstem Implant
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