A Case of too Much Love from the Liver: Hereditary Hemorrhagic Telangiectasia with Liver Vascular Malformation Presenting with High-output Heart Failure

2012 ◽  
Vol 107 ◽  
pp. S434
Author(s):  
Gurshawn Singh ◽  
Talal Adhami ◽  
Naim Alkhouri
2004 ◽  
Vol 99 ◽  
pp. S138
Author(s):  
Tal B. Hazan ◽  
Rahil D. Shah ◽  
Virginia M. Kania ◽  
James E. Selis ◽  
Bradford C Gelzayd

2012 ◽  
Vol 42 (12) ◽  
pp. 861 ◽  
Author(s):  
Donghyuk Cho ◽  
Sua Kim ◽  
Mina Kim ◽  
Young Ho Seo ◽  
Woohyeun Kim ◽  
...  

2015 ◽  
Vol 44 (3) ◽  
pp. 362-365 ◽  
Author(s):  
Emmanuelle Berthelot ◽  
Laurent Savale ◽  
Anne Guyot ◽  
Farid Chakib Rahmoune ◽  
Amir Bouchachi ◽  
...  

2017 ◽  
Vol 5 (1) ◽  
pp. 232470961769283
Author(s):  
Venugopal Brijmohan Bhattad ◽  
Jennifer N. Bowman ◽  
Hemang B. Panchal ◽  
Timir K. Paul

Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is a rare genetic blood disorder that leads to abnormal bleeding due to absent capillaries and multiple abnormal blood vessels known as arteriovenous malformations. A feature of HHT is high-output heart failure due to multiple arteriovenous malformations. High-output heart failure can lead to recurrent epistaxis Kiesselbach area syndrome (REKAS), further exacerbating heart failure through increased blood loss and resultant anemia. We report a patient with HHT who presented with high-output heart failure contributing to REKAS. In patients with REKAS, we propose if anemia is present, REKAS can be avoided by correcting the anemia by increasing the hemoglobin level to greater than 9 to 10 g/dL. This decreases hyperdynamic circulation and reduces pressure in the blood vessels of the nose.


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