scholarly journals Spontaneous Hemothorax in a Patient With von Recklinghausen’s Disease

Author(s):  
Rodriguez-Guzman
2011 ◽  
Vol 17 (3) ◽  
pp. 301-303 ◽  
Author(s):  
Takuro Miyazaki ◽  
Tomoshi Tsuchiya ◽  
Tsutomu Tagawa ◽  
Naoya Yamasaki ◽  
Takeshi Nagayasu

2005 ◽  
Vol 53 (12) ◽  
pp. 649-652 ◽  
Author(s):  
Takashi Miura ◽  
Yozo Kawano ◽  
Masao Chujo ◽  
Michiyo Miyawaki ◽  
Hiromu Mori ◽  
...  

2019 ◽  
Vol 89 (2) ◽  
Author(s):  
Monia Attia ◽  
Houda Gharsalli ◽  
Haifa Rmili ◽  
Meriem Affes ◽  
Soumaya Ben Saad ◽  
...  

Neurofibromatosis type 1 (NF1), also known as Von Recklinghausen’s disease is an autosomal dominant genetic disorder. It is the most common of phacomatoses. Pulmonary complications have been rarely described in the literature. It is generally a benign disease, but has the potential for rare and fatal complications, such as spontaneous hemothorax. We reported two cases of patients with a history of von Recklinghausen’s disease. Both of them suffered sudden chest pain. Chest-X ray revealed a hemi-thoracic opacity. Enhanced chest computed tomography showed massive hemothorax, but no evidence of tumors or an obvious bleeding point in the thorax. After we had ensured a stable hemodynamic condition, we performed video-assisted thoracic surgery to remove the hematoma. No evidence of bleeding was noticed in the first patient whereas an active bleeding was observed in the second patient. We could not determine which vessel was responsible of the hemorrhage. Electrocoagulation and clot removal were performed.  Evolution was favorable for both patients. Spontaneous hemothorax is a rare and potentially life threatening NF1’s complication. A tumor like neurofibroma or more rarely vascular involvement of large or small caliber arteries may be at hemothorax’s origin.


1999 ◽  
Vol 47 (4) ◽  
pp. 538 ◽  
Author(s):  
Mi Jeong Kang ◽  
Lee Young Chung ◽  
Su Jin Kim ◽  
Jung Hun Kang ◽  
Gyeong Won Jeong ◽  
...  

1986 ◽  
Vol 48 (3) ◽  
pp. 491-499
Author(s):  
Shuhei IMAYAMA ◽  
Yutaka YASHIMA ◽  
Atsushi IRIKI ◽  
Emiko SATO ◽  
Harukuni URABE

1987 ◽  
Vol 49 (3) ◽  
pp. 460-464
Author(s):  
Kazumoto KATAGIRI ◽  
Tomohito HONDA ◽  
Satoshi ITAMI ◽  
Etsuji MATSUNAGA ◽  
Hiroshi SHINKAI ◽  
...  

1994 ◽  
Vol 81 (3) ◽  
pp. 362-373 ◽  
Author(s):  
Thomas R. Donner ◽  
Rand M. Voorhies ◽  
David G. Kline

✓ Over a 22-year period, operations were performed on 263 patients for 288 primary benign tumors of major peripheral nerves. The tumors included 85 schwannomas, 197 neurofibromas, and six plexiform neurofibromas. Total removal was achieved in 83 of the 85 schwannomas, and 76 of these patients were available for follow-up evaluation. Motor function either improved or was unchanged in 87% of these patients and 85% of those with pain in the distribution of the involved nerve had either total or partial resolution of their symptoms. Of the neurofibromas, 123 occurred in 121 patients without von Recklinghausen's disease. All tumors within this group were completely excised using a fascicular approach to the tumor. Of the 99 patients available for follow-up evaluation, 90% had either improved or unchanged motor function and 88% had partial or complete resolution of pain syndromes. Fifty-nine patients with von Recklinghausen's disease had 80 tumors removed: 74 fusiform tumors (58 of which were completely removed) and six plexiform tumors. Forty-eight of the 58 patients with gross total removal of fusiform tumors were available for follow-up evaluation, of whom 83% had improved or unchanged motor function and 74% had partial or complete resolution of pain syndromes. All six patients with plexiform tumors had progression of symptoms postoperatively. One brachial plexus schwannoma recurred and was re-excised without subsequent recurrence at the 5-year follow-up evaluation. Several incompletely excised plexiform neurofibromas have recurred with a symptomatic presentation.


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