Carpal Tunnel Syndrome Due to Fibrolipomatous Hamartoma of the Median Nerve in Klippel-Trénaunay Syndrome

2009 ◽  
Vol 91 (5) ◽  
pp. 1223-1227 ◽  
Author(s):  
Mitsuhiro Matsubara ◽  
Hirotaka Tanikawa ◽  
Yuuji Mogami ◽  
Shunichi Shibata ◽  
Shigeharu Uchiyama ◽  
...  
Keyword(s):  
Carpal Tunnel Syndrome ◽  
Median Nerve ◽  
Carpal Tunnel ◽  
Fibrolipomatous Hamartoma ◽  
Tunnel Syndrome ◽  
Klippel Trenaunay Syndrome

scholarly journals Carpal Tunnel Syndrome due to Fibrolipomatous Hamartoma of the Median Nerve

Hand ◽  
2010 ◽  
Vol 6 (1) ◽  
pp. 76-79 ◽  
Author(s):  
Jamal Louaste ◽  
Hassan Zejjari ◽  
Mohamed Chkoura ◽  
Aziz Houmadi ◽  
Khalid Rachid
Keyword(s):  
Carpal Tunnel Syndrome ◽  
Median Nerve ◽  
Carpal Tunnel ◽  
Fibrolipomatous Hamartoma ◽  
Tunnel Syndrome

scholarly journals Carpal Tunnel Syndrome Associated with Klippel-Trénaunay Syndrome: A Case Report

2020 ◽  
Vol 6 (3) ◽  
pp. 161-164
Author(s):  
Joan Arenas-Prat ◽  
Keyword(s):  
Carpal Tunnel Syndrome ◽  
Median Nerve ◽  
Carpal Tunnel ◽  
Peripheral Nerves ◽  
Distribution Area ◽  
Left Hand ◽  
Nerve Involvement ◽  
Tunnel Syndrome ◽  
Operative Findings ◽  
Klippel Trenaunay Syndrome

Background and Importance: Klippel-Trénaunay syndrome is a rare congenital condition that rarely affects peripheral nerves. Median nerve involvement at the carpal tunnel level has only been reported on four occasions of this syndrome in the medical literature. Case Presentation: A 61-year-old Caucasian female patient with Klippel-Trénaunay syndrome presented with a 10-month history of paraesthesia and numbness affecting the median nerve distribution area of her left hand. The clinical and neurophysiological examination confirmed a moderately severe carpal tunnel syndrome that required surgical decompression. Conclusion: Pre-operative findings demonstrated diffuse vascular infiltration and engorgement of the median nerve. Flexor tendons had a normal appearance. The patient had a satisfactory post-operative period with full resolution of her symptoms 4 weeks after the procedure. Although peripheral nerves are rarely affected in patients with Klippel-Trénaunay syndrome, neurological symptoms could indicate nerve involvement and magnetic resonance imaging (MRI) examination should be considered to further assess the extension of the lesion.

scholarly journals Carpal Tunnel Syndrome Caused by A Fibrolipomatous Hamartoma of the Median Nerve

2021 ◽  
pp. 20200090
Author(s):  
Fouad Aladel ◽  
Ahmed Aldhafiri ◽  
Thabet Alghazal ◽  
Fahad Alsafran ◽  
Zainab Alrashed ◽  
...  
Keyword(s):  
Carpal Tunnel Syndrome ◽  
Median Nerve ◽  
Carpal Tunnel ◽  
Peripheral Nerves ◽  
Benign Lesion ◽  
Invasive Procedure ◽  
Fibrolipomatous Hamartoma ◽  
Tunnel Syndrome ◽  
The Right ◽  
Patient At Risk

Fibrolipomatous hamartoma (FLH) of the nerve (also known as perineural lipoma, neural fibrolipoma, or lipomatosis of the nerve) is a well-known, rare benign lesion that can affect any peripheral nerve, resulting in significant enlargement of the involved nerve with fibrofatty infiltration. Although it is most commonly involving the median nerve, other peripheral nerves can be also involved. Being familiar with the pathognomonic characteristics on different imaging modalities and the association of this entity with macrodactyly help reach the diagnosis, avoid putting the patient at risk of an invasive procedure, and can guide management. We present to you a rare case of a FLH of the median nerve that was diagnosed on MRI of an adult female who presented with carpal tunnel syndrome (CTS) and progressive swelling of the right hand and wrist.

scholarly journals Carpal Tunnel Syndrome Secondary to Fibrolipomatous Hamartoma of the Median Nerve

Cureus ◽  
2021 ◽  
Author(s):  
Christopher R Michel ◽  
Christopher Dijanic ◽  
Mark Woernle ◽  
Justin Fernicola ◽  
Jamie Grossman
Keyword(s):  
Carpal Tunnel Syndrome ◽  
Median Nerve ◽  
Carpal Tunnel ◽  
Fibrolipomatous Hamartoma ◽  
Tunnel Syndrome
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