A Case of Extrinsic Compression of the Left Main Coronary Artery by Dilated Pulmonary Artery in Eisenmengers Syndrome

2021 ◽  
Vol 4 (1) ◽  
pp. 01-03
Author(s):  
Varshit Hathi ◽  
Nagamani Alur Chikkabasavaiah ◽  
Beeresh Puttegowda ◽  
Yeriswamy Yeriswamy ◽  
Ramesh Basavappa ◽  
...  

The extrinsic compression of the left main coronary artery secondary to pulmonary artery trunk dilatation is a relatively rare syndrome. [1,2] It is mostly associated with congenital acyanotic heart disease, idiopathic pulmonary arterial dilatation or primary pulmonary hypertension. [3,4] Most cases of pulmonary artery hypertension with no atherosclerotic risk factors rarely undergo coronary angiography, and hence, diagnoses are seldom made and proper management is delayed.We describe a patient with Ostium secundum atrial septal defect with severe pulmonary hypertension who presented with clinical angina ,diagnosed to have left main coronary artery compression by CT angiography ,underwent successful percutaneous coronary intervention with good symptomatic relief.

1999 ◽  
Vol 83 (6) ◽  
pp. 984-986 ◽  
Author(s):  
Steven M Kawut ◽  
Frank E Silvestry ◽  
Victor A Ferrari ◽  
David DeNofrio ◽  
Leon Axel ◽  
...  

2017 ◽  
Vol 7 (3) ◽  
pp. 734-740 ◽  
Author(s):  
Akihiro Hirashiki ◽  
Shiro Adachi ◽  
Yoshihisa Nakano ◽  
Yoshihiro Kamimura ◽  
Takeshi Ogo ◽  
...  

Left main coronary artery (LMCA) disease due to external compression by a dilated main pulmonary artery (MPA) is an uncommon clinical entity. Here, we describe a 52-year-old woman with pulmonary arterial hypertension (PAH) and anteroseptal old myocardial infarction (OMI). The cause of the OMI was external compression of the LMCA by the dilated MPA and aneurysm of the left coronary sinus of Valsalva. The patient’s sister (aged 56 years) had also been diagnosed with PAH and both women had a novel heterozygous splicing mutation, IVS2-2A > G (c.374-2A > G in NM_001456), in the filamin A ( FLNA) gene. To our knowledge, this is the first report of HPAH which is likely to be due to FLNA mutation and compression of the LMCA between a dilated MPA and aneurysm of the left coronary sinus of Valsalva.


Sign in / Sign up

Export Citation Format

Share Document