Scimitar syndrome associated with ventricular septal defect and left pulmonary vein stenosis

We present the case of a 2-year-old girl with congenital stenosis of the left inferior pulmonary vein associated with a large perimembranous ventricular septal defect. The child underwent repair of the left inferior pulmonary vein with autologous left atrial appendage as a pedicled tube, followed by closure of the ventricular septal defect. Important technical steps to minimize the restenosis rate are highlighted.

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Proximal Isovelocity Surface Area Method for Diagnosing Isolated Pulmonary Vein Stenosis in a Case of Complete Atrioventricular Septal Defect With Increased Pulmonary Venous Blood Flow

A & A Practice ◽

10.1213/02054229-900000000-99774 ◽

2018 ◽

pp. 1

Author(s):

Saravana Babu ◽

Shrinivas Gadhinglajkar ◽

Rupa Sreedhar ◽

Kirubanand Senniappan ◽

Chennakeshavallu G. N. ◽

...

Keyword(s):

Blood Flow ◽

Pulmonary Vein ◽

Septal Defect ◽

Venous Blood ◽

Atrioventricular Septal Defect ◽

Pulmonary Vein Stenosis ◽

Venous Blood Flow ◽

Proximal Isovelocity Surface Area ◽

Vein Stenosis ◽

Complete Atrioventricular

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Complete congenital obstruction of a scimitar vein in an infant with severe respiratory failure

Cardiology in the Young ◽

10.1017/s1047951109990825 ◽

2009 ◽

Vol 19 (5) ◽

pp. 524-526

Author(s):

Alexandra Bauch ◽

Kyong-Jin Lee ◽

Shi-Joon Yoo

Keyword(s):

Pulmonary Hypertension ◽

Respiratory Failure ◽

Atrial Septal Defect ◽

Pulmonary Vein ◽

Septal Defect ◽

Scimitar Syndrome ◽

Severe Respiratory Failure ◽

Complete Obstruction ◽

Left Pulmonary Vein

AbstractWe report an infant of 3 1/2 months with complete obstruction of the venous component of the scimitar syndrome, a large atrial septal defect within the oval fossa, a common left pulmonary vein, and pulmonary hypertension. To the best of our knowledge, ours is the first description of complete congenital obstruction of a scimitar vein.

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Congenital Pulmonary Vein Stenosis with Anomalous Pulmonary Venous Connection

Asian Cardiovascular and Thoracic Annals ◽

10.1177/021849230701500517 ◽

2007 ◽

Vol 15 (5) ◽

pp. 438-440 ◽

Cited By ~ 1

Author(s):

Shin Takabayashi ◽

Hideto Shimpo ◽

Kazuto Yokoyama ◽

Masaki Kajimoto ◽

Koji Onoda

Keyword(s):

Pulmonary Vein ◽

Septal Defect ◽

Superior Vena ◽

Vena Cava ◽

Pulmonary Vein Stenosis ◽

The Right ◽

Vein Stenosis ◽

Anomalous Pulmonary Venous Connection ◽

Right Lower Lobectomy ◽

Congenital Pulmonary Vein Stenosis

An 11-month-old boy with congenital pulmonary vein stenosis, partial anomalous pulmonary venous connection, and ventricular septal defect is described. Angiocardiography demonstrated stenosis between the right upper pulmonary vein and high superior vena cava and obstruction of the right lower pulmonary vein. For pulmonary vein stenosis, we performed transverse sutured plasty for the right upper pulmonary vein, followed by right lower lobectomy. In some patients, combined management for pulmonary vein stenosis is effective.

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