Therapeutic Options in Alpha-1 Antitrypsin Deficiency: Liver Transplantation

2017 ◽  
pp. 263-265 ◽  
Author(s):  
Nedim Hadzic
Keyword(s):  
Liver Transplantation ◽  
Therapeutic Options ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin

Good and Bad Prognosis of Alpha-1-Antitrypsin Deficiency in Children: When to List for Liver Transplantation

2007 ◽  
Vol 39 (10) ◽  
pp. 3186-3188 ◽  
Author(s):  
A. Bakula ◽  
P. Socha ◽  
J. Pawlowska ◽  
M. Teisseyre ◽  
I. Jankowska ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin

scholarly journals Cardiac Failure after Liver Transplantation Requiring a Biventricular Assist Device

2014 ◽  
Vol 2014 ◽  
pp. 1-4
Author(s):  
Rita Jermyn ◽  
Eiei Soe ◽  
David D’Alessandro ◽  
Julia Shin ◽  
William Jakobleff ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Postoperative Complications ◽  
Liver Transplant ◽  
Hereditary Hemochromatosis ◽  
Iron Deposition ◽  
Circulatory Support ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin ◽  
Long Term Prognosis

Increased hepatic iron load in extrahepatic organs of cirrhotic patients with and without hereditary hemochromatosis portends a poorer long term prognosis after liver transplant. Hepatic as well as nonhepatic iron overload is associated with increased infectious and postoperative complications, including cardiac dysfunction. In this case report, we describe a cirrhotic patient with alpha 1 antitrypsin deficiency and nonhereditary hemochromatosis (non-HFE) that developed cardiogenic shock requiring mechanical circulatory support for twenty days after liver transplant. Upon further investigation, she was found to have significant iron deposition in both the liver and heart biopsies. Her heart regained complete and sustained recovery following ten days of mechanical biventricular support. This case highlights the importance of preoperatively recognizing extrahepatic iron deposition in patients referred for liver transplantation irrespective of etiology of liver disease as this may prevent postoperative complications.

Alpha-1-Antitrypsin Deficiency: Outcomes After Liver Transplantation

2008 ◽  
Vol 40 (5) ◽  
pp. 1492-1494 ◽  
Author(s):  
N. Kemmer ◽  
T. Kaiser ◽  
V. Zacharias ◽  
G.W. Neff
Keyword(s):  
Liver Transplantation ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin

scholarly journals Severe hypertension after liver transplantation in alpha 1 antitrypsin deficiency.

1990 ◽  
Vol 65 (11) ◽  
pp. 1217-1221 ◽  
Author(s):  
G Noble-Jamieson ◽  
N D Barnes ◽  
S Thiru ◽  
A P Mowat
Keyword(s):  
Liver Transplantation ◽  
Severe Hypertension ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin

Liver transplantation for alpha-1-antitrypsin deficiency in children

2000 ◽  
Vol 13 (3) ◽  
pp. 207-210 ◽  
Author(s):  
Andreas A. Prachalias ◽  
Mohamed Kalife ◽  
Ruggiero Francavilla ◽  
Paolo Muiesan ◽  
Anil Dhawan ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin

Long term results of liver transplantation for alpha-1 antitrypsin deficiency

2020 ◽  
Author(s):  
Olivier Guillaud ◽  
Emmanuel Jacquemin ◽  
Eduardo Couchonnal ◽  
Claire Vanlemmens ◽  
Claire Francoz ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Long Term Results ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin
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