The issue of congenital tumors of the sacrococcygeal region is far from new. The famous French obstetrician Philippe Retz wrote as early as 1694 about a similar tumor that was twice the size of a newborn's head and hindered childbirth. But all previous reports were limited to a macroscopic description of the size, shape and location of the tumor. When the microscope came to the aid of the clinic, however, the interesting structure of these tumors attracted the attention of researchers, who tried to work out their classification and identify their pathogenesis. In spite of numerous works in this direction, this question, however, has not yet been completely solved. It will be solved, as Pozharisky says, only when we are able to read the last pages of tumor doctrine.