Surgical closure of the tricuspid valve for pulmonary atresia, intact ventricular septum, and right ventricle to coronary artery communications

1984 ◽  
Vol 5 (3) ◽  
pp. 221-223 ◽  
Author(s):  
J. Deane Waldman ◽  
John J. Lamberti ◽  
James W. Mathewson ◽  
Lily George
Keyword(s):  
Coronary Artery ◽  
Right Ventricle ◽  
Tricuspid Valve ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Surgical Closure

Critical stenosis of a right ventricle to coronary artery fistula seen at dual-source CT in a newborn with pulmonary atresia and intact ventricular septum

2011 ◽  
Vol 41 (8) ◽  
pp. 1069-1072 ◽  
Author(s):  
Pierre-Emmanuel Séguéla ◽  
Lucile Houyel ◽  
Philippe Loget ◽  
Jean-Dominique Piot ◽  
Jean-François Paul
Keyword(s):  
Coronary Artery ◽  
Right Ventricle ◽  
Pulmonary Atresia ◽  
Coronary Artery Fistula ◽  
Ventricular Septum ◽  
Dual Source Ct ◽  
Intact Ventricular Septum ◽  
Critical Stenosis ◽  
Dual Source

Further morphologic studies on hearts with pulmonary atresia and intact ventricular septum

1991 ◽  
Vol 1 (2) ◽  
pp. 105-113 ◽  
Author(s):  
Robert H. Anderson ◽  
Christine Anderson ◽  
James R. Zuberbuhler
Keyword(s):  
Right Ventricle ◽  
Right Ventricular ◽  
Tricuspid Valve ◽  
Coronary Arteries ◽  
Pulmonary Atresia ◽  
Outflow Tract ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Ventricular Cavity ◽  
The Right

SummaryAtresia of the outflow tract of the right ventricle in the presence of an intact ventricular septum poses major problems for surgical management. In the light of known problems, 43 autopsied hearts with this congenital abnormality were evaluated to note the arrangement of the myocardium and the cavity of the right ventricle, the state of the tricuspid valve, the precise substrate for pulmonary atresia, and the presence offistulous communications between the ventricular cavity and the coronary arteries. The specimens could be divided into two groups. The first group (38 hearts) had hypoplasia of the cavity of the right ventricle with mural hypertrophy while the second group (5 hearts) had a dilated right ventricular cavity with thinning of the wall. The larger group could be divided into two subgroups on the basis of the substrate for pulmonary atresia. Twenty hearts had muscular atresia of the right ventricular outflow tract and 18 had a potentially patent outflow tract blocked by an imperforate pulmonary valve. A comparison of these two subgroups revealed that mural hypertrophy and cavitary hypoplasia were more severe in hearts with muscular atresia. The tricuspid valve was hypoplastic and its leaflets were not dysplastic in this group but the leaflets were dysplastic in hearts with valvar pulmonary atresia. Fistulous communications between the ventricular cavity and the coronary arteries were only seen in the cases with muscular atresia. In this series, recognition of muscular pulmonary atresia would have identified those patients with the worst surgical prognosis.

scholarly journals Treatment of right ventricle to coronary artery connections in infants with pulmonary atresia and intact ventricular septum

2008 ◽  
Vol 136 (3) ◽  
pp. 749-756 ◽  
Author(s):  
John E. Foker ◽  
Shaun P. Setty ◽  
James Berry ◽  
Prachi Jain ◽  
Kirsti Catton ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Right Ventricle ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum

scholarly journals Management of Congenital Heart Disease: State of the Art—Part II—Cyanotic Heart Defects

Children ◽  
2019 ◽  
Vol 6 (4) ◽  
pp. 54 ◽  
Author(s):  
P. Syamasundar Rao
Keyword(s):  
Pulmonary Artery ◽  
Right Ventricle ◽  
Congenital Heart ◽  
Heart Defects ◽  
Pulmonary Atresia ◽  
Ventricular Septum ◽  
Intact Ventricular Septum ◽  
Surgical Closure ◽  
Review Management ◽  
Different Types

In this review management of the most common cyanotic congenital heart defects (CHDs) was discussed; the management of acyanotic CHD was reviewed in Part I of this series. While the need for intervention in acyanotic CHD is by and large determined by the severity of the lesion, most cyanotic CHDs require intervention, mostly by surgery. Different types of tetralogy of Fallot require different types of total surgical corrective procedures, and some may require initial palliation, mainly by modified Blalock–Taussig shunts. Babies with transposition of the great arteries with an intact ventricular septum as well as those with ventricular septal defects (VSD) need an arterial switch (Jatene) procedure while those with both VSD and pulmonary stenosis should be addressed by Rastelli procedure. These procedures may need to be preceded by prostaglandin infusion and/or balloon atrial septostomy in some babies. Infants with tricuspid atresia require initial palliation either with a modified Blalock–Taussig shunt or banding of the pulmonary artery and subsequent staged Fontan (bidirectional Glenn and fenestrated Fontan with extra-cardiac conduit). Neonates with total anomalous pulmonary venous connection are managed by anastomosis of the common pulmonary vein with the left atrium either electively in non-obstructed types or as an emergency procedure in the obstructed types. Babies with truncus arteriosus are treated by surgical closure of VSD along with right ventricle to pulmonary artery conduit. The other defects, namely, hypoplastic left heart syndrome, pulmonary atresia with intact ventricular septum, double-outlet right ventricle, double-inlet left ventricle and univentricular hearts largely require multistage surgical correction. The currently existing medical, trans-catheter and surgical techniques to manage cyanotic CHD are safe and effective and can be performed at a relatively low risk.

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