First Description of Three Patients with Multifocal Lymphangiomatosis and Protein-Losing Enteropathy Following Palliation of Complex Congenital Heart Disease with Total Cavo-Pulmonary Connection

2008 ◽  
Vol 29 (4) ◽  
pp. 771-774 ◽  
Author(s):  
M. Glöckler ◽  
T. Severin ◽  
R. Arnold ◽  
P. Greiner ◽  
K. O. Schwab ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Complex Congenital Heart Disease ◽  
Protein Losing Enteropathy

Late presentation of the Fontan circulation

2020 ◽  
pp. 29-40
Author(s):  
Hannah Bellsham-Revell ◽  
Aaron Bell ◽  
Catherine Head
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Medical Therapy ◽  
Congenital Heart ◽  
Late Presentation ◽  
Fontan Circulation ◽  
Complex Congenital Heart Disease ◽  
Fontan Patient ◽  
Protein Losing Enteropathy ◽  
Life Threatening

A 16-year-old boy presented to the congenital heart disease department with oedema and chronic cough productive of casts. He had previously undergone Fontan completion for complex congenital heart disease overseas. Examination and basic investigations showed relapsed protein-losing enteropathy and plastic bronchitis, two significant complications of the Fontan circulation. He was extensively investigated, and his medical therapy optimized. Although initially referred for heart transplant assessment, he has been taken off the transplant list after good response to medical therapy alone. This case shows the complex multidisciplinary management of the adolescent Fontan patient with life-threatening complications.

Double-chambered left ventricle with complex congenital heart disease in an infant: an extremely rare pathology

2019 ◽  
Vol 16 (3) ◽  
pp. 187-191
Author(s):  
T.V. Rogova ◽  
A.I. Kim ◽  
A.V. Sobolev ◽  
S.A. Aleksandrova ◽  
E.V. Kholmanskaya ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Left Ventricle ◽  
Congenital Heart ◽  
Complex Congenital Heart Disease
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