Congenital Pulmonary Steal Phenomenon Associated with Tetralogy of Fallot, Right Aortic Arch, and Isolation of the Left Subclavian Artery

Tetralogy of Fallot without pulmonary valve syndrome is almost always associated with an absent ductus arteriosus. Patients with right aortic arch and retroesophageal left subclavian artery have a vascular ring if the left ductus arteriosus or its remnant and the Kommerell diverticulum are present. We report the cases of 2 infants in whom the role of an absent ductus arteriosus or its remnant is noteworthy. Both patients had a combination of tetralogy of Fallot with absent pulmonary valve syndrome and right aortic arch with retroesophageal left subclavian artery without a vascular ring. The absence of the ductus arteriosus has a role in the pathogenesis of tetralogy of Fallot with absent pulmonary valve syndrome. The absence of a ductus arteriosus in the right aortic arch with retroesophageal left subclavian artery precludes a vascular ring.

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Three-Dimensional Computed Tomography Scan Showing Isolation of the Left Subclavian Artery with Tetralogy of Fallot and Right Aortic Arch

Pediatric Cardiology ◽

10.1007/s00246-008-9321-1 ◽

2008 ◽

Vol 30 (2) ◽

pp. 203-204 ◽

Cited By ~ 1

Author(s):

Sho Takeda ◽

Yasumi Nakajima ◽

Masaaki Koide

Keyword(s):

Computed Tomography ◽

Aortic Arch ◽

Tetralogy Of Fallot ◽

Subclavian Artery ◽

Left Subclavian Artery ◽

Three Dimensional ◽

Right Aortic Arch ◽

Computed Tomography Scan ◽

Tomography Scan

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Subclavian and pulmonary artery steal phenomenon in a patient with isolated left subclavian artery and right aortic arch

Journal of Clinical Ultrasound ◽

10.1002/jcu.21874 ◽

2012 ◽

Vol 41 (4) ◽

pp. 265-268 ◽

Cited By ~ 3

Author(s):

Yasunobu Hayabuchi ◽

Miki Inoue ◽

Miho Sakata ◽

Tatsuya Ohnishi ◽

Shoji Kagami

Keyword(s):

Pulmonary Artery ◽

Aortic Arch ◽

Subclavian Artery ◽

Left Subclavian Artery ◽

Right Aortic Arch ◽

Steal Phenomenon

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Isolation of the left subclavian artery in an infant with tetralogy of Fallot, right aortic arch and DiGeorge syndrome. Echocardiographic diagnostic case study

Journal of Ultrasonography ◽

10.15557/jou.2019.0010 ◽

2019 ◽

Vol 19 (76) ◽

pp. 66-70

Author(s):

Maciej A. Karolczak ◽

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Wojciech Mądry ◽

Darren James Grégoire ◽

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...

Keyword(s):

Aortic Arch ◽

Tetralogy Of Fallot ◽

Subclavian Artery ◽

Digeorge Syndrome ◽

Left Subclavian Artery ◽

Right Aortic Arch

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Tetralogy of Fallot with coarctation of the aorta: a newly recognised developmental and anatomic syndrome

Cardiology in the Young ◽

10.1017/s1047951114000407 ◽

2014 ◽

Vol 24 (4) ◽

pp. 714-720 ◽

Cited By ~ 5

Author(s):

Elodie Perdreau ◽

Lucile Houyel ◽

Alban-Elouen Baruteau

Keyword(s):

Aortic Arch ◽

Tetralogy Of Fallot ◽

Subclavian Artery ◽

Left Subclavian Artery ◽

Pulmonary Atresia ◽

Coarctation Of The Aorta ◽

Mirror Image ◽

Right Aortic Arch ◽

Initial Assessment ◽

The Right

AbstractTetralogy of Fallot and coarctation of the aorta is an exceptional association. We report here four cases of infants referred for tetralogy of Fallot with or without pulmonary atresia associated with aortic coarctation from 1974 to 2013. All had a right aortic arch, and the coarctation was abnormally situated between the right common carotid and the right subclavian arteries. In all, two infants had an abnormal left subclavian artery and one child had DiGeorge syndrome. All underwent staged surgical repair of the left and right-sided obstructions. A review of the literature shows two types of coarctation in this context. In left aortic arch, coarctation is situated distal to the left subclavian artery. In right aortic arch, coarctation is distal to the right common carotid artery, mirror-image of interrupted left aortic arch type B, associated with anomalies of the branches of the aorta, and should be considered a complex anomaly of aortic arches in the setting of an outflow tract defect due to abnormal migration of cardiac neural crest cells. Screening for this unusual association is critical in the initial assessment of all patients with tetralogy of Fallot.

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