Duodenal and jejunal atresia with agenesis of the dorsal mesentery: “Apple peel” small bowel

1979 ◽  
Vol 137 (5) ◽  
pp. 676-678 ◽  
Author(s):  
Stojan M. Živković ◽  
Vukosava R. Miloševic
1972 ◽  
Vol 7 (4) ◽  
pp. 414-419 ◽  
Author(s):  
Gerald T. Zwiren ◽  
H. Gibbs Andrews ◽  
Peter Ahmann

1975 ◽  
Vol 10 (2) ◽  
pp. 277-279 ◽  
Author(s):  
James D. Hull ◽  
John L. Kiesel ◽  
Warren H. Proudfoot ◽  
Robert P. Belin

2013 ◽  
Vol 17 (1) ◽  
pp. 16-18 ◽  
Author(s):  
Anith Chacko ◽  
Farzanah Ismail ◽  
Sirajudeen Ellemdin

Agenesis of the dorsal mesentery is a rare occurrence that usually presents in children. It is associated with proximal small bowel malrotation as well as high jejunal atresia with discontinuity of the small bowel. We present a case report of an adolescent presenting with clinical features of proximal small bowel obstruction (confirmed on imaging) as well as acute pancreatitis. At laparotomy, he was found to have no dorsal mesentery, without small bowel atresia, and the duodenum was fixed to the posterior abdominal wall. The patient recovered well and remained symptom-free.


2019 ◽  
Vol 12 (8) ◽  
pp. e230160
Author(s):  
Jyotsna M Kirtane ◽  
Snehal A Bhange ◽  
Fazal Nabi ◽  
Varshil Shah

This is a case report of a neonate who was antenatally diagnosed with jejunal atresia which turned out to be duodenal atresia with apple peel syndrome. A previous sibling, who also had apple peel but with jejunal atresia, succumbed to sepsis after surgery. The first sibling had jejunal stenosis and had died of sepsis following surgery. Combination of duodenal atresia with apple peel is extremely rare. This coupled with a familial condition is rarer still. This case was challenging due to the short length of the gut and prolonged need for total parenteral nutrition and sepsis in postoperative period.


2015 ◽  
Vol 4 (56) ◽  
pp. 9849-9851
Author(s):  
Srinivas S ◽  
Ramesh Reddy K ◽  
Lavanya K
Keyword(s):  

2000 ◽  
Vol 124 (6) ◽  
pp. 880-882
Author(s):  
Shoji Yamanaka ◽  
Yukichi Tanaka ◽  
Motoyoshi Kawataki ◽  
Rieko Ijiri ◽  
Kiyoshi Imaizumi ◽  
...  

Abstract We present an autopsy case of a 46-day-old male infant with chromosome 22q11 deletion, which is considered the primary cause of several diseases, including DiGeorge syndrome and velocardiofacial syndrome. The patient had 2 notable congenital abnormalities: multiple dissecting pulmonary arterial aneurysms distributed in both lungs and multiple jejunal atresia with apple-peel deformity. The former, a very rare pathologic condition especially in infancy, was found incidentally at autopsy and was the primary cause of death. To our knowledge, neither of these lesions has been reported previously in a patient with chromosome 22q11 deletion.


2016 ◽  
Vol 76 (10) ◽  
Author(s):  
AK Oligmüller ◽  
E von Tucher ◽  
I Schönborn
Keyword(s):  

Author(s):  
Mahmoud Marei Marei ◽  
Mohamed Hamed Abouelfadl ◽  
Ahmed Arafa Elsayed Rawwash ◽  
Hamed Mahmoud Seleim ◽  
Wesam Mohamed Mahmoud ◽  
...  

Abstract Background High jejunal atresia is associated with significant dilatation of the proximal segment. This poses two problems: (a) calibre discrepancy with the distal unused segment and (b) hypomotility causing stasis. Tapering jejunoplasty/enteroplasty could offer a practical solution in selected cases, leading to early establishment of feeds. This work aims to evaluate the outcome of tapering jejunoplasty including its effect on establishing enteral feeding in neonates with proximal jejunal atresia. Results Twenty-two neonates with jejunal atresia (types I, II and IIIa) were reviewed. Cases with multiple atresia, apple-peel variant and meconium ileus were excluded. The included cases fell retrospectively into two groups: group A (13 cases)—very proximal atresia and significant dilatation and group B (9 cases)—mid/distal jejunal atresia. For group A, we excised only the distal tip of the dilated bowel and stripped a seromuscular triangle up to the duodenojejunal flexure and inverted the mucosa along the antimesenteric border, followed by an end-to-oblique anastomosis. For group B, we performed a standard excision of a short proximal segment and an end-to-oblique anastomosis. There was no significant difference in the gestation age or birth weight between both groups. The mean operative time was 90 min for group A and 60 min for group B. The duration until full enteral feeds became tolerated, and parenteral nutrition was weaned accordingly was shorter in group A (mean 10.8 days) as compared to group B (mean 14.5 days), p = 0.045. Conclusion Tapering jejunoplasty by seromuscular stripping and mucosal inversion facilitates early establishment of feeds in proximal jejunal atresia.


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