scholarly journals Endovascular Treatment for Type B Dissection in Marfan Syndrome: Is It Worthwhile?

2013 ◽  
Vol 95 (2) ◽  
pp. 737-749 ◽  
Author(s):  
Davide Pacini ◽  
Alessandro Parolari ◽  
Paolo Berretta ◽  
Roberto Di Bartolomeo ◽  
Francesco Alamanni ◽  
...  
2013 ◽  
Vol 82 (7) ◽  
pp. E898-E905 ◽  
Author(s):  
Guering Eid-Lidt ◽  
Jorge Gaspar ◽  
Gabriela Meléndez-Ramírez ◽  
Jorge Cervantes S. ◽  
Hector González-Pacheco ◽  
...  

Heart ◽  
2019 ◽  
Vol 105 (22) ◽  
pp. 1725-1731 ◽  
Author(s):  
Matthew Cauldwell ◽  
Philip J Steer ◽  
Stephanie L Curtis ◽  
Aarthi Mohan ◽  
Samuel Dockree ◽  
...  

ObjectivesInformation to guide counselling and management for pregnancy in women with Marfan syndrome (MFS) is limited. We therefore conducted a UK multicentre study.MethodsRetrospective observational study of women with MFS delivering between January 1998 and March 2018 in 12 UK centres reporting data on maternal and neonatal outcomes.ResultsIn total, there were 258 pregnancies in 151 women with MFS (19 women had prior aortic root replacements), including 226 pregnancies ≥24 weeks (two sets of twins), 20 miscarriages and 12 pregnancy terminations. Excluding miscarriages and terminations, there were 221 live births in 139 women. Only 50% of women received preconception counselling. There were no deaths, but five women experienced aortic dissection (1.9%; one type A and four type B—one had a type B dissection at 12 weeks and subsequent termination of pregnancy). Five women required cardiac surgery postpartum. No predictors for aortic dissection could be identified. The babies of the 131 (65.8%) women taking beta-blockers were on average 316 g lighter (p<0.001). Caesarean section rates were high (50%), particularly in women with dilated aortic roots. In 55 women, echocardiographic aortic imaging was available prepregnancy and postpregnancy; there was a small but significant average increase in AoR size of 0.84 mm (Median follow-up 2.3 months)ConclusionThere were no maternal deaths, and the aortic dissection rate was 1.9% (mainly type B). There with no identifiable factors associated with aortic dissection in our cohort. Preconception counselling rates were low and need improvement. Aortic size measurements increased marginally following pregnancy.


2014 ◽  
Vol 2014 ◽  
pp. 1-6
Author(s):  
Jesus Alvarez-Garcia ◽  
Stefan Stefanov Kiuri ◽  
Alvaro Fernandez Heredero ◽  
Andres Salazar Alvarez ◽  
Nieves Aleicel Concepcion Rodriguez ◽  
...  

Objective. To analyze and evaluate medium-term results obtained in endovascular treatment of complicated type B dissection. Methods. Prospective registry and retrospective analysis of the dissections treated with endoprosthesis in 1998 and 2010. Comorbidity, clinical presentation, anatomical characteristics, and evolution were recorded. Actuarial analysis was conducted for survival, follow-up and survival free of endoleaks, and free of reintervention due to relapse and/or progression. Results. Eighteen (18) patients were treated (14 male : 4 female), with a median age of 53 years (range 29–80). Their main symptoms were acute pain in 16 cases and hypertensive crisis in 15. The indications were 10 dissections not controlled by medication, 4 aneurysm dissecans, 2 acute lower limb ischemias, and 2 Type A progressions. Median 1.7 devices were used (range 1–4). Coverage of left subclavian artery was required in 3 cases, and of subclavian and left carotid artery in other 2 cases. There was a 100% technical success. Median follow-up was 43.1 months (1.5–127 range). There were two deaths caused by multiorganic failure, early mortality of 0%, and hospital mortality of 11%. There was a case of Type I Endoleak and 5 cases which required a new intervention due to relapse and/or progression. Cumulative survival at 30 months was 88%; follow-up free of endoleaks at 36 months was 91%. Follow-up free of progression/relapse at 12 months was 88%. Conclusion. Endovascular treatment of complicated type B acute dissection is an effective therapy for this condition, with a low associated mortality and with acceptable survival.


2015 ◽  
Vol 28 ◽  
pp. 11-13
Author(s):  
Serkan Ertugay ◽  
Hakan Posacıoglu ◽  
Mustafa Parildar ◽  
Halil Bozkaya

2011 ◽  
Vol 34 (5) ◽  
pp. 1080-1084 ◽  
Author(s):  
Dominik Ketelsen ◽  
Guenay Kalender ◽  
Martin Heuschmid ◽  
Roland Syha ◽  
Stefanie Mangold ◽  
...  

Sign in / Sign up

Export Citation Format

Share Document