scholarly journals A 3-year-old boy with congenital absence of the portal vein presenting fasting hypoglycemia and postprandial hyperglycemia with hyperinsulinemia

2021 ◽  
Vol 75 ◽  
pp. 102052
Author(s):  
Hisakazu Nakajima ◽  
Kazuki Kodo
Keyword(s):  
Portal Vein ◽  
Postprandial Hyperglycemia ◽  
Congenital Absence ◽  
Fasting Hypoglycemia

Congenital Absence of the Portal Vein Presenting as Pulmonary Hypertension

2007 ◽  
Vol 57 (5) ◽  
pp. 423
Author(s):  
Suryoung Jun ◽  
Whal Lee ◽  
Jung Eun Cheon ◽  
Woo Sun Kim ◽  
In One Kim ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Portal Vein ◽  
Congenital Absence

Subclinical portal-systemic encephalopathy in a child with congenital absence of the portal vein.

1999 ◽  
Vol 21 (6) ◽  
pp. 425-428 ◽  
Author(s):  
Hiroyuki Wakamoto ◽  
Kohji Manabe ◽  
Hitoshi Kobayashi ◽  
Masatoshi Hayashi
Keyword(s):  
Portal Vein ◽  
Congenital Absence ◽  
Portal Systemic Encephalopathy

Congenital absence of the portal vein-Case report and a review of literature

2010 ◽  
Vol 23 (7) ◽  
pp. 750-758 ◽  
Author(s):  
Jana Mistinova ◽  
Frantisek Valacsai ◽  
Ivan Varga
Keyword(s):  
Case Report ◽  
Portal Vein ◽  
Congenital Absence ◽  
Review Of Literature

Congenital Absence of the Portal Vein: A Complex Disease with Multiple Manifestations and Types of Treatment

2011 ◽  
Vol 21 (04) ◽  
pp. 269-272 ◽  
Author(s):  
U. Tannuri ◽  
F. Galvão ◽  
A. J. G. Leal ◽  
N. E. Gibelli ◽  
A. C. Tannuri
Keyword(s):  
Portal Vein ◽  
Complex Disease ◽  
Congenital Absence

A case of congenital absence of the portal vein

2005 ◽  
Vol 31 (1) ◽  
pp. 43-47 ◽  
Author(s):  
K TSUJI ◽  
K NAOKI ◽  
Y TACHIYAMA ◽  
A FUKUMOTO ◽  
Y ISHIDA ◽  
...  
Keyword(s):  
Portal Vein ◽  
Congenital Absence

scholarly journals Case 177: Congenital Absence of the Portal Vein with Hepatic Adenomatosis

Radiology ◽  
2012 ◽  
Vol 262 (1) ◽  
pp. 364-367 ◽  
Author(s):  
Mohamed K. Asran ◽  
Evelyne M. Loyer ◽  
Harmeet Kaur ◽  
Haesun Choi
Keyword(s):  
Portal Vein ◽  
Congenital Absence ◽  
Hepatic Adenomatosis

The variable clinical phenotype of three patients with hepatic glycogen synthase deficiency

2017 ◽  
Vol 30 (4) ◽  
Author(s):  
Çiğdem Seher Kasapkara ◽  
Zehra Aycan ◽  
Esma Açoğlu ◽  
Saliha Senel ◽  
Melek Melahat Oguz ◽  
...  
Keyword(s):  
Glycogen Synthase ◽  
Glucose Monitoring ◽  
Glycogen Metabolism ◽  
Liver Glycogen ◽  
Postprandial Hyperglycemia ◽  
Hepatic Glycogen ◽  
Case Presentation ◽  
Ketotic Hypoglycemia ◽  
Fasting Hypoglycemia ◽  
Lactic Acidemia

AbstractBackground:Glycogen synthase deficiency, also known as glycogenosis (GSD) type 0 is an inborn error of glycogen metabolism caused by mutations in theCase presentation:Herein we report three new cases of liver glycogen synthase deficiency (GSD0). The first patient presented at the 4 years of age with recurrent hypoglycemic seizures. The second patient who is the brother of the first patient presented at 15 months with asymptomatic incidental hypoglycemia. Glucose monitoring in both patients revealed daily fluctuations from fasting hypoglycemia to postprandial hyperglycemia and lactic acidemia. A third patient was consulted for ketotic hypoglycemia and postprandial hyperglycemia at the 5 years of age.Conclusions:Genetic analyses of the siblings revealed homozygosity for mutation c.736C>T on the

Congenital absence of the portal vein associated with focal nodular hyperplasia of the liver and cystic dysplasia of the kidney

1998 ◽  
Vol 157 (4) ◽  
pp. 287-290 ◽  
Author(s):  
G. Guariso ◽  
S. Fiorio ◽  
G. Altavilla ◽  
P. G. Gamba ◽  
T. Toffolutti ◽  
...  
Keyword(s):  
Portal Vein ◽  
Focal Nodular Hyperplasia ◽  
Congenital Absence ◽  
Nodular Hyperplasia

scholarly journals Congenital Absence of the Portal Vein Complicating Hepatic Tumors

2004 ◽  
Vol 43 (3) ◽  
pp. 194-198 ◽  
Author(s):  
Kosuke TAKAGAKI ◽  
Makoto KODAIRA ◽  
Shigeru KURIYAMA ◽  
Yasushi ISOGAI ◽  
Atsuhiro NOGAKI ◽  
...  
Keyword(s):  
Portal Vein ◽  
Congenital Absence ◽  
Hepatic Tumors
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