Pulmonary arterial hypertension in patients with prior atrial switch procedure for d-transposition of great arteries (dTGA)

2010 ◽  
Vol 143 (3) ◽  
pp. 271-275 ◽  
Author(s):  
Amin Yehya ◽  
Teresa Lyle ◽  
Maria A. Pernetz ◽  
M.E. McConnell ◽  
B. Kogon ◽  
...  
Keyword(s):  
Pulmonary Arterial Hypertension ◽  
Arterial Hypertension ◽  
Transposition Of Great Arteries ◽  
Atrial Switch ◽  
Pulmonary Arterial

scholarly journals Late-onset pulmonary arterial hypertension in repaired D-transposition of great arteries: an uncommon complication

2017 ◽  
Vol 7 (2) ◽  
pp. 547-550 ◽  
Author(s):  
Janani Baskaran ◽  
Kimara S. March ◽  
Thenappan Thenappan
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Arterial Hypertension ◽  
Arterial Hypertension ◽  
Surgical Repair ◽  
Late Onset ◽  
Fatal Complication ◽  
Transposition Of Great Arteries ◽  
Pathogenic Mechanisms ◽  
Pulmonary Arterial ◽  
Uncommon Complication

Late-onset pulmonary arterial hypertension (PAH) is a rare but fatal complication in patients with childhood surgical repair of dextro-transposition of great arteries (D-TGA), especially with the Mustard and Senning procedures. The pathogenic mechanisms of PAH in patients with repaired D-TGA are not well understood and treatment is not standardized. In this manuscript, we present a case of late-onset PAH in an adult D-TGA patient after Mustard repair and discuss the pathogenic mechanisms, diagnosis, and treatment of pulmonary hypertension in repaired D-TGA.

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