New onset refractory status epilepticus: State of the art

2022 ◽  
Author(s):  
B. Périn ◽  
W. Szurhaj
Keyword(s):  
Status Epilepticus ◽  
State Of The Art ◽  
Refractory Status Epilepticus ◽  
Refractory Status ◽  
New Onset

New-onset refractory status epilepticus (NORSE) and febrile infection-related epilepsy syndrome (FIRES): State of the art and perspectives

Epilepsia ◽  
2018 ◽  
Vol 59 (4) ◽  
pp. 745-752 ◽  
Author(s):  
Nicolas Gaspard ◽  
Lawrence J. Hirsch ◽  
Claudine Sculier ◽  
Tobias Loddenkemper ◽  
Andreas van Baalen ◽  
...  
Keyword(s):  
Status Epilepticus ◽  
State Of The Art ◽  
Refractory Status Epilepticus ◽  
Epilepsy Syndrome ◽  
Refractory Status ◽  
New Onset

scholarly journals How to Help Your Patients Enroll in the New-Onset Refractory Status Epilepticus (NORSE) and Febrile Infection-Related Epilepsy Syndrome (FIRES) Family Registry, and Other Rare Epilepsy Registries

2021 ◽  
pp. 153575972199832
Author(s):  
Karnig Kazazian ◽  
Marissa Kellogg ◽  
Nora Wong ◽  
Krista Eschbach ◽  
Raquel Farias Moeller ◽  
...  
Keyword(s):  
Status Epilepticus ◽  
Refractory Status Epilepticus ◽  
Epilepsy Syndrome ◽  
Neurologic Disorder ◽  
Mortality And Morbidity ◽  
Refractory Status ◽  
Rigorous Research ◽  
Active Epilepsy ◽  
New Onset

New-onset refractory status epilepticus (NORSE) is a rare clinical presentation of refractory status epilepticus (RSE) that occurs in people without active epilepsy or preexisting neurologic disorder. Febrile infection-related epilepsy syndrome (FIRES) is a subcategory of NORSE. New-onset refractory status epilepticus/FIRES are becoming increasingly recognized; however, information pertaining to disease course, clinical outcomes, and survivorship remains limited, and mortality and morbidity are variable, but often high. The objective of the NORSE/FIRES Family Registry is to (1) provide an easily accessible and internationally available multilingual registry into which survivors or NORSE/FIRES surrogates or family members of people affected by NORSE/FIRES or their physicians can enter data in a systematic and rigorous research study from anywhere in the world where internet is available; and (2) to examine past medical history, outcomes, and quality of life for people affected by NORSE/FIRES.

scholarly journals Resolution of cryptogenic new onset refractory status epilepticus with tocilizumab

2021 ◽  
Vol 15 ◽  
pp. 100431
Author(s):  
Jonathan P. Donnelly ◽  
Nidhi Kasatwar ◽  
Shaheryar Hafeez ◽  
Ali Seifi ◽  
Andrea Gilbert ◽  
...  
Keyword(s):  
Status Epilepticus ◽  
Refractory Status Epilepticus ◽  
Refractory Status ◽  
New Onset

scholarly journals New-onset super refractory status epilepticus: A case-series

Seizure ◽  
2020 ◽  
Vol 75 ◽  
pp. 174-184 ◽  
Author(s):  
Sidra Aurangzeb ◽  
Lara Prisco ◽  
Jane Adcock ◽  
Mahiri Speirs ◽  
Simon Raby ◽  
...  
Keyword(s):  
Status Epilepticus ◽  
Case Series ◽  
Refractory Status Epilepticus ◽  
Refractory Status ◽  
New Onset

New Onset Refractory Status Epilepticus (NORSE)

2009 ◽  
Vol 284 (1-2) ◽  
pp. 220 ◽  
Author(s):  
Rahul Rathakrishnan ◽  
Einar P. Wilder-Smith
Keyword(s):  
Status Epilepticus ◽  
Refractory Status Epilepticus ◽  
Refractory Status ◽  
New Onset

New-Onset Refractory Status Epilepticus (NORSE): The Queen Square Neuro-ICU experience

2021 ◽  
Vol 125 ◽  
pp. 108387
Author(s):  
Aidan Neligan ◽  
Bellami Kerin ◽  
Matthew C Walker ◽  
Sanjeev Rajakulendran
Keyword(s):  
Status Epilepticus ◽  
Refractory Status Epilepticus ◽  
Refractory Status ◽  
New Onset

A case of very prolonged new onset refractory status epilepticus (NORSE) with no evidence of autoimmune activation and a good neurological recovery

2020 ◽  
Vol 41 (10) ◽  
pp. 3003-3006 ◽  
Author(s):  
Monica Ferlisi ◽  
Elena Greco ◽  
Tiziano Zanoni ◽  
Monica Zamagni ◽  
Marilena Casartelli Liviero ◽  
...  
Keyword(s):  
Status Epilepticus ◽  
Refractory Status Epilepticus ◽  
Neurological Recovery ◽  
Refractory Status ◽  
New Onset

New onset refractory status epilepticus research

Neurology ◽  
2019 ◽  
Vol 92 (17) ◽  
pp. 802-810 ◽  
Author(s):  
Teneille E. Gofton ◽  
Nicolas Gaspard ◽  
Sara E. Hocker ◽  
Tobias Loddenkemper ◽  
Lawrence J. Hirsch
Keyword(s):  
Status Epilepticus ◽  
Professional Education ◽  
Age Groups ◽  
Refractory Status Epilepticus ◽  
Epilepsy Syndrome ◽  
Current State ◽  
Refractory Status ◽  
Management Approaches ◽  
Active Epilepsy ◽  
New Onset

New-onset refractory status epilepticus (NORSE) is a clinical presentation, not a specific diagnosis, in a patient without active epilepsy or other preexisting relevant neurologic disorder, with new onset of refractory status epilepticus (RSE) that does not resolve after 2 or more rescue medications, without a clear acute or active structural, toxic, or metabolic cause. Febrile infection-related epilepsy syndrome is a subset of NORSE in which fever began at least 24 hours prior to the RSE. Both terms apply to all age groups. Until recently, NORSE was a poorly recognized entity without a consistent definition or approach to care. We review the current state of knowledge in NORSE and propose a roadmap for future collaborative research. Research investigating NORSE should prioritize the following 4 domains: (1) clinical features, etiology, and pathophysiology; (2) treatment; (3) adult and pediatric evaluation and management approaches; and (4) public advocacy, professional education, and family support. We consider international collaboration and multicenter research crucial in achieving these goals.

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