COMPUTED TOMOGRAPHY ANGIOGRAPHY ASSISTED EMBOLIZATION OF ARTERIOVENOUS MALFORMATION PRIOR TO DENTAL EXTRACTIONS IN A PATIENT WITH STURGE-WEBER SYNDROME

Author(s):  
GIULIANNA LIMA PINHEIRO ◽  
BERNARDO CORREIA LIMA ◽  
LUIZA MÁXIMO CUNHA PINTO ◽  
LUCIANA MOURA FARJOUN DA SILVA ◽  
MARIA APARECIDA DE ALBUQUERQUE CAVALCANTE
2014 ◽  
Vol 60 (1) ◽  
pp. 22-24
Author(s):  
Suciu Zsuzsanna ◽  
Jakó Beáta ◽  
Benedek Theodora ◽  
Benedek I

Abstract Background: Coronary arteriovenous malformation is a rare congenital disease consisting mainly in a direct communication between a coronary artery and any one of the four cardiac chambers, coronary sinus, pulmonary arteries or veins. This disease can lead to various cardiovascular events, their severity depending on the degree of the malformation. Case report: We present the case of a 56-year-old male patient, who was admitted to our institution with dyspnea, palpitation and chest pain, having a history of hypertension and hyperlipidemia, and an abnormal electrocardiogram. Physical examination did not reveal any alterations and the cardiac enzymes were in normal ranges. Cardiac computed tomography was performed before any other invasive studies, with a 64-row scanner (Somatom Sensation multislice 64 equipment, Siemens) after intravenous administration of non-ionic contrast material. CT scan revealed a large (2-2.5 mm) coronary fistula originating from the LAD to the main pulmonary artery, and multiple significant atherosclerotic coronary lesions. Coronary angiography confirmed the arteriovenous malformation between LAD and pulmonary artery, associated with three vascular coronary artery disease. Conclusions: Cardiac computed tomography angiography can help for a non-invasive diagnosis of the coronary artery malformations, in the same time revealing anatomic details which can be particulary useful for choosing the appropriate management strategy (surgical planning, interventional treatment or optimum medical treatment)


2010 ◽  
Vol 5 (5) ◽  
pp. 529-534 ◽  
Author(s):  
Kazuhiko Nishino ◽  
Yasushi Ito ◽  
Takatoshi Sorimachi ◽  
Junsuke Shimbo ◽  
Yukihiko Fujii

Sturge-Weber syndrome (SWS) is a neurocutaneous disorder presenting with a facial port-wine stain, along with an occipital leptomeningeal angiomatosis that is typically located ipsilateral to the stain. In this paper, the authors present a rare case of SWS associated with an arteriovenous malformation (AVM) instead of an angiomatosis in the ipsilateral occipital lobe. While the patient was in the care of the authors, the AVM progressively enlarged, and was accompanied by progressive stenoocclusive changes of the venous system. The resulting brain edema finally brought about a serious neurological condition 13 years after the initial diagnosis. Transarterial embolization and medical treatments decreased the edema. Subsequently, however, a large intraparenchymal cyst appeared, aggravating the patient's motor weakness. Aspiration of the cyst ameliorated these symptoms. The analysis of the fluid from the cyst revealed that it contained a very high concentration of protein. Although there is no proven pathogenic mechanism to explain these protein concentrations and the enlargement of the AVM, the authors hypothesize that the progressive edema resulted from a synergic augmentation of the inflow from the AVM and the progressive obstruction of venous drainage that is a hallmark of SWS. The formation of the cyst probably resulted from the blood vessel hyperpermeability that is inherent to SWS.


2009 ◽  
Vol 14 (1) ◽  
pp. 91-92 ◽  
Author(s):  
Giuseppe Straface ◽  
Federico Biscetti ◽  
Giovanni Ghirlanda ◽  
Andrea Flex

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