A Renal Cause for Massive Retroperitoneal Hemorrhage—renal Angiomyolipoma

1976 ◽  
Vol 116 (3) ◽  
pp. 372-374 ◽  
Author(s):  
Walter P. Beh ◽  
David H. Barnhouse ◽  
S. Harris Johnson ◽  
Matthew Marshall ◽  
Stuart E. Price
Keyword(s):  
Renal Angiomyolipoma ◽  
Retroperitoneal Hemorrhage

scholarly journals Urgent arterial embolization of ruptured renal angiomyolipoma

Open Medicine ◽  
2015 ◽  
Vol 10 (1) ◽  
Author(s):  
Selim Kervancioglu ◽  
Feyza Yilmaz
Keyword(s):  
Transarterial Embolization ◽  
Arterial Embolization ◽  
Renal Angiomyolipoma ◽  
Tumor Rupture ◽  
Retroperitoneal Hemorrhage ◽  
Life Threatening

AbstractThe most undesired complication of renal angi- omyolipoma (AML) is bleeding. Because of tumor rupture, the bleeding can spread to the retroperitoneal field and can be severe enough to be life threatening. We report a case of retroperitoneal hemorrhage caused by a ruptured AML that was successfully treated with transarterial embolization with N-butyl cyanoacrylate.

scholarly journals Renal angiomyolipoma in pregnancy: surgical management with fetal preservation - Approach in a developing setting

2016 ◽  
Vol 6 (4) ◽  
Author(s):  
Fred O. Ugwumba ◽  
Emeka F. Nnakenyi ◽  
Okechukwu C. Okafor ◽  
Augustine C. Onuh ◽  
Paschalina C. Ezechukwu ◽  
...  
Keyword(s):  
Renal Function ◽  
Surgical Management ◽  
Management Strategy ◽  
Fetal Loss ◽  
Severe Bleeding ◽  
Renal Angiomyolipoma ◽  
Retroperitoneal Hemorrhage ◽  
Unique Challenge ◽  
Renal Tumours ◽  
In Pregnancy

Renal angiomyolipomas (RAML) are uncommon benign renal tumours that are associated with a tendency to rupture resulting in sometimes- torrential retroperitoneal hemorrhage as the Wunderlich syndrome or as severe potentially exsanguinating hematuria. When hemorrhage from RAML occurs in pregnancy it presents a unique challenge requiring timely and appropriately adapted intervention with the goal of preventing fatality, preserving renal function as well as preventing fetal loss if possible. We report the management of severe bleeding from RAML in pregnancy and highlight the need to adopt a management strategy that suits the practice environment and offers the patient standard and enduring care.

scholarly journals Partial Nephrectomy for a Massive Sporadic Renal Angiomyolipoma: Case Report and Review of the Literature

2016 ◽  
Vol 2016 ◽  
pp. 1-5
Author(s):  
Jacob Albersheim-Carter ◽  
Molly Klein ◽  
Paari Murugan ◽  
Christopher J. Weight
Keyword(s):  
Partial Nephrectomy ◽  
Radical Nephrectomy ◽  
Arterial Embolization ◽  
Hemodynamic Instability ◽  
Renal Angiomyolipoma ◽  
Management Options ◽  
Retroperitoneal Hemorrhage ◽  
Common Benign Tumor ◽  
Renal Artery Embolization ◽  
Segmental Renal Artery

Introduction.Angiomyolipomas are the most common benign tumor of the kidney, associated with Tuberous Sclerosis in 20% of cases and arising sporadically in 80% of cases. Renal angiomyolipomas are neoplasms of mesenchymal origin with varying proportions of vasculature, smooth muscle spindle cells, and adipocytes, making management of such neoplasms a challenging endeavor. Possible management options include partial or radical nephrectomy and segmental renal artery embolization.Case Presentation.A 61-year-old woman admitted for a large retroperitoneal hemorrhage was discovered to have a giant, sporadic, 3818.3 g, 30.0 × 26.5 × 18.0 cm left perinephric angiomyolipoma. Given her hemodynamic instability upon presentation, she underwent segmental arterial embolization, followed by an open left partial nephrectomy. Ten-month follow-up revealed no noticeable loss of renal function.Discussion.Literature review revealed occasional renal angiomyolipomas of comparable size, with all angiomyolipomas larger than this requiring treatment with radical nephrectomy.Conclusion.We show that nephron-sparing surgery may be considered in the treatment of even the largest of renal angiomyolipomas.

S257 Renal angiomyolipoma causing retroperitoneal hemorrhage(wunderlich syndrome): Presentation of our clinical experiences

2013 ◽  
Vol 12 (4) ◽  
pp. e1365, S257
Author(s):  
S. Adanur ◽  
T. Ziypak ◽  
E. Koç ◽  
F. Özkaya ◽  
T. Yapanoğlu ◽  
...  
Keyword(s):  
Renal Angiomyolipoma ◽  
Clinical Experiences ◽  
Retroperitoneal Hemorrhage

scholarly journals Nephron sparing surgery for giant renal angiomyolipoma; a viable option?

2020 ◽  
Vol 2 (1) ◽  
Keyword(s):  
Correct Choice ◽  
Positive Outcome ◽  
Flank Pain ◽  
Benign Tumors ◽  
Histopathological Analysis ◽  
Renal Angiomyolipoma ◽  
Retroperitoneal Hemorrhage ◽  
Open Partial Nephrectomy ◽  
Nephron Sparing ◽  
Left Flank Pain

Angiomyolipomas (AML) are most common benign tumors of the Kidney. It may be an incidental diagnosis or in symptomatic patients it may cause flank pain,hematuria or renal mass. Also, sometimes renal AML may present initially as spontaneous retroperitoneal hemorrhage secondary to rupture (Wunderlich syndrome). AML >10 cm in size is known as giant AML and the data available on this entity is sparse. Herein, we report a case of a 28-year-old homemaker who had left flank pain for 3 months, on evaluation elsewhere, Ultrasonography, and Contrast Computed Tomography Scan - Kidney Ureter Bladder showed a left giant renal AML. This patient came to our centre for further management. Subsequently, this patient underwent left open Partial Nephrectomy; specimen was 21.5 cm x 16 cm x 14 cm in size and weighed 1330 g. Histopathological analysis showed AML. It is important to contemplate a primary nephron sparing approach even in a case of giant renal AML, as it may turn out to be a correct choice with a positive outcome.

scholarly journals Wunderlich’s Syndrome, or Spontaneous Retroperitoneal Hemorrhage, in a Patient with Tuberous Sclerosis and Bilateral Renal Angiomyolipoma

2017 ◽  
Vol 18 ◽  
pp. 1309-1314 ◽  
Author(s):  
Sara Catarino Santos ◽  
Liliana Duarte ◽  
Fernando Valério ◽  
Júlio Constantino ◽  
Jorge Pereira ◽  
...  
Keyword(s):  
Tuberous Sclerosis ◽  
Renal Angiomyolipoma ◽  
Retroperitoneal Hemorrhage

Retroperitoneal hemorrhage during pregnancy secondary to renal angiomyolipoma

1982 ◽  
Vol 4 (1) ◽  
pp. 255-257 ◽  
Author(s):  
Philip A. Brodey ◽  
Richard J. Gabbay ◽  
Jerome B. Jacobson
Keyword(s):  
Renal Angiomyolipoma ◽  
Retroperitoneal Hemorrhage

scholarly journals Spontaneous Retroperitoneal Hemorrhage (Wunderlich Syndrome) due to Large Upper Pole Renal Angiomyolipoma: Does Robotic-Assisted Laparoscopic Partial Nephrectomy Have a Role in Primary Treatment?

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Achilles Ploumidis ◽  
Ioannis Katafigiotis ◽  
Maria Thanou ◽  
Nikos Bodozoglou ◽  
Labros Athanasiou ◽  
...  
Keyword(s):  
Partial Nephrectomy ◽  
Arterial Embolization ◽  
Primary Treatment ◽  
Young Female ◽  
Minimal Invasive ◽  
Laparoscopic Partial Nephrectomy ◽  
Renal Angiomyolipoma ◽  
Retroperitoneal Hemorrhage ◽  
Robotic Assisted ◽  
Elective Setting

Spontaneous rapture with consequent retroperitoneal hemorrhage (Wunderlich’s syndrome) is the complication mostly feared from large renal angiomyolipomas (RAMLs). In hemodynamic stable patients, minimal invasive therapies have superseded open surgery as the mainstay of treatment, with contemporary cases mostly treated by selective arterial embolization. Robotic-assisted laparoscopic partial nephrectomy (RALPN) is an established minimal access treatment that has been used in the past for benign and malignant lesions of the kidney in the elective setting, but rarely in urgent situations as primary treatment. We present a case of a ruptured RAML in a young female treated effectively by RALPN.

Sign in / Sign up

Export Citation Format

Share Document