Tetralogy of Fallot with pulmonary atresia associated with aortopulmonary window and major aortopulmonary collaterals

1995 ◽  
Vol 5 (3) ◽  
pp. 289-290 ◽  
Author(s):  
A. R. Bhagwat ◽  
R. J. Pinto ◽  
Satyavan Sharma
Keyword(s):  
Tetralogy Of Fallot ◽  
Pulmonary Atresia ◽  
Postoperative Recovery ◽  
Aortopulmonary Window ◽  
Descending Thoracic Aorta ◽  
Additional Source ◽  
Collateral Arteries ◽  
Arterial Blood ◽  
Aortopulmonary Collaterals ◽  
Major Aortopulmonary Collaterals

SummaryWe report a patient with tetralogy of Fallot and pulmonary atresia in whom the predominant extracardiac supply of arterial blood was via an aortopulmonary window. Major aortopulmonary collateral arteries originating from the descending thoracic aorta provided an additional source of pulmonary blood flow. The patient underwent successful correction and the postoperative recovery was uneventful.

Use of pre-intervention imaging with a novel image fusion software for guidance of cardiac catheterisation in a patient with pulmonary atresia and major aortopulmonary collaterals

2016 ◽  
Vol 26 (7) ◽  
pp. 1438-1440 ◽  
Author(s):  
Sebastian Goreczny ◽  
Pawel Dryzek ◽  
Tomasz Moszura
Keyword(s):  
Image Fusion ◽  
Ct Scan ◽  
Tetralogy Of Fallot ◽  
Pulmonary Atresia ◽  
Cardiac Catheterisation ◽  
Two Dimensional ◽  
Heart Catheterisation ◽  
Aortopulmonary Collaterals ◽  
Selective Cannulation ◽  
Major Aortopulmonary Collaterals

AbstractWe present a 3.5-year-old patient with tetralogy of Fallot, pulmonary atresia, and major aortopulmonary collaterals, after repeat implantation of a central shunt, in whom we successfully re-purposed previous imaging scans with a novel image fusion software to guide diagnostic heart catheterisation. The pre-registered CT scan was segmented before the procedure and subsequently manually fused with two-dimensional fluoroscopy images. The overlaid roadmap enhanced selective cannulation of all major vessels originating from the aorta, making aortography unnecessary.

Tetralogy of Fallot with pulmonary atresia and aortopulmonary window may mimic common arterial trunk

2021 ◽  
pp. 1-5
Author(s):  
Sudesh Prabhu ◽  
Manaswini Keshav ◽  
Prakash Ramachandra ◽  
Vimal Raj ◽  
Colin John ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Tetralogy Of Fallot ◽  
Pulmonary Blood Flow ◽  
Pulmonary Atresia ◽  
Aortopulmonary Window ◽  
Collateral Arteries ◽  
Common Arterial Trunk ◽  
Arterial Trunk ◽  
Pulmonary Arterial ◽  
Morphological Differences

Abstract Tetralogy of Fallot with pulmonary atresia is a group of congenital cardiac malformations, which is defined by the absence of luminal continuity between both ventricles and the pulmonary artery, and an interventricular communication. Pulmonary arterial supply in patients with tetralogy of Fallot with pulmonary atresia can be via the arterial duct or from collateral arteries arising directly or indirectly from the aorta (systemic-to-pulmonary artery collaterals), or rarely both. The rarest sources of pulmonary blood flow are aortopulmonary window and fistulous communication with the coronary artery. Herein, we describe an outflow tract malformation, tetralogy of Fallot with pulmonary atresia and aortopulmonary window, which was misdiagnosed as common arterial trunk. We emphasise the morphological differences.

Postoperative feeding problems in patients with tetralogy of Fallot, pulmonary atresia, and major aortopulmonary collaterals undergoing unifocalisation surgery

2018 ◽  
Vol 28 (11) ◽  
pp. 1329-1332
Author(s):  
Andrew M. Koth ◽  
Charlotte Sakarovitch ◽  
Douglas R. Sidell ◽  
Lisa M. Schultz ◽  
Allison Freccero ◽  
...  
Keyword(s):  
Mechanical Ventilation ◽  
Tetralogy Of Fallot ◽  
Prolonged Mechanical Ventilation ◽  
Pulmonary Atresia ◽  
Feeding Tube ◽  
Tube Placement ◽  
22Q11 Deletion ◽  
Feeding Problems ◽  
Aortopulmonary Collaterals ◽  
Major Aortopulmonary Collaterals

AbstractBackgroundPatients with tetralogy of Fallot, pulmonary atresia, and major aortopulmonary collaterals are at risk for prolonged hospitalisation after unifocalisation. Feeding problems after congenital heart surgery are associated with longer hospital stay. We sought to determine the impact of baseline, intra-operative, and postoperative factors on the need for feeding tube use at the time of discharge.MethodsWe included patients with the aforementioned diagnosis undergoing unifocalisation from ages 3 months to 4 years from 2010 to 2016. We excluded patients with a pre-existing feeding tube. Patients discharged with an enteric tube were included in the feeding tube group. We compared the feeding tube group with the non-feeding-tube group by univariable and multi-variable logistic regression.ResultsOf the 56 patients studied, 41% used tube feeding. Median age and weight z-score were similar in the two groups. A chromosome 22q11 deletion was associated with the need for a feeding tube (22q11 deletion in 39% versus 15%, p=0.05). Median cardiopulmonary bypass time in the feeding tube group was longer (335 versus 244 minutes, p=0.04). Prolonged duration of mechanical ventilation was associated with feeding tube use (48 versus 3%, p=0.001). On multi-variable analysis, prolonged mechanical ventilation was associated with feeding tube use (odds ratio 10.2, 95% confidence intervals 1.6; 63.8).ConclusionAmong patients with tetralogy of Fallot, pulmonary atresia, and major aortopulmonary collaterals who were feeding by mouth before surgery, prolonged mechanical ventilation after unifocalisation surgery was associated with feeding tube use at discharge. Anticipation of feeding problems in this population and earlier feeding tube placement may reduce hospital length of stay.

Bronchoscopy in children with tetralogy of fallot, pulmonary atresia, and major aortopulmonary collaterals

2017 ◽  
Vol 52 (12) ◽  
pp. 1599-1604 ◽  
Author(s):  
Douglas R. Sidell ◽  
Andrew M. Koth ◽  
Holly Bauser-Heaton ◽  
Doff B. McElhinney ◽  
Lisa Wise-Faberowski ◽  
...  
Keyword(s):  
Tetralogy Of Fallot ◽  
Pulmonary Atresia ◽  
Aortopulmonary Collaterals ◽  
Major Aortopulmonary Collaterals

Pulmonary vasodilator therapy in tetralogy of Fallot with pulmonary atresia and major aortopulmonary collaterals: case series and review of literature

2017 ◽  
Vol 27 (9) ◽  
pp. 1861-1864 ◽  
Author(s):  
Sotiria C. Apostolopoulou ◽  
George Vagenakis ◽  
Spyridon Rammos
Keyword(s):  
Tetralogy Of Fallot ◽  
Pulmonary Atresia ◽  
Case Series ◽  
Review Of Literature ◽  
Vasodilator Therapy ◽  
Pulmonary Vasodilators ◽  
Pulmonary Vasodilator ◽  
Aortopulmonary Collaterals ◽  
Pulmonary Arterial ◽  
Major Aortopulmonary Collaterals

AbstractWe present the use of pulmonary vasodilators in three adult patients with unrepaired tetralogy of Fallot, pulmonary atresia, aortopulmonary collaterals, and segmental pulmonary arterial hypertension. Patients improved by 1–2 NYHA classes with modest exercise-tolerance increase, and remained stable without side effects during 2.5, 10, and 14 years. Literature review revealed five studies with pulmonary vasodilators in heterogeneous, mostly repaired patient populations.

Prenatal identification of the pulmonary arterial supply in tetralogy of Fallot with pulmonary atresia

2009 ◽  
Vol 19 (2) ◽  
pp. 185-191 ◽  
Author(s):  
Anna N. Seale ◽  
Siew Y. Ho ◽  
Elliot A. Shinebourne ◽  
Julene S. Carvalho
Keyword(s):  
Tetralogy Of Fallot ◽  
Pulmonary Arteries ◽  
Pulmonary Atresia ◽  
Postmortem Examination ◽  
Aortopulmonary Window ◽  
Cardiac Defect ◽  
Pulmonary Flow ◽  
Collateral Arteries ◽  
Arterial Duct ◽  
Pulmonary Arterial

AbstractObjectiveTo define the patterns of flow of blood to the lungs in fetuses with tetralogy of Fallot and pulmonary atresia.BackgroundIn this condition, supply of blood to the lungs is provided via an arterial duct or systemic-to-pulmonary collateral arteries, or very rarely through other conduits such as coronary arterial fistulas or an aortopulmonary window. The intrapericardial pulmonary arteries vary in size, and may be absent. These variables influence the prognosis and management.MethodsWe carried out a retrospective review of cases from a tertiary service for fetal cardiology, identifying all cases of tetralogy of Fallot with pulmonary atresia diagnosed antenatally between January, 1997, and April, 2006. We established pre- and postnatal outcomes, and compared the prenatal diagnosis with postnatal or autopsy findings.ResultsOf 6587 fetuses scanned during this period, 11 were diagnosed as having tetralogy of Fallot with pulmonary atresia and no other cardiac defect. In 5, arterial flow to the lungs was via an arterial duct, and in the other 6, the main identified source of flow was systemic-to-pulmonary collateral arteries. Of the latter 6 pregnancies, 4 were terminated, along with 3 of the 5 with ductal supply. The presence of systemic-to-pulmonary collateral arteries was confirmed at postmortem examination in 3 instances, and in the two delivered neonates, in neither of whom was an infusion of prostaglandin commenced.ConclusionThe patterns of pulmonary flow can be identified prenatally in the setting of tetralogy with pulmonary atresia. Supply through systemic-to-pulmonary collateral arteries impacts on counselling, introducing uncertainty regarding postnatal surgical management.

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