Repair in infancy of right aortic arch with aberrant left brachiocephalic artery in the setting of a variant of the hypoplastic left heart syndrome

A right aortic arch, with a retroesophageal transverse arch and an aberrant left brachiocephalic artery, is a rare anomaly by itself. When combined with severe mitral stenosis and hypoplasia of the left ventricle, it is rarer still. We describe the diagnosis and treatment of this rare anomaly in an infant using a modification of the Norwood operation.

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Total anomalous pulmonary venous connection mimicking hypoplastic left heart syndrome

Cardiology in the Young ◽

10.1017/s1047951121001670 ◽

2021 ◽

pp. 1-3

Author(s):

Ryohei Matsuoka ◽

Jun Muneuchi ◽

Yoshie Ochiai

Keyword(s):

Left Ventricle ◽

Systemic Circulation ◽

Z Score ◽

Left Heart ◽

Hypoplastic Left Heart ◽

Transverse Arch ◽

Anomalous Pulmonary Vein ◽

Pulmonary Arterial ◽

Left Heart Syndrome ◽

Anomalous Pulmonary Venous Connection

Abstract A newborn with supracardiac total anomalous pulmonary venous connection vein presented the small left ventricle with z score of −7.5, retrograde blood supply in the transverse arch, and the dutcus-dependent systemic circulation. The patient underwent the repair of the anomalous pulmonary vein and bilateral pulmonary arterial banding soon after the birth and then transcatheter pulmonary arterial debanding at the age of 10 months because of an appropriate growth of the left ventricle.

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Early results of aortic arch reconstruction and bilateral pulmonary artery banding: modification of the Norwood operation for treatment of hypoplastic left heart syndrome

Kardiologia Polska ◽

10.5603/kp.a2018.0025 ◽

2018 ◽

pp. 770-775

Author(s):

Jacek W. Pająk ◽

Michał Buczyński ◽

Piotr Stanek ◽

Grzegorz Zalewski ◽

Marek Wites ◽

...

Keyword(s):

Pulmonary Artery ◽

Aortic Arch ◽

Left Heart ◽

Norwood Operation ◽

Hypoplastic Left Heart ◽

Early Results ◽

Bilateral Pulmonary Artery Banding ◽

Aortic Arch Reconstruction ◽

Arch Reconstruction ◽

Left Heart Syndrome

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Hypoplastic left heart syndrome with right aortic arch, bilateral arterial ducts and origin of the left subclavian artery from the left pulmonary artery

Cardiology in the Young ◽

10.1017/s1047951100005047 ◽

1999 ◽

Vol 9 (3) ◽

pp. 331-334 ◽

Cited By ~ 3

Author(s):

Chandrakant R. Patel ◽

Michael L. Specter ◽

Kenneth G. Zahka

Keyword(s):

Pulmonary Artery ◽

Aortic Arch ◽

Hypoplastic Left Heart Syndrome ◽

Subclavian Artery ◽

Left Subclavian Artery ◽

Left Pulmonary Artery ◽

Right Aortic Arch ◽

Left Heart ◽

Hypoplastic Left Heart ◽

Left Heart Syndrome

AbstractThe rare association, in a left-sided heart with hypoplastic left heart syndrome, of right aortic arch, bilateral patent arterial ducts and origin of the left subclavian artery from the left pulmonary artery are described. Cardiac catheterization was performed because of the abnormal anatomy of the arch noted at echocardiographic examination. This abnormality is of surgical importance when planning the Norwood operation.

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