Apical hypertrophic cardiomyopathy: an uncommon cause of exertional chest pain in children

2019 ◽  
Vol 29 (12) ◽  
pp. 1533-1535 ◽  
Author(s):  
Qu-ming Zhao ◽  
Lan He ◽  
Fang Liu
Keyword(s):  
Chest Pain ◽  
Hypertrophic Cardiomyopathy ◽  
Apical Hypertrophic Cardiomyopathy ◽  
Cardiac Angiography ◽  
First Case ◽  
Asymptomatic Children

AbstractApical hypertrophic cardiomyopathy is an uncommon morphologic variant of hypertrophic cardiomyopathy, which is rarely diagnosed in childhood. To date, very few cases of asymptomatic children younger than 18 years have been reported in the literature. To the best of our knowledge, this is the first case of paediatric apical hypertrophic cardiomyopathy presenting with exertional chest pain, with characteristic electrocardiographic, echocardiographic, MRI, and cardiac angiography findings.

scholarly journals APICAL HYPERTROPHIC CARDIOMYOPATHY: CHEST PAIN AND PERFUSION DEFECTS ARE ASSOCIATED WITH CAVITY OBLITERATION AND POST-SYSTOLIC STRAIN

2014 ◽  
Vol 63 (12) ◽  
pp. A844
Author(s):  
Edward James Stephenson ◽  
Danielle Longchamp ◽  
James Malcolmson ◽  
Redha Boubertakh ◽  
Howell Williams ◽  
...  
Keyword(s):  
Chest Pain ◽  
Hypertrophic Cardiomyopathy ◽  
Systolic Strain ◽  
Apical Hypertrophic Cardiomyopathy ◽  
Perfusion Defects ◽  
Cavity Obliteration

scholarly journals Left Ventricular Apical Hypertrophy (Yamaguchi Disease)

2021 ◽  
Author(s):  
Hatim Al Lawati ◽  
Marwa Al Habsi ◽  
Adil B Al Riyami
Keyword(s):  
Chest Pain ◽  
Hypertrophic Cardiomyopathy ◽  
Coronary Angiography ◽  
Left Ventricular ◽  
Apical Hypertrophic Cardiomyopathy ◽  
Cardiac Evaluation ◽  
Apical Hypertrophy

Abstract Apical Hypertrophic Cardiomyopathy (Ap-HCM) also known as Yamaguchi Disease is characterized by limited involvement of the left ventricular (LV) apex. It can present with typical ischaemic chest pain, dyspnoea and arrhythmias. We report the case of patient with ischaemic chest pain who was diagnosed with Ap-HCM at the time of coronary angiography. We share representative images from his cardiac evaluation.

scholarly journals Extended Myectomy for Apical Hypertrophic Cardiomyopathy: A Case Report

2021 ◽  
Author(s):  
Daiki Saitoh ◽  
Mike Saji ◽  
Schuichiro Takanashi
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Left Ventricle ◽  
Papillary Muscle ◽  
Left Ventricular ◽  
Left Ventricular Aneurysm ◽  
Apical Hypertrophic Cardiomyopathy ◽  
End Diastolic Volume ◽  
First Case ◽  
Surgical Myectomy ◽  
Apical Hypertrophy

Abstract BackgroundApical hypertrophic cardiomyopathy is a variant of hypertrophic cardiomyopathy that predominantly affects the left ventricle apex and rarely involves the right ventricular apex or both apexes. Traditional treatment for apical hypertrophic cardiomyopathy is heart transplantation. Although surgical myectomy approaching the apex has been available for decades, its safety and accuracy greatly depend on the surgeon’s skills and experience.Case presentationThe first case is of a 63-year-old man with apical hypertrophic cardiomyopathy in whom a preoperative contrast computed tomography revealed apical hypertrophy and complete apical cavity obliteration. The patient underwent extended myectomy. The inside of the apex cavity was filled with abnormal muscles. Using the transaortic approach, the location of the bilateral papillary muscle was confirmed, which provided the required orientation. The abnormal muscle mass was successfully resected, and postoperative end-diastolic volume was extremely increased. The second case is of a 43-year-old man with an apical left ventricular aneurysm and mid- hypertrophic cardiomyopathy obstruction. The thin-walled apical aneurysm contained a large apical-basal band. After detecting the bilateral papillary muscle, mid-ventricular myectomy was performed from the apex. During postoperative catheterization, there was no pressure gradient between the left ventricle and aorta.ConclusionsWe reviewed two cases of apical hypertrophic cardiomyopathy, efficiently treated using extended apical myectomy. Although apical myectomy is an uncommon procedure, the cases presented herein show that it can successfully manage apical hypertrophic cardiomyopathy. However, it is important to secure the postoperative left ventricular end-diastolic volume.

scholarly journals Ineffective and prolonged apical contraction is associated with chest pain and ischaemia in apical hypertrophic cardiomyopathy

2018 ◽  
Vol 251 ◽  
pp. 65-70 ◽  
Author(s):  
Edward Stephenson ◽  
Pierre Monney ◽  
Francesca Pugliese ◽  
James Malcolmson ◽  
Steffen E. Petersen ◽  
...  
Keyword(s):  
Chest Pain ◽  
Hypertrophic Cardiomyopathy ◽  
Apical Hypertrophic Cardiomyopathy

scholarly journals Extended myectomy for apical hypertrophic cardiomyopathy: a case report

2021 ◽  
Vol 16 (1) ◽  
Author(s):  
Daiki Saitoh ◽  
Mike Saji ◽  
Schuichiro Takanashi
Keyword(s):  
Hypertrophic Cardiomyopathy ◽  
Left Ventricle ◽  
Papillary Muscle ◽  
Left Ventricular ◽  
Left Ventricular Aneurysm ◽  
Apical Hypertrophic Cardiomyopathy ◽  
End Diastolic Volume ◽  
First Case ◽  
Surgical Myectomy ◽  
Apical Hypertrophy

Abstract Background Apical hypertrophic cardiomyopathy is a variant of hypertrophic cardiomyopathy that predominantly affects the apex of the left ventricle and rarely involves the right ventricular apex or both apexes. Heart transplantation is the traditional treatment for apical hypertrophic cardiomyopathy. Although surgical myectomy approaching the apex has been available for decades, its safety and accuracy greatly depend on the surgeon’s skills and experience. Case presentation The first case involved a 63-year-old man with apical hypertrophic cardiomyopathy, wherein preoperative contrast computed tomography findings revealed apical hypertrophy and complete apical cavity obliteration. The patient underwent extended myectomy, which revealed the apex cavity filled with abnormal muscles. Using the transaortic approach, the location of the bilateral papillary muscle was confirmed, thereby providing the required orientation. The abnormal muscle mass was successfully resected, and the postoperative end-diastolic volume was extremely increased. The second case involved a 43-year-old man with an apical left ventricular aneurysm and mid-hypertrophic cardiomyopathy obstruction. The thin-walled apical aneurysm contained a large apical-basal band. Upon detecting the bilateral papillary muscle, mid-ventricular myectomy was performed from the apex. During postoperative catheterization, there was no pressure gradient between the left ventricle and aorta. Conclusions We reviewed two cases of apical hypertrophic cardiomyopathy, efficiently treated using extended apical myectomy. Although it is an uncommon procedure, the cases presented show how it can be used to successfully manage cases of apical hypertrophic cardiomyopathy. However, it is important to secure the postoperative left ventricular end-diastolic volume.

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