Peripheral primitive neuroectodermal tumor of the small bowel mesentery: A case showing perforation at onset

2000 ◽  
Vol 50 (5) ◽  
pp. 398-403 ◽  
Author(s):  
Yasushi Horie ◽  
Masako Kato
2015 ◽  
Vol 143 (9-10) ◽  
pp. 619-622
Author(s):  
Helena Maric ◽  
Radovan Cvijanovic ◽  
Igor Ivanov ◽  
Ljiljana Gvozdenovic ◽  
Dejan Ivanov ◽  
...  

Introduction. Primitive neuroectodermal tumor or Ewing?s sarcoma is a tumor of undifferentiated small round cells that arise from the soft tissues, and is believed to be of neural origin. It occurs most often in children, followed by adolescents and young adults. Case Outline. A case of a 24-year-old patient with ulcerostenosans Ewing?s sarcoma of the initial part of the small intestine is presented in our paper. Reviewing the literature and using as an example the case of a female patient with signs of sideropenic anemia caused by primitive neuroectodermal tumor of the small intestine, an attempt was made to clarify the etiology, clinical presentation, diagnosis and therapy with the aim of its rapid detection and treatment. Conclusion. Mesenteric primitive neuroectodermal tumor is a rare neoplasm in adults, while it usually occurs in children and young adults. Surgical resection of the lesions with the application of chemotherapy is the main form of treatment of patients suffering from this disease.


2002 ◽  
Vol 5 (1) ◽  
pp. 86-90 ◽  
Author(s):  
Douglas K. Graham ◽  
Linda C. Stork ◽  
Qi Wei ◽  
J. David Ingram ◽  
Frederick M. Karrer ◽  
...  

We present a pediatric peripheral primitive neuroectodermal tumor (pPNET) localized exclusively to the small bowel. The tumor presented in an adolescent male and the diagnosis was confirmed by electron microscopy, CD99 immunopositivity, and molecular genetic analysis that demonstrated an EWS-FLI1 type 2 fusion transcript. This case report and a review of the literature underscore the considerable phenotypic overlap in EWS-related tumors in this site and the necessity for molecular genetic analysis to permit accurate classification.


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