Introduction. Primitive neuroectodermal tumor or Ewing?s sarcoma is a tumor
of undifferentiated small round cells that arise from the soft tissues, and
is believed to be of neural origin. It occurs most often in children,
followed by adolescents and young adults. Case Outline. A case of a
24-year-old patient with ulcerostenosans Ewing?s sarcoma of the initial part
of the small intestine is presented in our paper. Reviewing the literature
and using as an example the case of a female patient with signs of
sideropenic anemia caused by primitive neuroectodermal tumor of the small
intestine, an attempt was made to clarify the etiology, clinical
presentation, diagnosis and therapy with the aim of its rapid detection and
treatment. Conclusion. Mesenteric primitive neuroectodermal tumor is a rare
neoplasm in adults, while it usually occurs in children and young adults.
Surgical resection of the lesions with the application of chemotherapy is the
main form of treatment of patients suffering from this disease.