Pulmonary lymphangioleiomyomatosis masquerading as unilateral heterogeneous emphysema
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Abstract Pulmonary lymphangioleiomyomatosis (LAM) is a rare, well-described pathology and usually is exclusive to females of a reproductive age. We present a 45 year-old lady who presented to the surgeons 1 year after an admission with acute dyspnoea following influenza infection. Initial computed tomography imaging findings demonstrated severe, heterogenous right-sided bullous emphysematous changes, but histopathological analysis of the post-operative specimen favoured a diagnosis of LAM. This case demonstrates the importance of considering LAM as a differential diagnosis for findings of unilateral emphysema or lobar emphysema, in which alpha 1-antitrypsin deficiency has been excluded and in those without a significant smoking history.
1995 ◽
Vol 131
(10)
◽
pp. 1175-1177
◽
2010 ◽
Vol 9
(4)
◽
pp. 289-298
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