An unusual occurence of plexiform fibrohistiocytic tumour: congenital tumour diagnosed at 7 years of age

Pathology ◽  
2011 ◽  
Vol 43 (4) ◽  
pp. 380-381 ◽  
Author(s):  
Bahar Muezzinoglu ◽  
Aysegul Tohumcu ◽  
Gulsen Ekingen
Keyword(s):  
The Lancet ◽  
1922 ◽  
Vol 199 (5132) ◽  
pp. 17
Author(s):  
R. Handfield-Jones
Keyword(s):  

2021 ◽  
Vol 49 (2) ◽  
pp. 030006052199687
Author(s):  
Peng Zhu ◽  
Xiao-Yan Li

Pharyngeal teratomas are very rare congenital tumours derived from pluripotent stem cells. Surgical resection is the main treatment to avoid breathing and feeding difficulties. This current case report describes two newborn infants with congenital oropharyngeal teratomas. In one of the infants, the tumour presented along with a cleft tongue and cleft palate. Prenatal diagnosis by ultrasonography did not identify the tumours because the masses were small and there was no polyhydramnios. Both cases were treated surgically and histological examination of the masses in both cases confirmed the diagnosis of a congenital epignathus. There were no complications such as infection, bleeding or residual recurrence following surgery. After 1-year follow-up, there was no recurrence of the epignathus in either case. Oropharyngeal teratoma is a very rare congenital tumour that may cause upper airway obstruction and feeding difficulties in the newborn, so it should be treated surgically in a timely manner.


2017 ◽  
Vol 9 (1) ◽  
pp. 79-82 ◽  
Author(s):  
Simanta Khadka ◽  
Gulshan Bahadur Shrestha ◽  
Pragati Gautam ◽  
Jyoti Baba Shrestha

Background: Orbital teratomas are congenital, unilateral germ cell tumors, which are present at birth with moderate to massive proptosis. The rare tumour has to be managed individually and is at times difficult. Case: A female child in her 2nd day of life was brought to our department with complains of forward bulging of the left eye which was noticed since the time of her birth. Observation: Examination and investigations revealed a mass with scattered foci of calcification. The mass was causing expansion of left orbit with thinning and scalloping of bony boundaries of left orbit with no intracranial component. The scan suggests the diagnosis of orbital teratoma which was further confirmed by histopathological examination. Conclusion: The rare tumour presents a challenge in management. The aim of management depends upon the extent of tumour, preservation of vision whenever possible, promotion of normal orbital growth and cosmesis. 


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