The first case report of a patient with acquired factor XIII deficiency in the context of autoimmune encephalitis

Haemophilia ◽  
2017 ◽  
Vol 23 (5) ◽  
pp. e461-e464 ◽  
Author(s):  
I. Soto ◽  
A. Bernardo ◽  
T. Arias ◽  
C. Ramón ◽  
I. Noval ◽  
...  
Keyword(s):  
Case Report ◽  
Factor Xiii ◽  
Autoimmune Encephalitis ◽  
Factor Xiii Deficiency ◽  
First Case

scholarly journals Anti-NMDA Encephalitis: A Rare Encephalitis in a Child- A Case Report

2020 ◽  
Vol 19 (2) ◽  
pp. 108-111
Author(s):  
Saurav Khetan ◽  
Nikhil Agrawal ◽  
Prakash Rajoli
Keyword(s):  
Case Report ◽  
Japanese Encephalitis ◽  
Viral Encephalitis ◽  
Psychiatric Symptoms ◽  
Autoimmune Encephalitis ◽  
High Index ◽  
First Case ◽  
High Index Of Suspicion

Anti-NMDA encephalitis is second commonest cause of autoimmune encephalitis among children; however, it is hardly diagnosed and often not considered as one of the differentials when a child presents with encephalitis-related symptoms. In children, it presents mostly with seizures or psychiatric symptoms without prodrome. Here we present a six years old girl who presented with seizures and inappropriate behaviour. We investigated her in the line of viral encephalitis such as Japanese Encephalitis, which is very common in our region. However, results were not suggestive of Japanese Encephalitis and further investigations subsequently lead to diagnosis of anti- NMDA encephalitis. This is probably one of the first case report of this disease in our country. We want to highlight the significance of high index of suspicion for looking out for an organic cause in any child who presents with psychiatric symptoms, along with seizures.

scholarly journals Management of Neuraxial Analgesia in a Parturient with Factor XIII Deficiency: A Case Report and Proposed Management Algorithm

2020 ◽  
Vol 2020 ◽  
pp. 1-4
Author(s):  
David B. Carroll ◽  
Conrad Myler ◽  
Natthapol Songdej ◽  
Khaled Sedeek ◽  
Dmitri Bezinover
Keyword(s):  
Case Report ◽  
Factor Xiii ◽  
Hemorrhagic Stroke ◽  
Factor Xiii Deficiency ◽  
Neuraxial Analgesia ◽  
Management Algorithm ◽  
Coagulation Defect ◽  
Active Labor ◽  
History Of ◽  
Fxiii Deficiency

Factor XIII (FXIII) deficiency is a rare coagulation defect that can be associated with significant bleeding. A 28-year-old pregnant woman, with a history of hemorrhagic stroke secondary to severe congenital FXIII deficiency, presented in active labor requesting an epidural. Factor XIII levels had been monitored throughout her pregnancy and treated with intermittent factor XIII infusions to maintain factor levels above 30% of normal. After careful multidisciplinary peripartum evaluation and FXIII replacement, neuraxial analgesia was performed without complication. Neuraxial analgesia can be performed without complication in patients with FXIII deficiency if FXIII levels are carefully managed and no other coagulopathy exists.

Combined Heterozygous Factor XIII-Deficiency in a Family Case Report

2005 ◽  
pp. 380-382
Author(s):  
E. Rusicke ◽  
V. Ivaskevicius ◽  
D. Klarmann ◽  
C. Escuriola Ettingshausen ◽  
J. Oldenburg ◽  
...  
Keyword(s):  
Case Report ◽  
Factor Xiii ◽  
Factor Xiii Deficiency ◽  
Family Case

Factor XIII Deficiency Presenting As Persistent Umbilical Bleeding In Newborn - A Case Report

2012 ◽  
Vol 3 (6) ◽  
pp. 174-175
Author(s):  
Dr.Shivaprakash N C Dr.Shivaprakash N C ◽  
◽  
Dr.Kedarnath G T Dr.Kedarnath G T ◽  
Dr Uday Shankar S
Keyword(s):  
Case Report ◽  
Factor Xiii ◽  
Factor Xiii Deficiency

scholarly journals Effectiveness of Factor XIII Infusion in Treatment of Refractory Ureteral Leakage after Kidney Transplantation

2020 ◽  
Vol 2020 ◽  
pp. 1-5
Author(s):  
Ryoichi Maenosono ◽  
Tomohisa Matsunaga ◽  
Hajime Hirano ◽  
Hayahito Nomi ◽  
Shunri Taniguchi ◽  
...  
Keyword(s):  
Renal Failure ◽  
Kidney Transplantation ◽  
Case Report ◽  
Side Effects ◽  
Factor Xiii ◽  
Dizygotic Twin ◽  
First Case ◽  
Urological Complications ◽  
Plasma Factor ◽  
Urine Leakage

Despite the evolution of transplantation techniques, urological complications are common and result in loss of graft. We report the case of a 57-year-old man who developed continuous urine leakage despite pyeloureteral neoanastomosis and stenting after kidney transplantation from his dizygotic twin. Suspecting ureteral leakage, we performed pyeloureteral neoanastomosis using his native right ureter and a ureteral stent 5 days after the kidney transplant. However, urine leakage continued for several days. Because the plasma factor XIII level decreased to 48%, we administered factor XIII products (Fibrogammin P; CSL Behring, King of Prussia, PA) after the surgery. Although its utility and safety in patients with renal failure and/or transplantation are unclear, urine leakage stopped after the infusion of fibrogammin without any side effects. This is the first case report of the use of factor XIII for refractory urine leakage after kidney transplantation. Although further studies are needed, administration of factor XIII products could be one option for refractory urine leakage after transplantation.

scholarly journals Autoimmune Acquired Factor XIII Deficiency: A Case Report

2021 ◽  
Vol Volume 12 ◽  
pp. 63-68
Author(s):  
Ana Marco ◽  
Pascual Marco
Keyword(s):  
Case Report ◽  
Factor Xiii ◽  
Factor Xiii Deficiency

Spontaneous intracerebral hematoma in an adolescent with factor XIII deficiency. Case report

1989 ◽  
Vol 10 (6) ◽  
pp. 579-582
Author(s):  
C. Giraldi ◽  
S. Creta ◽  
A. Martini ◽  
C. Ioppoli ◽  
A. Valleriani ◽  
...  
Keyword(s):  
Case Report ◽  
Factor Xiii ◽  
Intracerebral Hematoma ◽  
Factor Xiii Deficiency
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