Budd-Chiari syndrome and veno-occlusive disease/sinusoidal obstruction syndrome

Gut ◽  
2008 ◽  
Vol 57 (10) ◽  
pp. 1469-1478 ◽  
Author(s):  
D-C Valla
Keyword(s):  
Occlusive Disease ◽  
Sinusoidal Obstruction Syndrome ◽  
Budd Chiari Syndrome ◽  
Chiari Syndrome

scholarly journals Imaging findings and differential diagnosis of hepatic sinusoidal occlusion syndrome and Budd-Chiari syndrome

2021 ◽  
Author(s):  
Cui yu Jia ◽  
Da wei Zhao ◽  
Ji liang Feng ◽  
Rui li Li ◽  
Xin xin Wang ◽  
...  
Keyword(s):  
Clinical Symptoms ◽  
Reduction Rate ◽  
Gallbladder Wall ◽  
Wall Thickening ◽  
Sinusoidal Obstruction Syndrome ◽  
Imaging Findings ◽  
Laboratory Examination ◽  
Budd Chiari Syndrome ◽  
Hepatic Sinusoidal Obstruction Syndrome ◽  
Chiari Syndrome

Abstract Objective To retrospectively analyze the clinical and imaging manifestations differential points between hepatic sinusoidal obstruction syndrome (SOS) and Budd-Chiari syndrome (BCS). Material The clinical symptoms, laboratory examination and imaging findings of 15 cases of hepatic sinusoidal obstruction syndrome and 33 cases of Budd-Chiari syndrome were statistically analyzed, find the identification points. The study used the Fisher test, P values of 0.05 or less were considered to indicate significant differences. The retrospective study was approved by the hospital's ethics committee. Results Laboratory tests: There were significant differences in total protein reduction rate (66.7% vs 9.1%, p༜0.01), albumin reduction rate (66.7% vs 9.1%, p༜0.01), Gamma-glutamyltransferase elevation rate (100% vs 6.1%, P༜0.01), alkaline phosphatase elevation rate (60% vs 6.1%, p༜0.01), and abnormal rate of prothrombin time (100% vs 21.2%, p༜0.01) between the two groups (BCS vs SOS). It also indicates that the liver function of SOS patients is more seriously impaired. Image findings: The following image findings were observed significant more frequently in SOS than in BCS and were statistically significant: gallbladder wall thickening (66.7% vs 78.2%, p༜0.01), ascites (80% vs 27.3%, p༜0.01), cloverleaf or claw-like shapes (80% vs 0%, p༜0.01). The following images appeared more frequently in BCS than in BCS and were statistically significant: caudate lobe enlargement (33.3% vs 75.8%, p༜0.01), collateral circulation (46.7% vs 93.9%, p༜0.01), diffuse patchy enhancement (20% vs 93.9%, p༜0.01), homogeneous in delayed phase (13.3% vs 90.1%, p༜0.01). Conclusion To Identification of SOS and BCS should be based on the patient's laboratory examination and imaging findings to improve diagnostic accuracy.

A Case Report on Budd Chiari Syndrome – Which Mimics Multiple Disorders

2021 ◽  
Vol 2 (3) ◽  
pp. 4-7
Author(s):  
Niveditha Dileep ◽  
John Thomas ◽  
Jisha James ◽  
Abhijith V
Keyword(s):  
Liver Parenchyma ◽  
Sinusoidal Obstruction Syndrome ◽  
Biliary Disease ◽  
Budd Chiari Syndrome ◽  
Clinical Presentations ◽  
Chiari Syndrome ◽  
History Of ◽  
Clinical Variants ◽  
Diagnostic Approaches

Background: Budd Chiari Syndrome (BCS) is the king of disorders which will mimic other disorders like chronic biliary disease, constrictive pericarditis, sinusoidal obstruction syndrome and so on, as it be like that, it is less diagnosed and treated in many countries. The prevalence of BCS is one in one million population, so it is a very rare case therefore it should be treated properly because many disorders like hematologic or malignant disease are the complications of BCS [1], [2]. Objective: To access the clinical variants of BCS along with the similarities and differences in clinical presentation, diagnostic approaches, and general treatment pattern which mimic, BCS thus gives the physician a clear outline about those disorders. Method: A man of 42 years old having BCS was taken for the study to carry out the differences in clinical features of BCS which distinguish the mimicking disorders. Clinical presentations were noted. Laboratory tests and diagnostic tests showed that the patient is having comorbidities including fatty liver with cholelithiasis, mild splenomegaly, liver parenchyma diseases, large esophageal varies with signs of recent hemorrhage, port hypertensive gastropathy and minimal ascites [3]. Patient get discharged after feeling better. Result: This patient is having chronic BCS with DIPS dysfunction. The patient had no history of liver disease before diagnosing BCS. BCS is almost curable when it is diagnosed correctly as early as possible. If not diagnosed early and treated well, comorbidities will occur, and it will affect the patient quality of life. Discussion: Early detection and proper treatment will help to control the disease up to an extent. This is depending on the physician’s knowledge. Hence, this case study clearly explains the disorders which mimic BCS for better understanding.

A CASE OF BUDD CHIARI SYNDROME IN 16 YEARS OLD MALE

2021 ◽  
pp. 50-50
Author(s):  
Sangita Rathod ◽  
Shweta Pandher
Keyword(s):  
Hepatic Vein ◽  
Sinusoidal Obstruction Syndrome ◽  
Budd Chiari Syndrome ◽  
Pericardial Disease ◽  
Cardiac Cirrhosis ◽  
Chiari Syndrome

Budd chiari syndrome is an uncommon disorder dened as hepatic vein outow tract obstruction, which is independent of the level and mechanism of obstruction( except pericardial disease and cardiac cirrhosis and sinusoidal obstruction syndrome)

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