Auditory Skills following Cochlear Implantation in Children with the Charge Syndrome

2019 ◽  
Vol 24 (3) ◽  
pp. 139-146
Author(s):  
Paula Aragón-Ramos ◽  
Maria-Fernanda Pedrero-Escalas ◽  
Javier Gavilán ◽  
Rosa Pérez-Mora ◽  
Belén Herrán-Martin ◽  
...  
Keyword(s):  
Oral Language ◽  
Cochlear Implantation ◽  
Charge Syndrome ◽  
Safe Procedure ◽  
Adequate Treatment ◽  
Study Materials ◽  
Ear Malformations ◽  
Facial Nerve Anatomy ◽  
Cochlear Malformation ◽  
Auditory Skills

Objectives: To assess the auditory outcomes and skills of pediatric cochlear implant (CI) users with the CHARGE syndrome. To determine the influence of inner ear malformations on the surgical procedure and speech understanding outcomes in this population. Study Design: Observational, retrospective study. Materials and Methods: Imaging, auditory testing, intraoperative findings, complications, and postoperative auditory skills and outcomes of pediatric CI users with CHARGE syndrome were recorded. Results: 6 children (8 ears) were included, 5 of whom had prelingual deafness. Their mean age at implantation was 37 months. Six of the 8 ears presented cochlear malformation; the most frequent was hypoplasia type III. Intraoperatively, the transmastoid facial recess approach was used in 5 ears, and abnormalities of facial nerve anatomy were found in 5 ears. All electrode insertions were complete. All children were, to a varying degree, able to detect and identify sound. Verbalization skills were developed by 2 children, 1 of whom used oral language as his primary mode of communication. Conclusions: Cochlear implantation performed by an experienced surgeon in patients with the CHARGE syndrome is a safe procedure with adequate treatment planning. All children had improved auditory skills although the improvement was variable.

Outcomes and Time to Emergence of Auditory Skills After Cochlear Implantation of Children With Charge Syndrome

2017 ◽  
Vol 38 (8) ◽  
pp. 1085-1091 ◽  
Author(s):  
Nancy M. Young ◽  
Elizabeth Tournis ◽  
Jenelle Sandy ◽  
Stephen R. Hoff ◽  
Maura Ryan
Keyword(s):  
Cochlear Implantation ◽  
Charge Syndrome ◽  
Auditory Skills

Development of auditory skills after cochlear implantation in children with inner ear malformations

2015 ◽  
Vol 136 (1) ◽  
pp. 78-82 ◽  
Author(s):  
Teru Kamogashira ◽  
Yusuke Akamatsu ◽  
Akinori Kashio ◽  
Erika Ogata ◽  
Shotaro Karino ◽  
...  
Keyword(s):  
Inner Ear ◽  
Cochlear Implantation ◽  
Inner Ear Malformations ◽  
Ear Malformations ◽  
Auditory Skills

scholarly journals The Development of Auditory Skills in Young Children with Mondini Dysplasia after Cochlear Implantation

PLoS ONE ◽  
2014 ◽  
Vol 9 (9) ◽  
pp. e108079 ◽  
Author(s):  
Xueqing Chen ◽  
Fei Yan ◽  
Bo Liu ◽  
Sha Liu ◽  
Ying Kong ◽  
...  
Keyword(s):  
Young Children ◽  
Cochlear Implantation ◽  
Mondini Dysplasia ◽  
Auditory Skills

Cochlear implantation in patients afflicted with inner ear malformations – the Pécs experience

2018 ◽  
Vol 16 (4) ◽  
pp. 232-237
Author(s):  
Peter Bako ◽  
Adrienn Nemeth ◽  
Krisztian Molnar ◽  
Tamas Toth ◽  
Kinga Harmat ◽  
...  
Keyword(s):  
Inner Ear ◽  
Cochlear Implantation ◽  
Inner Ear Malformations ◽  
Ear Malformations

Post-operative problems and complications in 313 consecutive cochlear implantations

2008 ◽  
Vol 123 (5) ◽  
pp. 492-496 ◽  
Author(s):  
T Ovesen ◽  
L V Johansen
Keyword(s):  
Cochlear Implantation ◽  
Surgical Planning ◽  
Chart Review ◽  
Retrospective Chart Review ◽  
Safe Procedure ◽  
Tertiary Referral Centre ◽  
Antibiotic Resistant ◽  
Danish Patient ◽  
Study Population ◽  
Radical Cavity

AbstractObjective:To describe problems and complications associated with cochlear implantation, and their management, in a Danish patient population comprising both paediatric and adult patients.Design:Retrospective chart review.Setting:Tertiary referral centre.Subjects:Three hundred and thirteen consecutive cochlear implantations were studied. The median age of the study population was 10 years. Sixty per cent of patients were children and 40 per cent were adult; 52 per cent were female and 48 per cent were male.Intervention:Two hundred and ninety-four patients received a Cochlear Nucleus®implant. The remaining 19 received an Advanced Bionics implant.Main outcome measure:Presence of problems and complications after cochlear implantation.Results:Post-operative complications were found in 15.7 per cent of patients. The majority of these complications (11.2 per cent) were minor; 4.5 per cent were major. The major complications included one patient with meningitis, one patient with multiple antibiotic resistantStaphylococcus aureusinfection of a radical cavity, and one diabetic patient who developed a severe skin infection and whose implant became exposed.Conclusion:Cochlear implantation is a safe procedure within the studied setting. However, it is essential that careful attention be paid to surgical planning and technique, and it is important that healthcare staff and patients be aware of the possible problems and complications.

B111 Cochlear implantation in congenital middle and inner ear malformations in children

2011 ◽  
Vol 75 ◽  
pp. 30
Author(s):  
H. Skarzynski ◽  
M. Porowski ◽  
M. Mrówka ◽  
P. Mlotkowska-Klimek ◽  
A. Lorens ◽  
...  
Keyword(s):  
Inner Ear ◽  
Cochlear Implantation ◽  
Inner Ear Malformations ◽  
Ear Malformations

Role of Electrically Evoked Auditory Brainstem Response in Cochlear Implantation of Children With Inner Ear Malformations

2008 ◽  
Vol 29 (5) ◽  
pp. 626-634 ◽  
Author(s):  
Ana H. Kim ◽  
Paul R. Kileny ◽  
H. Alexander Arts ◽  
Hussam K. El-Kashlan ◽  
Steven A. Telian ◽  
...  
Keyword(s):  
Inner Ear ◽  
Cochlear Implantation ◽  
Auditory Brainstem Response ◽  
Auditory Brainstem ◽  
Inner Ear Malformations ◽  
Ear Malformations ◽  
Brainstem Response

The role of preoperative imaging for auditory implants in children

2020 ◽  
Vol 74 (6) ◽  
pp. 1-5
Author(s):  
Małgorzata Burzyńska-Makuch ◽  
Józef Mierzwiński ◽  
Karolina Haber
Keyword(s):  
Inner Ear ◽  
Cochlear Implantation ◽  
Preoperative Imaging ◽  
Surgical Approaches ◽  
Clinical Decisions ◽  
Imaging Studies ◽  
Inner Ear Malformations ◽  
Ear Malformations ◽  
Cochlear Ossification ◽  
Temporal Bones

<b>Introduction:</b> Preoperative imaging, besides audiological evaluation, plays a major role in evaluation of candidacy for auditory implants, and in particular cochlear implants. It is essential to assess whether the basic criteria necessary for implantation are met. Diagnostic imaging is crucial not only in determining candidacy, but also determining the feasibility of cochlear implantation as it allow to anticipate surgical difficulties which could preclude or complicate the implantation of the device. The aim of the study is to present the protocol for the evaluation of preoperative imaging studies with particular focus on the factors potentially affecting clinical decisions in children qualified for cochlear implantation. <br><b>Material and method:</b> Preoperative imaging studies of 111 children performed prior to cochlear implantation were analyzed: high-resolution computed tomography (HRCT) of temporal bones and MRI. The assessment was made according to the presented protocol. <br><b>Results:</b> Pathologies and anomalies identified during the assessment of preoperative imaging studies significantly altered clinical decisions in 30% of patients. In the study group, in 17% of patients inner ear malformations were identified. 2.7% of children were disqualified from a cochlear implantation due to severe congenital inner ear malformations. 9% of the patients have had bacterial meningitis. In 50% of them difficulties related to complete or progressive cochlear ossification occurred. In 4.5% of patients less common surgical approaches other than mastoidectomy with a posterior tympanotomy were applied. <br><b>Discussion:</b> Preoperative imaging allow for the identification of significant pathologies and anomalies affecting qualification decisions and further treatment. HRCT and MRI are complementary to each other for preoperative imaging. The two modalities in combination allow accurate and optimal evaluation of the anatomical structures prior to implantation. Inner ear malformations and cochlear ossification following meningitis are relatively frequently encountered in children qualified for a cochlear implant.

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