A Case of Large Aplasia Cutis Congenita with Underlying Skull Defect: Effective Surgical Treatment with Integra® Dermal Regeneration Template

2021 ◽  
pp. 1-6
Author(s):  
Andrea Scotti ◽  
Elisa Benanti ◽  
Federica Augelli ◽  
Franz Wilhelm Baruffaldi Preis
Keyword(s):  
Free Flaps ◽  
Bony Defect ◽  
Large Defect ◽  
Aplasia Cutis Congenita ◽  
Rare Congenital Abnormality ◽  
Dermal Regeneration Template ◽  
Congenital Condition ◽  
Dermal Regeneration ◽  
Aplasia Cutis

<b><i>Introduction:</i></b> Aplasia cutis congenita (ACC) is a rare congenital abnormality characterized by the absence of a portion of skin at birth which most commonly involves the scalp and can affect the galea, the pericranium, the bone, and the dura mater. It can be an isolated condition or associated with other disorders. <b><i>Case Report:</i></b> We present a case of ACC with a large defect of the scalp and the underlying bone treated with the use of Integra® Dermal regeneration template. At 5 months of follow-up, the wound is completely healed and the bony defect greatly reduced. Contraction of the area of alopecia was observed. <b><i>Discussion:</i></b> Several surgical and conservative options have been described to treat this congenital condition: advanced dressing, skin graft, local flaps, free flaps, and other methods. In our case, we used Integra® Dermal templates which provide a barrier for infections, promote cellular activity for a rapid vascularization, and improve healing.

Management of severe hand wounds with integra® dermal regeneration template

2010 ◽  
Vol 36 (3) ◽  
pp. 185-193 ◽  
Author(s):  
R. Weigert ◽  
H. Choughri ◽  
V. Casoli
Keyword(s):  
Clinical Experience ◽  
Free Flap ◽  
Skin Grafting ◽  
Effective Technique ◽  
Flap Coverage ◽  
Thickness Skin ◽  
Split Thickness Skin Grafting ◽  
Dermal Regeneration Template ◽  
Dermal Regeneration

We report our experience with the use of Integra® for the management of severe traumatic wounds of the hand. Fifteen patients were treated with follow-up ranging from 10 to 37 months. Wounds were associated with an osseous and/or joint and/or tendon exposure. Following Integra® placement, patients were managed with dressings and subsequent split-thickness skin grafting an average of 26 days later. Integra® was successful in achieving durable, functional and aesthetic definitive coverage in 13 of 15 applications while allowing a satisfying pollicidigital prehension. Regarding our clinical experience, Integra® is an effective technique to deal with severe wounds of the hand with exposed tendon and/or bone and/or joint, even in the absence of paratenon or periosteum. This can potentially lessen the need for local rotational or free flap coverage and should be taken into consideration as a viable alternative in traumatic reconstruction of the hand.

scholarly journals Truncal aplasia cutis congenita grafted with dermal regeneration matrix – A case report

2017 ◽  
Vol 1 (2) ◽  
Author(s):  
Mauro Schiavon ◽  
Eugenio Fraccalanza ◽  
Carla Pittini ◽  
Roberto Baraziol ◽  
Jacopo Tesei ◽  
...  
Keyword(s):  
Case Report ◽  
Aplasia Cutis Congenita ◽  
Dermal Regeneration ◽  
Aplasia Cutis

Nonsurgical approach to congenital scalp and skull defects

1982 ◽  
Vol 56 (5) ◽  
pp. 711-715 ◽  
Author(s):  
Kamel F. Muakkassa ◽  
Robert B. King ◽  
David B. Stark
Keyword(s):  
Natural Course ◽  
Aplasia Cutis Congenita ◽  
Content Type ◽  
Skull Defects ◽  
Aplasia Cutis ◽  
Fine Print

✓ The management of congenital scalp and skull defects, as generally advocated, is surgical. The authors report such a case that was treated conservatively. At her 3-year follow-up review, the patient's scalp and skull defects and other associated cutaneous defects were fully reconstituted. Such a nonoperative approach, while rarely reported, emphasizes the natural course that some of these lesions may follow. The literature on aplasia cutis congenita is briefly reviewed.

scholarly journals Type VI Aplasia Cutis Congenita: Bart’s Syndrome

2015 ◽  
Vol 2015 ◽  
pp. 1-3 ◽  
Author(s):  
Ferit Kulalı ◽  
Ahmet Yagmur Bas ◽  
Yusuf Kale ◽  
Istemi Han Celik ◽  
Nihal Demirel ◽  
...  
Keyword(s):  
Signs And Symptoms ◽  
Final Diagnosis ◽  
Complete Healing ◽  
Aplasia Cutis Congenita ◽  
Surgical Interventions ◽  
Histologic Evaluation ◽  
Topical Antibacterial ◽  
Gauze Dressing ◽  
Aplasia Cutis

Bart’s syndrome is characterized by aplasia cutis congenita and epidermolysis bullosa. We present the case of a newborn male who developed blisters on the mucous membranes and the skin following congenital localized absence of skin. Bart’s syndrome (BS) is diagnosed clinically based on the disorder’s unique signs and symptoms but histologic evaluation of the skin can help to confirm the final diagnosis. The patient was managed conservatively with topical antibacterial ointment and wet gauze dressing. Periodic follow-up examinations showed complete healing. We emphasized that it is important to use relatively simple methods for optimal healing without the need for complex surgical interventions.

Erosive pustular dermatosis of the scalp after aplasia cutis congenita in a 9-year-old patient: A 5-year follow-up

2017 ◽  
Vol 34 (6) ◽  
pp. 695-696 ◽  
Author(s):  
Raymond Fertig ◽  
Austin Maddy ◽  
Débora Cadore de Farias ◽  
Sandro Simão Corrêa Filho ◽  
Marcelo Rigatti ◽  
...  
Keyword(s):  
Aplasia Cutis Congenita ◽  
Aplasia Cutis
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