scholarly journals Outcomes of Multistage Palliation of Infants With Single Ventricle and Atrioventricular Septal Defect

2019 ◽  
Vol 11 (1) ◽  
pp. 39-48 ◽  
Author(s):  
Bahaaldin Alsoufi ◽  
Courtney McCracken ◽  
Kirk Kanter ◽  
Subhadra Shashidharan ◽  
William Border ◽  
...  
Keyword(s):  
Competing Risks ◽  
Septal Defect ◽  
Single Ventricle ◽  
Distinct Group ◽  
Atrioventricular Septal Defect ◽  
Genetic Syndromes ◽  
Factors Associated ◽  
Competing Risks Analysis ◽  
One Year ◽  
Anomalous Pulmonary Venous Connection

Background: Published palliation outcomes of infants with functional single ventricle (SV) and common atrioventricular septal defect (AVSD) are poor due to associated cardiac and extracardiac anomalies and development of atrioventricular valve (AVV) regurgitation. We report current palliation results. Methods: From 2002 to 2012, 80 infants with functional SV with AVSD underwent multistage palliation. Competing-risks analyses modeled events after first-stage surgery and Glenn (death/transplantation vs next palliation surgery) and examined factors associated with survival and AVV intervention. Results: Sixty-eight (80%) patients received neonatal palliation: modified Blalock-Taussig shunt (n = 33, 41%), Norwood (n = 20, 25%), and pulmonary artery band (n = 15, 19%), whereas 12 (15%) received primary Glenn. On competing-risks analysis, one-year following first-stage surgery, 29% of patients had died or received transplantation and 62% had undergone Glenn. Five years following Glenn, 9% of patients had died or received transplantation and 68% had undergone Fontan. Overall eight-year survival was 64% and was lower in patients with genetic syndromes (53% vs 82%), patients requiring concomitant total anomalous pulmonary venous connection repair (53% vs 69%), and those requiring neonatal palliation (48% vs 100%). Factors associated with mortality were unplanned reoperation (hazard ratio [HR]: 3.7 [1.7-8.0], P = .001) and extracorporeal membrane oxygenation use (HR: 7.1 [3.0-16.6], P < .001). Initial AVV regurgitation ≥ moderate was associated with AVV intervention (HR: 6.2 [2.4-16.1], P = .002) with eight-year freedom from death or AVV intervention of 25% in those patients. Conclusions: Patients with SV with AVSD are a distinct group and commonly have associated cardiac and extracardiac malformations that complicate care and affect survival. The development of AVV regurgitation requiring intervention is common but does not affect survival.

scholarly journals Echocardiographic preoperative evaluation of unbalanced atrioventricular septal defect

2020 ◽  
Vol 26 (2) ◽  
pp. 46-58
Author(s):  
Zornitsa Vassileva ◽  
Anna Kaneva
Keyword(s):  
Congenital Heart ◽  
Septal Defect ◽  
Single Ventricle ◽  
Preoperative Evaluation ◽  
Atrioventricular Septal Defect ◽  
Precise Determination ◽  
Moderate Degree ◽  
Surgical Strategies ◽  
Single Ventricle Palliation

Unbalanced atrioventricular septal defect is seen by 10-15% of the patients with this congenital heart disease and poses serious challenges for the treating physicians regarding the choice of the most suitable operative intervention. The forms with moderate degree of unbalance between the two ventricles, especially when the size of the left ventricle is considered borderline, make the choice between two-ventricle correction and single-ventricle palliation quite difficult. The most important factor when judging the degree of unbalance is not the size of the ventricles but rather the redistribution of blood flow. The use of different echocardiographic measurements could contribute to the more precise determination of the indications for one of the two surgical strategies with resulting improvement of patient outcome.

Replacement of the left atrioventricular valve after repair of atrioventricular septal defect

1991 ◽  
Vol 1 (4) ◽  
pp. 383-389 ◽  
Author(s):  
Keishi Kadoba ◽  
Richard A. Jonas
Keyword(s):  
Heart Block ◽  
Septal Defect ◽  
Complete Heart Block ◽  
Ventricular Outflow Tract ◽  
Atrioventricular Septal Defect ◽  
Left Ventricular ◽  
Atrioventricular Valve ◽  
Left Ventricular Outflow ◽  
One Year ◽  
First Year Of Life

SummaryA retrospective analysis of 55 patients who underwent replacement of the left atrioventricular valve following surgery for atrioventricular septal defect with separate right and left atrioventricular valves or with a common valvar orifice has revealed a marked decrease in the need for valvar replacement over time. Between 1983 and 1987, the incidence of replacement following repair has been 3% in infants. Overall early mortality for the entire series, extending from 1970 to 1987, was 22%. Mortality in the first year of life was 58%, which was significantly greater than mortality beyond one year of age (14%, p<0.01). Obstruction of the left ventricular outflow tract was a frequent incremental risk factor for death during infancy. The incidence of complete heart block (25%) is disappointingly high, and may reflect distortion of the left atrioventricular junction in an attempt to place as large a prosthesis as possible. The incidence of complete heart block has not decreased with time. These results confirm the desirability of secondary valvoplasty procedures to enable a child to be larger before ultimate replacement of the valve is required.

Partial anomalous pulmonary venous connection and partial atrioventricular septal defect in an adult: Report of a case

Surgery Today ◽  
2011 ◽  
Vol 41 (10) ◽  
pp. 1421-1423
Author(s):  
Yoshimasa Seike ◽  
Yoshitsugu Nakamura ◽  
Osamu Tagusari ◽  
Satoru Domoto ◽  
Kiyoharu Nakano ◽  
...  
Keyword(s):  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Anomalous Pulmonary Venous Connection

Unique foetal diagnosis of aorto-pulmonary collaterals in right atrial isomerism

2020 ◽  
pp. 1-3
Author(s):  
Wadi Mawad ◽  
Nathalie Dutil ◽  
Varsha Thakur
Keyword(s):  
Septal Defect ◽  
Single Ventricle ◽  
Pulmonary Stenosis ◽  
Venous Drainage ◽  
Atrioventricular Septal Defect ◽  
Right Atrial ◽  
Collateral Arteries ◽  
Anomalous Venous Drainage ◽  
Atrial Isomerism ◽  
Foetal Diagnosis

Abstract Right atrial isomerism is associated with complex cardiac malformations, particularly single-ventricle lesions; right atrial isomerism is rarely associated with aorto-pulmonary collateral arteries. We report a foetal diagnosis of right atrial isomerism, with an unbalanced atrioventricular septal defect, pulmonary stenosis, total anomalous venous drainage, and significant aorto-pulmonary collaterals diagnosed at 22 weeks’ gestation.

Implantation of drug-eluting stents for relief of obstructed infra-cardiac totally anomalous pulmonary venous connection in isomerism of the right atrial appendages

2008 ◽  
Vol 18 (6) ◽  
pp. 628-630 ◽  
Author(s):  
Derek T. H. Wong ◽  
Shi-Joon Yoo ◽  
Kyong-Jin Lee
Keyword(s):  
Septal Defect ◽  
Pulmonary Atresia ◽  
Atrioventricular Septal Defect ◽  
Right Atrial ◽  
Collateral Arteries ◽  
Vertical Vein ◽  
Right Isomerism ◽  
Drug Eluting ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection

AbstractWe describe an infant with severe obstruction of infra-cardiac totally anomalous pulmonary venous connection associated with right isomerism, atrioventricular septal defect, pulmonary atresia, and multiple aortopulmonary collateral arteries. Implantation of a stent into the obstructed descending vertical vein provided effective palliation, with a dramatic increase in saturations of oxygen obviating the need for urgent high-risk surgery.

Rare Type of Mixed Total Anomalous Pulmonary Venous Drainage

1996 ◽  
Vol 4 (4) ◽  
pp. 238-240
Author(s):  
Anvay V Mulay ◽  
Michael T Ashworth ◽  
Janardan P Dhasmana
Keyword(s):  
Septal Defect ◽  
Congenital Abnormalities ◽  
Left Lung ◽  
Venous Drainage ◽  
Atrioventricular Septal Defect ◽  
Rare Form ◽  
Rare Type ◽  
Anomalous Pulmonary Venous Drainage ◽  
Anomalous Pulmonary Venous Connection

We describe a rare form of total anomalous pulmonary venous connection in a neonate with major extracardiac congenital abnormalities. The infracardiac communication was hypoplastic, whereas the supracardiac connection had an intrapulmonary course through the left lung. There was an associated atrioventricular septal defect.

scholarly journals Rare Association Between Atrioventricular Septal Defect and Partial Anomalous Pulmonary Venous Connection

2019 ◽  
Vol 34 (6) ◽  
Author(s):  
Alexandre Noboru Murakami ◽  
Gabriela Guimarães Baston ◽  
Mariana Ribeiro Rodero Cardoso ◽  
Carlos Henrique De Marchi ◽  
Ulisses Alexandre Croti
Keyword(s):  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Rare Association ◽  
Anomalous Pulmonary Venous Connection
Sign in / Sign up

Export Citation Format

Share Document