Clear cell sarcoma of the hand: Mimicking a palm phlegmon in a young adult

2017 ◽  
Author(s):  
Rym Bouriga
Keyword(s):  
Young Adult ◽  
Clear Cell ◽  
Clear Cell Sarcoma ◽  
Cell Sarcoma

Multimodality Therapy for Advanced Clear Cell Sarcoma of the Kidney in a Young Adult

1993 ◽  
Vol 51 (1) ◽  
pp. 39-42 ◽  
Author(s):  
Yoshiki Sugimura ◽  
Itsuo Yamamoto ◽  
Hiromi Tochigi ◽  
Jaichi Kawamura
Keyword(s):  
Young Adult ◽  
Clear Cell ◽  
Clear Cell Sarcoma ◽  
Multimodality Therapy ◽  
Cell Sarcoma

Clear cell sarcoma of tendons and aponeuroses, and osteoclast-rich tumour of the gastrointestinal tract with features resembling clear cell sarcoma of soft parts: a review and update

2010 ◽  
Vol 63 (5) ◽  
pp. 416-423 ◽  
Author(s):  
Kemal Kosemehmetoglu ◽  
Andrew L Folpe
Keyword(s):  
Gastrointestinal Tract ◽  
Young Adult ◽  
Malignant Melanoma ◽  
Soft Tissue ◽  
Clear Cell ◽  
Clear Cell Sarcoma ◽  
Soft Tissue Neoplasm ◽  
Cell Sarcoma ◽  
Melanocytic Differentiation ◽  
Gastrointestinal Neoplasm

Clear cell sarcoma (CCS) is a rare, distinctive soft tissue neoplasm, typically occurring in the distal extremities of young adult patients. Although CCS shows melanocytic differentiation, it is now clear that it is clinicopathologically and genetically distinct from conventional malignant melanoma. The ‘osteoclast-rich tumour of the gastrointestinal tract with features resembling clear cell sarcoma of soft parts’ is an extraordinarily rare gastrointestinal neoplasm that shares some features of CCS, but differs from it in other ways. The historical, histopathological, ultrastructural, immunohistochemical and genetic aspects of these two tumours are reviewed in this article.

Unusual Renal Sarcoma in a Young Adult: Its Similarities to Clear Cell Sarcoma of the Kidney

1987 ◽  
Vol 137 (4) ◽  
pp. 730-731 ◽  
Author(s):  
K. Ogawa ◽  
Y. Nakashima ◽  
Y.-C. Kim ◽  
H. Yamabe ◽  
T. Mizukami ◽  
...  
Keyword(s):  
Young Adult ◽  
Clear Cell ◽  
Clear Cell Sarcoma ◽  
Cell Sarcoma

An immunohistochemical study comparing clear cell sarcoma of the kidney and wilms' tumor

Pathology ◽  
1993 ◽  
Vol 25 (2) ◽  
pp. 106-109 ◽  
Author(s):  
Lai-Meng Lool ◽  
Phaik-Leng Cheah
Keyword(s):  
Clear Cell ◽  
Immunohistochemical Study ◽  
Wilms Tumor ◽  
Clear Cell Sarcoma ◽  
Cell Sarcoma

scholarly journals A long-term survivor of clear cell sarcoma-like tumor of the gastrointestinal tract with liver metastasis: a case report

2020 ◽  
Vol 6 (1) ◽  
Author(s):  
Takuhisa Okada ◽  
Yasumitsu Hirano ◽  
Shintaro Ishikawa ◽  
Hiroka Kondo ◽  
Toshimasa Ishii ◽  
...  
Keyword(s):  
Small Intestine ◽  
Lymph Node ◽  
Gastrointestinal Tract ◽  
Liver Metastasis ◽  
Surgical Resection ◽  
Clear Cell ◽  
Clear Cell Sarcoma ◽  
Cell Sarcoma

Abstract Background Clear cell sarcoma-like tumor of the gastrointestinal tract (CCSLTGT) is extremely rare. It is a mesenchymal neoplasm that usually forms in the small intestine of adolescents and young adults, is prone to local recurrence and metastasis, and has a high mortality rate. We report a patient with CCSLTGT with lymph node- and liver metastases, who continues to survive 6 years after initial surgical resection. Case presentation A 38-year-old woman presented with lightheadedness. Laboratory analysis revealed anemia (hemoglobin, 6.7 g/dL), and enhanced computed tomography (CT) demonstrated a mass in the small intestine, about 6 cm in diameter, with swelling of 2 regional lymph nodes. Double-balloon small intestine endoscopic examination revealed a tumor accompanied by an ulcer; the biopsy findings suggested a primary cancer of the small intestine. She was admitted, and we then performed a laparotomy for partial resection of the small intestine with lymph node dissection. Pathologic examination revealed CCSLTGT with regional lymph node metastases. About 3 years later, follow-up CT revealed a single liver metastasis. Consequently, she underwent a laparoscopic partial liver resection. Histopathologic examination confirmed that the liver metastasis was consistent with CCSLTGT. It has now been 3 years without a recurrence. Conclusion Repeated radical surgical resection with close follow-up may be the only way to achieve long-term survival in patients with CCLSTGT.

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